Filed (PHiled). Greater than 1-2 years since publication

Patent ductus arteriosus shunting direction and diameter predict inpatient outcomes in newborns with congenital diaphragmatic hernia

Min Bao, Tao Wu, Jinghui Guo, Ying Wang, Aimei Cao, Chao Liu, Yandong Wei, Chunhua Zheng, Lin Shi, Lishuang MaChildren’s Hospital in Capital Institute of Pediatrics.China Frontiers in PediatricsFront Pediatr 2023; 11:DOI: 10.3389/fped.2023.1272052 AbstractObjective: To evaluate whether the patent ductus arteriosus (PDA) can serve as a predictive factor for inpatient outcomes in congenital diaphragmatic hernia (CDH) patients.Methods: A […]

Patent ductus arteriosus shunting direction and diameter predict inpatient outcomes in newborns with congenital diaphragmatic hernia Read More »

Spontaneous breathing in selected neonates with very mild congenital diaphragmatic hernia

Florian Kipfmueller, Judith Leyens, Flaminia Pugnaloni, Bartolomeo Bo, Tamara Grass, Lotte Lemloh, Lukas Schroeder, Patrizia Nitsch‐Felsecker, Christoph Berg, Andreas Heydweiller, Brigitte Strizek, Andreas MuellerChildren’s Hospital and University Hospital Bonn and University of Bonn. “Bambino Gesù” Children’s Hospital. Germany and Italy Pediatric PulmonologyPediatr Pulmonol 2023; DOI: 10.1002/ppul.26791 AbstractAims: Current treatment guidelines recommend immediate postnatal intubation in all neonates

Spontaneous breathing in selected neonates with very mild congenital diaphragmatic hernia Read More »

An extreme case of cor triatriatum mimicking hypoplastic left heart syndrome and combined pulmonary vein stenosis

Hee Ju Hong, Hye Won Kwon, Jae Gun Kwak, Sang Yun Lee, Yoon Seong LeeSeoul National University Hospital.South Korea Cardiology in the YoungCardiol Young 2023; DOI: 10.1017/S1047951123003724 AbstractA 65-day-old girl presented to the emergency room with lethargy, requiring emergency venoarterial extracorporeal membrane oxygenation for refractory cardiogenic shock. Initially, hypoplastic left heart syndrome was suspected. However, cor

An extreme case of cor triatriatum mimicking hypoplastic left heart syndrome and combined pulmonary vein stenosis Read More »

Patent Ductus Arteriosus and Bronchopulmonary Dysplasia-Associated Pulmonary Hypertension: A Bayesian Meta-Analysis

Eduardo Villamor, Elkevan Westering-Kroon, Gema E. Gonzalez-Luis, František Bartoš, Steven H. Abman, Maurice J. HuizingMosaKids Children’s Hospital and Maastricht University Medical Center. Hospital Universitario Materno-Infantil de Canarias. University of Amsterdam. University of Colorado Anschutz School of Medicine and Children’s Hospital Colorado, Aurora.Netherlands, Spain and United States Journal of the American Medical Association Network OpenJAMA Netw

Patent Ductus Arteriosus and Bronchopulmonary Dysplasia-Associated Pulmonary Hypertension: A Bayesian Meta-Analysis Read More »

Altered Smooth Muscle Cell Histone Acetylome by the SPHK2/S1P Axis Promotes Pulmonary Hypertension

A. Dushani C. U. Ranasinghe, Maggie Holohan, Kalyn M. Borger, Deborah L. Donahue, Rafael D. Kuc, Martin Gerig, Andrew Kim, Victoria A. Ploplis, Francis J. Castellino, Margaret A. SchwarzHarper Cancer Research Institute and University of Notre Dame.United States Circulation ResearchCirc Res 2023; 133: 704-719DOI: 10.1161/CIRCRESAHA.123.322740 AbstractBackground: Epigenetic regulation of vascular remodeling in pulmonary hypertension (PH) is poorly

Altered Smooth Muscle Cell Histone Acetylome by the SPHK2/S1P Axis Promotes Pulmonary Hypertension Read More »

In vivo hepatic flow distribution by computational fluid dynamics can predict pulmonary flow distribution in patients with Fontan circulation

