Diagnostic Testing for Pulmonary Vascular Disease. Invasive Testing

Congenital unilateral pulmonary venous atresia: definitive diagnosis and treatment

K. K. Pourmoghadam, J. W. Moore, M. Khan, E. M. Geary, N. Madan, B. J. Wolfson, J. P. de Chadarevian, D. S. Holsclaw, M. L. JacobsSt Christopher’s Hospital for Children. United States Pediatric CardiologyPediatr Cardiol 2003; 24: 73-79DOI: 10.1007/s00246-002-0220-6 AbstractThree cases of unilateral right-sided pulmonary venous atresia were evaluated over an 18-year period. These bring the […]

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Bronchoscopic diagnosis of asymptomatic unilateral pulmonary vein atresia in an infant

Cécile Tissot, Regula Corbelli, Yacine Aggoun, Maurice Beghetti, Eduardo da CruzChildren’s Hospital of Denver and University of Colorado at Denver. University of Geneva.United States and Switzerland Pediatric CardiologyPediatr Cardiol 2008; 29: 976-979DOI: 10.1007/s00246-007-9143-6 AbstractAn eight-month-old boy with findings of persistent left pulmonary basal infiltrate was diagnosed with congenital unilateral pulmonary vein atresia by bronchoscopy. Cardiac catheterization

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CT angiography of mildly symptomatic, isolated, unilateral right pulmonary vein atresia

Mindaugas Mataciunas, Lina Gumbiene, Sigitas Cibiras, Virgilijus Tarutis, Algirdas E. TamosiunasVilnius University.Lithuania Pediatric RadiologyPediatr Radiol 2009; 39: 1087-1090DOI: 10.1007/s00247-009-1291-9 AbstractWe report a mildly symptomatic 12-year-old boy with a very rare congenital anomaly-isolated unilateral pulmonary vein atresia. Diagnosis was made using CT angiography and its role in diagnosis is discussed. CategorySegmental Pulmonary Venous Disease. Without a Focus

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Congenital localized stenosis of the pulmonary veins

M. Henry, J. C. Hoeffel, C. PernotHospital Jeanne d’Arc.France Pediatric RadiologyPediatr Radiol 1975; 4: 49-52DOI: 10.1007/BF00978821 AbstractOne case of localized stenosis of the extrapulmonary portion of pulmonary veins is reported in a 3 years old child. The chest X-Ray showed a rounded and pulsatile opacification over the right hilum and on angiocardiography the right superior pulmonary

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Unilateral pulmonary vein atresia

Leonard E. Swischuk, Philippe L’HeureuxUniversityb of Texas Medical Branch. University of Minnesota Medical School.United States American Journal of RoentgenologyAJR Am J Roentgenol 1980; 135: 667-672DOI: 10.2214/ajr.135.4.667 AbstractThree cases of unilateral pulmonary vein atresia in children are described. The findings in all three cases were similar and consisted of hemoptysis, recurrent pulmonary infections, and a normal size

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Esophageal varices in association with unilateral pulmonary vein atresia

J. Kevin Harrison, Steven E. Hearne, William M. Baker, Peter Van Trigt, Gil Leidig, Thomas M. Bashore, Martin P. O’LaughlinDuke University Medical Center.United States Catheterization and Cardiovascular DiagnosesCathet Cardiovasc Diagn 1996; 38: 387-392DOI: 10.1002/(SICI)1097-0304(199608)38:4<387::AID-CCD14>3.0.CO;2-C AbstractA 27-yr-old woman with recurrent episodes of hemoptysis (and hematemesis due to esophageal varices) was found to have unilateral pulmonary vein atresia.

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Congenital unilateral pulmonary vein atresia: radiologic findings in three adult patients

Laura E. Heyneman, Robert L. Nolan, J. Kevin Harrison, H. Page McAdamsDuke University Medical Center.United States American Journal of RoentgenologyAJR Am J Roentgenol 2001; 177: 681-685DOI: 10.2214/ajr.177.3.1770681 AbstractObjective: The purpose of our study is to describe the radiologic findings of adult patients presenting with congenital unilateral pulmonary vein atresia.Conclusion: Chest radiography in affected patients typically reveals a small

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Survival comparison in adults with congenital systemic to pulmonary shunt and borderline elevated pulmonary vascular resistance versus Eisenmenger syndrome

Jantaras Sengsim, Chodchanok Vijarnsorn, Prakul Chanthong, Paweena Chungsomprasong, Supaluck Kanjanauthai, Ploy Thammasate, Thita Pacharapakornpong, Nalin Chaiwangyen, Densiri Bositthipichet, Jarupim Soongswang, Teerapong Tocharoenchok, Ekarat Nitiyarom, Kriangkrai Tantiwongkosri, Thaworn Subtaweesin, Kritvikrom DurongpisitkulSiriraj Hospital and Mahidol University.Thailand Scientific ReportsSci Rep 2024; 14: DOI: 10.1038/s41598-024-81834-9 AbstractPulmonary arterial hypertension (PAH) associated with congenital heart disease (PAH-CHD) is a consequence of unrepaired

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SOX17 – Associated Pulmonary Hypertension in Children: A Distinct Developmental and Clinical Syndrome

Mary P. Mullen, D. Dunbar Ivy, Nidhy P. Varghese, Abbey J. Winant, Nahir Cortes-Santiago, Sara O. Vargas, Diego Porres, Nicola Maschietto, Paul J. Critser, Russel Hirsch, Catherine M. Avitabile, Rachel K. Hopper, Benkamin S. Frank, Ryan D. Coleman, Pankaj B. Agrawal, Jill A. Madden, Amy E. Roberts, Shane L. Collins, J. Usha Raj, Eric D.

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MicroRNA Profiling to Inform Disease Classification, Severity, and Treatment Response in Pediatric Pulmonary Hypertension

Michael A. Smith, Sam Chiacchia, Jason Boehme, Sanjeev A. Datar, Emily Morell, Roberta L. Keller, Amy Romer, Elizabeth Colglazier, Clair Parker, Jasmine Becerra, Jeffrey R. FinemanUniversity of California, San Francisco. Stanford University. Children’s Hospital of Philadelphia.United States American Journal of Physiology Heart and Circulatory PhysiologyAm J Physiol Heart Circ Physiol 2024; DOI: https://doi.org/10.1152/ajpheart.00622.2024 AbstractPediatric pulmonary

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