Filed (PHiled). Greater than 1-2 years since publication

Role of phosphodiesterase-3 inhibitor in cardiorespiratory fitness and functional class of patients with pulmonary hypertension: A randomized, double-blind, placebo-controlled trial

Sefri N. Sofia, Udin Bahrudin, Ilham Uddin, Muhammad A. Sobirin, Erna Setiawati, Galuh Hardaningsih, Kevin C. Tjandra, Edward K. S. LimijadiUniversitas Diponegoro. Dr. Kariadi Hospital. Indonesia Narra JNarra J 2025; 5: DOI: 10.52225/narra.v5i1.1301 AbstractMany patients with acyanotic shunt congenital heart disease (CHD) are diagnosed only in adulthood, by which time pulmonary hypertension (PH) has developed, impairing

Role of phosphodiesterase-3 inhibitor in cardiorespiratory fitness and functional class of patients with pulmonary hypertension: A randomized, double-blind, placebo-controlled trial Read More »

[Hereditary hemorrhagic telangiectasia: a report of two cases]

Yan Huang, Chen-Tao Liu, Xiang-Rong Zheng, Bo Dou, Rong HuangXiangya Hospital of Central South University.China Chinese Journal of Contemorary PediatricsZhongguo Dang Dai Er Ke Za Zhi 2020; 22: 1041-1042DOI: 10.7499/j.issn.1008-8830.2004196 AbstractThis article reports two children with hereditary hemorrhagic telangiectasia (HHT). Patient 1 was a boy aged 12 years and was admitted due to intermittent cough and

[Hereditary hemorrhagic telangiectasia: a report of two cases] Read More »

Juvenile polyposis syndrome-hereditary hemorrhagic telangiectasia associated with a SMAD4 mutation in a girl

Yusuke Hashimoto, Koji Yokoyama, Hideki Kumagai, Yuko Okada, Takanori YamagataJichi Medical University.Japan Clinical Journal of GastroenterologyClin J Gastroenterol 2020; 13: 1096-1101DOI: 10.1007/s12328-020-01238-w AbstractJuvenile polyposis syndrome (JPS) and hereditary hemorrhagic telangiectasia (HHT) are both relatively rare hereditary disorders. Some patients with the SMAD4 gene mutation develop both JPS and HHT, a condition termed JPS-HHT. We herein report

Juvenile polyposis syndrome-hereditary hemorrhagic telangiectasia associated with a SMAD4 mutation in a girl Read More »

Is Pulmonary Embolism a Chronic Disease?

Gerard Gurumurthy, Lianna Reynolds, Kirsten de Wit, Lara N. Roberts, Jecko ThachilUniversity of Manchester. Royal Manchester Children’s Hospital. Queen’s University. McMaster University. King’s College Hospital NHS. United Kingdom and Canada Clinical Medicine JournalClin Med 2025;DOI: 10.1016/j.clinme.2025.100325 AbstractPulmonary embolism (PE) is often regarded as an acute disorder, yet emerging evidence underscores its chronic trajectory. Many survivors endure

Is Pulmonary Embolism a Chronic Disease? Read More »

Mechanotransductive stabilization of HIF-1α is inhibited by mitochondrial antioxidant therapy in the setting of pulmonary overcirculation

Jason T. Boehme, Sanjeev A. Datar, Xutong Sun, Wenhui Gong, Qing Lu, Jamie Soto, Michael A. Smith, Alejandro E. Garcia-Flores, Gary W. Raff, TingWang, Emin Maltepe, Stephen M. Black, Jeffrey R. FinemanUniversity of California San Francisco. Florida International University. University of California Davis. United States Scientific ReportsSci Rep 2025; 15: DOI: 10.1038/s41598-025-99062-0 AbstractIn patients with congenital

Mechanotransductive stabilization of HIF-1α is inhibited by mitochondrial antioxidant therapy in the setting of pulmonary overcirculation Read More »

Inhibiting Serotonin Synthesis for the Treatment of Pulmonary Arterial Hypertension