Petter Frieberg, Pia Sjöberg, Erik Hedström, Marcus Carlsson, Petru LiubaLund University and Skåne University Hospital.Sweden Scientific ReportsSci Rep 2023; 13:DOI: 10.1038/s41598-023-45396-6 AbstractIn Fontan patients, a lung deprived of hepatic blood may develop pulmonary arterio-venous malformations (PAVMs) resulting in shunting, reduced pulmonary vascular resistance (PVR) and decreased oxygenation. To provide guidance for corrective invasive interventions, we aimed

In vivo hepatic flow distribution by computational fluid dynamics can predict pulmonary flow distribution in patients with Fontan circulation Read More »

Pregnancy and delivery after percutaneous embolization with a combination of microvascular plugs and hydrogel-coated coils for unilateral diffuse pulmonary arteriovenous malformations: a case report

Kayo Ogino, Tomohiro Hayashi, Kenji Waki, Masanobu OhyaKurashiki Central Hospital.Japan European Heart Journal Case ReportsEur Heart J Case Rep 2023; 7:DOI: 10.1093/ehjcr/ytad468 AbstractBackground: Pulmonary arteriovenous malformations (PAVMs) are abnormal communications between the pulmonary arteries and veins; right-to-left shunts can cause hypoxaemia, emboli to systemic circulation, and brain abscesses. Cyanosis during pregnancy may increase the probability of premature

Pregnancy and delivery after percutaneous embolization with a combination of microvascular plugs and hydrogel-coated coils for unilateral diffuse pulmonary arteriovenous malformations: a case report Read More »

Prevalence and Predictors of Hereditary Hemorrhagic Telangiectasia and Capillary-Malformation Arteriovenous Malformation Syndrome Among Children with Neurovascular Malformations

Elissa R. Engel, Katie Wusik, Philip Bright, Sudhakar Vadivelu, J. Michael Taylor, Adrienne HammelUniversity of Cincinnati College of Medicine and Cincinnati Children’s Hospital Medical Center. University of Kentucky College of Medicine.United States Journal of PediatricsJ Pediatr 2023; DOI: 10.1016/j.jpeds.2023.113761 AbstractObjective: To investigate the prevalence and predictors of hereditary hemorrhagic telangiectasia (HHT) and capillary-malformation arteriovenous malformation (CM-AVM) syndrome

Prevalence and Predictors of Hereditary Hemorrhagic Telangiectasia and Capillary-Malformation Arteriovenous Malformation Syndrome Among Children with Neurovascular Malformations Read More »

Longitudinal Assessment of Curaçao Criteria in Children with Hereditary Hemorrhagic Telangiectasia

Mordechai Pollak, Dvir Gatt, Michelle Shaw, Sheryl Hewko, Anthony Lamanna, Sara Santos, Felix RatjenHospital for Sick Children and Ruth Rappaport Children’s Hospital.Canada Journal of PediatricsJ Pediatr 2023; DOI: 10.1016/j.jpeds.2023.113665 AbstractObjective: To assess the utility of the Curaçao criteria by age over time in children with hereditary hemorrhagic telangiectasia (HHT).Study design: This was a single-center, retrospective analysis of patients

Longitudinal Assessment of Curaçao Criteria in Children with Hereditary Hemorrhagic Telangiectasia Read More »

Effective long-term sirolimus treatment in hypoxemia mainly due to intrapulmonary right-to-left shunt in a patient with multiple vascular anomalies

Jinrong Liu, Xiaomin Duan, Jie Yin, Haiming Yang, Ruxuan He, Shunying ZhaoBeijing Children’s Hospital, National Center for Children’s Health and Capital Medical University.China Orphanet Journal of Rare DiseasesOrphanet J Rare Dis 2023; 18:DOI: 10.1186/s13023-023-02732-3 AbstractPulmonary arteriovenous malformations (PAVMs), particularly where feeding artery/arteries to PAVMs ≥ 3 mm can be treated with embolization. The treatment for hypoxemia

Effective long-term sirolimus treatment in hypoxemia mainly due to intrapulmonary right-to-left shunt in a patient with multiple vascular anomalies Read More »

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