Diagnostic Testing for Pulmonary Vascular Disease. Non-invasive Testing

Chest computed tomography findings of ground-glass nodules with enhancing central vessel/nodule in pediatric patients with BMPR2 mutations and plexogenic arteriopathy

Jason P. Weinman, David A. Mong, LaDonna J. Malone, D. Dunbar Ivy, Robin R. Deterding, Csaba GalambosChildren’s Hospital Colorado.United States Pediatric RadiologyPediatr Radiol 2022; 52: 2549-2556DOI: 10.1007/s00247-022-05413-8 AbstractBackground: Germline mutation in bone morphogenetic protein type II (BMPR2) is the most common cause of idiopathic/heritable pulmonary hypertension in pediatric patients. Despite the discovery of this gene there are […]

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A novel non-invasive and echocardiography-derived method for quantification of right ventricular pressure-volume loops

Manuel J. Richter, Athiththan Yogeswaran, Faeq Husain-Sved, Istvan Vadasc, Zvomimir Rako, Emad Mojajerani, Hossein A. Ghofrani, Robert Naeije, Werner Seeger, Ulrike Herberg, Andreas Rieth, Ryan J. Tedford, Friedrich Grimminger, Henning Gall, Khodr TelloJustus-Liebig-University Giessen. Kerckhoff Heart, Rheuma and Thoracic Center. Imperial College London. Erasme University Hospital. University of Bonn. Medical University of South Carolina. Germany,

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Benefit of stereoscopic volume rendering for the identification of pediatric pulmonary vein stenosis from CT angiography

Michelle Noga, Ross Cockburn, Jiali Luan, Deepa Krishnaswamy, Kumaradevan PunithakumarUniversity of Alberta. Mazankowski Alberta Heart Institute. University of Manitoba. Dalhousie University.Canada PLOS Digital HealthPLOS Digit Health 2023; 2: DOI: 10.1371/journal.pdig.0000215 AbstractThe use of three-dimensional (3D) technologies in medical practice is increasing; however, its use is largely untested. One 3D technology, stereoscopic volume-rendered 3D display, can improve

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Factors associated with discontinuation of pulmonary vasodilator therapy in children with bronchopulmonary dysplasia-associated pulmonary hypertension

Catherine M. Avitabile, Xuemei Zhang, Steve B. Ampah, Yan Wang, Devon Ash, Kathleen Nilan, Laura Mercer-Rosa, Julie L. Fierro, David B. Frank, Kathleen A. GibbsUniversity of Pennsylvania and Children’s Hospital of Philadelphia.United States Journal of PerinatologyJ Perinatol 2022; 42: 1246-1254DOI: 10.1038/s41372-022-01421-6 AbstractObjective: To evaluate factors associated with discontinuation of pulmonary vasodilator therapy in bronchopulmonary dysplasia-related pulmonary hypertension

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Late onset of pulmonary hypertension in very low birth weight infants

Joseph Ginski, Dmitry Tumin, Devon Kuehn, Jason Higginson, Scott MacGilvrayEast Carolina UniversityUnited States Journal of Maternal Fetal and Neonatal MedicineJ Matern Fetal Neonatal Med 2022; 35: 3516-3518DOI: 10.1080/14767058.2020.1826924 AbstractIntroduction: Pulmonary hypertension (PH) is a recognized complication of bronchopulmonary dysplasia (BPD). Recent guidelines recommend evaluating all infants with BPD for PH via echocardiogram, but the specific timing of this screening

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SCMR expert consensus statement for cardiovascular magnetic resonance of acquired and non-structural pediatric heart disease

Adam L. Dorfman, Tal Geva, Margaret M. Samyn, Gerald Greil, Rajesh Krishnamurthy, Daniel Messroghli, Pierluigi Festa, Aurelio Secinaro, Brian Soriano, Andrew Taylor, Michael D. Taylor, René M. Botnar, Wyman W. LaiUniversity of Michigan and C.S. Mott Children’s Hospital.Boston Children’s Hospital. Medical College of Wisconsin. University of Texas Southwestern Medical Center. Nationwide Children’s Hospital. Deutsches Herzzentrum

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Repolarization Dispersion Is Associated With Diastolic Electromechanical Discoordination in Children With Pulmonary Arterial Hypertension

Michal Schäfer, Benjamin S. Frank, D. Dunbar Ivy, Max B. Mitchell, Kathryn K. Collins, Pei-Ni Jone, Johannes C. von AlvenslebenUniversity of Colorado and Children’s Hospital Colorado.United States Journal of the American Heart AssociationJ Am Heart Assoc 2022; 11: DOI: 10.1161/JAHA.121.024787 AbstractBackground: Electromechanical dyssynchrony is a well described comorbidity in pulmonary arterial hypertension (PAH). ECG-derived measurements reflective

Repolarization Dispersion Is Associated With Diastolic Electromechanical Discoordination in Children With Pulmonary Arterial Hypertension Read More »

Pulmonary artery acceleration time in young children is determined by heart rate and transpulmonary gradient but not by pulmonary blood flow: A simultaneous echocardiography-cardiac catheterization study

Christiana Tai, Anyir Hsieh, Anita J. Moon-Grady, Roberta L. Keller, David Teitel, Hythem M. NawaytouUniversity of California, San FranciscoUnited States EchocardiographyEchocardiography 2022; 39: 895-905DOI: 10.1111/echo.15397 AbstractIntroduction: Pulmonary artery acceleration time (PAAT) is considered useful for the non-invasive evaluation of pulmonary artery pressure (PAP) and pulmonary vascular resistance (PVR). PAAT is dependent on PAP, PVR, pulmonary artery compliance,

Pulmonary artery acceleration time in young children is determined by heart rate and transpulmonary gradient but not by pulmonary blood flow: A simultaneous echocardiography-cardiac catheterization study Read More »

Kynurenine metabolites predict survival in pulmonary arterial hypertension: A role for IL-6/IL-6Rα

Zongye Cai, Siyu Tian, Theo Klein, Ly Tu, Laurie W. Geenen, Thomas Koudstaal, Annemien E. van den Bosch, Yolanda B. de Rijke, Irwin K. M. Reiss, Eric Boersma, Claude van der Ley, Martijn Van Faassen, Ido Kema, Dirk J. Duncker, Karin A. Boomars, Karin Tran‑Lundmark, Christophe Guignabert, Daphne MerkusErasmus MC University Medical Center. Zhejiang University

Kynurenine metabolites predict survival in pulmonary arterial hypertension: A role for IL-6/IL-6Rα Read More »

Misclassification of Pulmonary Hypertension in Partial Anomalous Pulmonary Venous Return

Clifford W. Chin, David P. BichellVanderbilt University and Monroe Carell Junior Children’s HospitalUnited States Annals of Thoracic SurgeryAnn Thorac Surg 2022; 114: e447-e449DOI: 10.1016/j.athoracsur.2022.02.021 AbstractPartial anomalous pulmonary venous return is a rare congenital heart defect that can escape detection until adulthood and can be misdiagnosed as pulmonary hypertension and managed with vasodilators before the anomaly is

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