Diagnostic Testing for Pulmonary Vascular Disease. Invasive Testing

A Large Animal Model of Heritable Pulmonary Arterial Hypertension Using Gene-edited BMPR2 Sheep

Sanjeev A. Datar, Nicholas Werry, Austin R. Brown, Devon S. Fitzpatrick, Oluwafemi Falade, Josephine F. Trott, Rachel Hutchings, Elena K. Amin, Jessica M. Morgan, Hythem Nawaytou, Gail H. Deutsch, Eric G. Johnson, Omar A. Gonzales Viera, Thomas F. Bishop, Tara Urbano, Bret R. McNabb, Eric D. Austin, Jeffery R. Fineman, and Alison L. Van EenennaamUniversity […]

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Beyond the Echocardiogram: Cardiac Catheterization in Infants With Bronchopulmonary Dysplasia Associated Pulmonary Hypertension

Samuel J. Gentle, Audrey HebertYale School of Medicine. Centre Hospitalier Universitaire de Quebec.United States and Canada Journal of PediatricsJ Pediatr 2026; DOI: 10.1016/j.jpeds.2026.115026 AbstractAbstract Not Available CategoryClass III. Pulmonary Hypertension Associated with Lung DiseaseDiagnostic Testing for Pulmonary Vascular Disease. Non-invasive TestingDiagnostic Testing for Pulmonary Vascular Disease. Invasive Testing Age Focus: Pediatric Pulmonary Vascular Disease Fresh or

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Increased lung vasoreactivity in children from Leadville, Colorado, after recovery from high-altitude pulmonary edema

James W. Fasules, James W. Wiggins, Robert R. WolfeUniversity of Colorado School of Medicine.United States CirculationCirculation 1985; 72: 957-962DOI: 10.1161/01.cir.72.5.957 AbstractCardiac catheterization was performed on seven children after recovery from high-altitude pulmonary edema. All were life-long residents at elevations above 10,000 feet. Three of the seven had developed pulmonary edema without antecedent travel to low altitude

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Right ventricular adaptation in congenital heart disease: Does the type of right ventricular overload matter?

Renee S. Joosen, Gregor J. Krings, Heleen B. van der Zwaan, Nefise Karaman, Marco Guglielmo, Lucas R. Celant, Marco J. W. G€otte, Michael G. Dickinson, Michiel Voskuil, Marielle C. van de Veerdonk, Johannes M. P. J. BreurUniversity Medical Center Utrecht. Amsterdam University Medical Center and University of Amsterdam. Netherlands Journal of Thoracic and Cardiovascular Surgery

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Pulmonary Hemodynamics and Long-Term Outcomes in Children with Pulmonary Hypertension-Associated Bronchopulmonary Dysplasia

Eric D. Austin, Mary P. Mullen, Catherine M. Avitabile, Usha S. Krishnan, Erika B. Rosenzweig, Roberta L. Keller, John P. Kinsella, Delphine Yung, Lea Steffes, Angela Bates, Eleni G. Elia, Lewis H. Romer, Sharon McGrath-Morrow, Meghan L. Bernier, Kenneth D. Mandl, J.Usha Raj, Lynn A. Sleeper, Steven H. AbmanVanderbilt University Medical Center. Boston Children’s Hospital

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Prolonged Postnatal Hypoxia Impairs Lung Development and Causes Severe Pulmonary Hypertension in Mice

Luca Zazzeron, Kakeru Shimoda, Paul Lichtenegger, Elizabeth Moore, Helena Tattersfield, Alexandra K. Marenco, Jiayi Kang, Haobo Li, Eizo Marutani, Donald B. Bloch, Fumito IchinoseMassachusetts General Hospital and Harvard Medical School. United States Journal of the American Heart AssociationJ Am Heart Assoc 2025; DOI: 10.1161/JAHA.125.042608 AbstractBackground: In children born at high altitude, lung development is affected by hypoxia, which can lead to pulmonary hypertension and right ventricular failure.

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Porto-Pulmonary Hypertension in Children: Insights From a National Registry

Sadia Quyam, Alastair Baker, Alistair Calder, Shahin MoledinaGreat Ormond Street Hospital for Children. University College London. King’s College Hospital .Inited Kingdom Pulmonary CirculationPulm Circ 2025; 15: DOI: 10.1002/pul2.70133 AbstractPorto-pulmonary hypertension (PoPH) represents a rare but significant form of pulmonary arterial hypertension (PAH) in children. Despite its clinical importance, systematic analyses of paediatric presentations and outcomes remain limited.

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Right atrial function is impaired in pediatric pulmonary arterial hypertension: a multi-center cardiac MRI study

Kimberley G. Miles, Hieu T. Ta, Kurt R. Bjorkman, Zhiqian Gao, Nicholas J. Ollberding, Russel Hirsch, D. Dunbar Ivy, Sean M. Lang, Michelle Cash, Melissa Magness, Meredith O’Neil, Kimberly Luebbe, Benjamin S. Frank, Paul J. CritserCincinnati Children’s Hospital Medical Center and University of Cincinnati College of Medicine. Helen DeVos Children’s Hospital. University of Colorado School

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International Society for Heart and Lung Transplantation (ISHLT) Consensus Statement on Risk Stratification in Pulmonary Arterial Hypertension

Sandeep Sahay 1, Scott Visovatti 2, Adriano R Tonelli 3, Nelson Villasmil Hernandez 4, Eric D Austin 5, Roberto Badagliacca 6, Rolf M F Berger 7, Athénaïs Boucly 8, Yucheng Chen 9, Colin Church 10, Marion Delcroix 11, Allen D Everett 12, Harrison W Farber 13, Charles Fauvel 14, Mardi Gomberg-Maitland 15, Megan Griffiths 16, Francois Haddad 17, Yuchi Han 18, Anna Hemnes 5, Marius M Hoeper 19, Manreet K Kanwar 20, Daniel Lachant 21, Sandhya Murthy 22, Karen M Olsson 19, Ioana Preston 23, Göran Rådegran 24, Olivier Sitbon 25, Maria G Trivieri 26, Jean-Luc Vachiery 27, Rebecca Vanderpool 2, Jason Weatherald 28, R James White 21, Helen Whitford 29, Melisa Wilson 30, Raymond L Benza  Houston Methodist Hospital. Ohio State University.

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Pulmonary Vascular Compromise Is Associated With Survival in Pediatric Pulmonary Hypertension: A New Computational Model

Maria Niccum, Catherine M. Avitabile, Dana Albizem, Heather Meluskey, Christopher Penney, Brian D. Hanna, Michael L. O’Byrne, Zoheir Bshouty, David B. FrankPerelman School of Medicine at the University of Pennsylvania and Children’s Hospital of Philadelphia. University of Manitoba.United States and Canada Pulmonary CirculationPulm Circ 2025; 15: DOI: 10.1002/pul2.70156 AbstractPediatric pulmonary arterial hypertension (PAH) has a long

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