Georg Hansmann, Michael BaderFriedrich-Alexander-University Erlangen-Nürnberg. Trypto Therapeutics. Charité-Universitätsmedizin. University of LübeckGermany Pulmonary CirculationPulm Circ 2025; 15: DOI: 10.1002/pul2.70100 AbstractAbstract Not Available CategoryMedical Therapy. Efficacy or Lack of EfficacyMedical Therapy. Adverse Effects or Lack of Adverse Effects Age Focus: No Age-Related Focus Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication Article Access Free

Inhibiting Serotonin Synthesis for the Treatment of Pulmonary Arterial Hypertension Read More »

Embolization of Acquired Pulmonary Arteriovenous Malformations Resulting from Metastatic Gestational Trophoblastic Neoplasia

Gretchen A. Ferber, Sarah Khoncarly, James J. Buchino, Janice D. McDanielUniversity of Pittsburgh Medical Center. Case Western Reserve University MetroHealth Medical Center. Cleveland Clinic Akron General Hospital. Akron Children’s Hospital.United States Journal of Vascular and Interventional RadiologyJ Vasc Interv Radiol 2020; 31: 1890-1892DOI: 10.1016/j.jvir.2020.01.021 AbstractAbstract Not Available CategoryPulmonary Arteriovenous Malformations Age Focus: Pediatric Pulmonary Vascular Disease

Embolization of Acquired Pulmonary Arteriovenous Malformations Resulting from Metastatic Gestational Trophoblastic Neoplasia Read More »

The clinical and genetic features of hereditary haemorrhagic telangiectasia (HHT) in central South Africa-three novel pathogenic variants

Tendaishe T. Mutize, Riaz Y. Seedat, Johannes K. Ploos van Amstel, Johannes J. Mager, Stephen C. Brown, Fekade Gebremariam, Marius J. CoetzeeUniversity of the Free State nd Universitas Academic Hospital. Utrecht University. Shelly Beach Hospital. National Health Laboratory Service.South Africa and Netherlands Molecular Biology ReportsMol Biol Rep 2020; 47: 9967-9972DOI: 10.1007/s11033-020-05985-4 AbstractHereditary haemorrhagic telangiectasia (HHT) is

The clinical and genetic features of hereditary haemorrhagic telangiectasia (HHT) in central South Africa-three novel pathogenic variants Read More »

Comparative study between nebulized and intravenous magnesium sulfate for treatment of persistent pulmonary hypertension in neonates

Nashwa Farouk Mohamed, Osama Abu El Fetouch Zaki El Feky, Heba Morsy Saad El Din El Ganady, Walid Abd Elatif Abd El HalimBenha University.Egypt Journal of Neonatal-Perinatal MedicineJ Neonatal Perinatal Med 2025; 18: 246-254DOI: 10.1177/19345798251325510 AbstractBackground: Persistent pulmonary hypertension of the newborn (PPHN) is a life-threatening condition resulting from elevated pulmonary vascular resistance, causing severe hypoxemia.

Comparative study between nebulized and intravenous magnesium sulfate for treatment of persistent pulmonary hypertension in neonates Read More »

Pulmonary arteriole narrowing in end-stage cystic fibrosis lungs occurs with and without small airway disease

Astrid Vermaut, Gitte Aerts, Lynn Willems, Vincent Geudens, Charlotte Hooft, Pieterjan Kerckhof, Lise Vanvuchelen, Marta Zapata-Ortega, Hanne Beeckmans, Xin Jin, Yousry Mohamady, Jan Van Slambrouck, Lucia Aversa, Janne Verhaegen, Emanuela E. Cortesi, Charlotte De Fays, Birgit Weynand,Dirk E. Van Raemdonck, Laurens J. Ceulemans, Wim A. Wuyts, Marianne Carlon, Robin Vos, Natalie Lorent, Ghislaine Gayan-Ramirez, Laurent

Pulmonary arteriole narrowing in end-stage cystic fibrosis lungs occurs with and without small airway disease Read More »

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