Diagnostic Testing for Pulmonary Vascular Disease. Invasive Testing

Right ventriculo-pulmonary arterial uncoupling and poor outcomes in pulmonary arterial hypertension

Toshitaka Nakaya, Hiroshi Ohira, Takahiro Sato, Taku Watanabe, Masaharu Nishimura, Noriko Oyama-Manabe, Masaru Kato, Yoichi M. Ito and Ichizo TsujinoHokkaido University Hospital. The Institute of Statistical Mathematics.Japan Pulmonary CirculationPulm Circ 2020; 10: DOI: 10.1177/2045894020957223 AbstractRight ventricular function critically affects the prognosis of patients with pulmonary arterial hypertension. We aimed to analyze the prognostic value of right […]

Right ventriculo-pulmonary arterial uncoupling and poor outcomes in pulmonary arterial hypertension Read More »

Prognostic value of longitudinal vasoreactivity in pediatric pulmonary hypertension

Patrick D. Evers, Patrick Quinn, Paul J. Critser, Benjamin S. Frank, Laurie B. ArmsbyOregon Health Sciences University. University of Cininnati. University of Colorado.United States Pulmonary CirculationPulm Circ 2022; 12: e12152DOI: 10.1002/pul2.12152 AbstractUpon diagnosis of pulmonary hypertension in pediatrics, standard practice often involves acute vasoreactivity testing (AVT) in the cardiac catheterization laboratory. However, the importance of repeated

Prognostic value of longitudinal vasoreactivity in pediatric pulmonary hypertension Read More »

Management of Complex Pulmonary Vein Stenosis at Altitude Combining Comprehensive Percutaneous Interventional Treatment with Sirolimus, Pulmonary Hypertension Medications and Intraluminal Imaging with Optical Coherence Tomography

Michael J. Shorofsky, Gareth J. Morgan, Ernesto Mejia, Salvador A. Rodriguez, Megan Greene, Paige Sheaks, Dunbar Ivy, Jenny E. ZablahUniversity of Colorado and Children’s Hospital Colorado.United States Pediatric CardiologyPediatr Cardiol 2023; DOI: 10.1007/s00246-023-03102-3 AbstractBackground: Pulmonary vein stenosis (PVS) is a growing problem for the pediatric congenital heart population. Sirolimus has previously been shown to improve survival and

Management of Complex Pulmonary Vein Stenosis at Altitude Combining Comprehensive Percutaneous Interventional Treatment with Sirolimus, Pulmonary Hypertension Medications and Intraluminal Imaging with Optical Coherence Tomography Read More »

Paediatric pulmonary arterial hypertension: updates on definition, classification, diagnostics and management

Erika B. Rosenzweig, Steven H. Abman, Ian Adatia, Maurice Beghetti, Damien Bonnet, Sheila Haworth, D. Dunbar Ivy, Rolf M. F. BergerColumbia University and New York Presbyterian Hospital. University of Colorado and Children’s Hospital Colorado. Glenwood Children’s Heart Clinic. University Hospitals of Geneva and Lausanne. Hôpital Necker Enfants Malades, AP-HP, Université Paris Descartes. University College London.

Paediatric pulmonary arterial hypertension: updates on definition, classification, diagnostics and management Read More »

International practice heterogeneity in pre-transplant management of pulmonary hypertension related to pediatric left heart disease

Rachel K. Hopper, Oscar van der Have, Seth A. Hollander, Anne I. Dipchand, Valeria Perez de Sa, Jeffery A. Feinstein, Karin Tran-LundmarkStanford University and Lucille Packard Children’s Hospital. Lund University. Skane University Hospital. University of Toronto and the Hospital for Sick ChildrenUnited States, Sweden and Canada Pediatric TransplantationPediatr Transplant 2023; DOI: 10.1111/petr.14461 AbstractBackground: Elevated pulmonary vascular resistance

International practice heterogeneity in pre-transplant management of pulmonary hypertension related to pediatric left heart disease Read More »

Cardiac Catheterization and Hemodynamics in a Multicenter Cohort of Children with Pulmonary Hypertension

Erika B. Rosenzweig, Angela Bates, Mary P. Mullen, Steven H. Abman, Eric D. Austin, Allen Everett, Jeffrey Fineman, Jeffrey Feinstein, Rachel K. Hopper, John P. Kinsella, Usha S. Krishnan, Minmin Lu, Kenneth D, Mandl, J. Usha Raj, Nidhy Varghese, Delphene Yung, Stephanie S. Handler, Lynn A. SleeperPediatric Pulmonary Hypertension NetworkUnited States and Canada Annals of

Cardiac Catheterization and Hemodynamics in a Multicenter Cohort of Children with Pulmonary Hypertension Read More »

Diagnosis and management of pulmonary hypertension in congenital diaphragmatic hernia

Shazia Bombal, Neil PatelStanford University and Lucille Packard Children’s Hospital. Royal Hospital for Children, Glasgow. United States and United Kingdom Seminars in Fetal and Neonatal MedicineSemin Fetal Neonatal Med 2022; 27: DOI: 10.1016/j.siny.2022.101383 AbstractCongenital diaphragmatic hernia (CDH) contributes to neonatal morbidity and mortality worldwide. Pulmonary hypertension (PH) is a key component of CDH pathophysiology and critical

Diagnosis and management of pulmonary hypertension in congenital diaphragmatic hernia Read More »

Prevalence of variants in methylenetetrahydrofolate reductase and the severity of pulmonary vascular disease

Ronald W. Day, Gordon K. Mack, Andrea M. Barker, Tiffany Q. Rees, Lynda O. Jorgensen, Lorenzo D. BottoUniversity of Utah and Primary Children’s HospitalUnited States Pediatric CardiologyPediatr Cardiol 2015; 36: 524-530DOI: 10.1007/s00246-014-1044-x AbstractPulmonary hypertension is a serious disease associated with constriction, cellular proliferation, inflammation, and in situ thrombosis of the small vessels of the lung. Some

Prevalence of variants in methylenetetrahydrofolate reductase and the severity of pulmonary vascular disease Read More »

A long-term survivor with alveolar capillary dysplasia

Chandler E. Yost, Angelica R. Putnam, Megan K. Dishop, Lynda O. Jorgenson, Paul E. Wirkus, Ronald W. DayUniversity of Utah, Primary Children’s Hospital, Phoenix Children’s Hospital and Wasatch PediatricsUnited States Journal of the American College of Cardiology Case ReportsJACC Case Rep 2020; 2: 1492-1495DOI: 10.1016/j.jaccas.2020.05.055 AbstractA patient with alveolar capillary dysplasia has survived more than 56

A long-term survivor with alveolar capillary dysplasia Read More »

Improving guidance for the correctability of congenital shunts with increased pulmonary vascular resistance

Ronald W. DayUniversity of Utah and Primary Children’s HospitalUnited States International Journal of Cardiology Congenital Heart DefectsInt J Cardiol Congenit Heart Dis 2021;doi.org/10.1016/j.ijcchd.2021.100184 AbstractBackground. Based upon expert opinion, guidelines have been proposed for the correctability of congenital cardiovascular shunts with increased pulmonary vascular resistance. This study reports the accuracy of published guidelines using a dataset

Improving guidance for the correctability of congenital shunts with increased pulmonary vascular resistance Read More »

Scroll to Top