Class 5. Pulmonary Hypertension Associated with Hematological, Systemic, Metabolic, Nutritional and Other Disorders

Is restrictive atrial septal defect a risk in partial anomalous pulmonary venous drainage repair?

Jiaquan Zhu, Yasuhiro Kotani, Devin Chetan, Lisa Zhao, John G. Coles, Christopher A. Caldarone, Glen S. Van Arsdell, Osami HonjoThe Hospital for Sick Children and University of Toronto.Canada Annals of Thoracic SurgeryAnn Thorac Surg 2014; 97: 1664-1670DOI: 10.1016/j.athoracsur.2014.01.051 AbstractBackground: The creation or enlargement of an atrial septal defect (ASD) in partial anomalous pulmonary venous drainage (PAPVD) repair […]

Is restrictive atrial septal defect a risk in partial anomalous pulmonary venous drainage repair? Read More »

Anomalous origin of the left pulmonary artery from the right pulmonary artery. Report of 2 cases and review of the literature

Kenneth L. Jue, Gunay Raghib, Kurt Amplatz, Paul Adams Jr, Jesse E. EdwardsCharles T. Miller Hospital and University of Minnesota.United States American Journal of Roentgenology Radium Therapy and Nuclear MedicineAm J Roentgenol Radium Ther Nucl Med 1965; 95: 598-610DOI: 10.2214/ajr.95.3.598 AbstractAbstract Not Available CategorySegmental Pulmonary Venous Disease. Without a Focus on Pulmonary HypertensionPulmonary Vascular Pathology Age

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Dual-energy computed tomography to detect early pulmonary vascular changes in children with sickle cell disease: a pilot study

Raphael Joye, Julie Wacker, Duy-Anh Nguyen, Anne-Lise Hachulla, Albane B. R. Maggio, Laurent Cimasoni, Frederic Lador, Marc Ansari, Maurice BeghettiGeneva University Hospitals and University of Geneva.Switzerland Frontiers in PediatricsFront Pediatr 2023; 11DOI: 10.3389/fped.2023.1221977 AbstractIntroduction: Pulmonary hypertension (PH) is a rare but fatal complication of sickle cell disease (SCD) that is possibly reversible if treated early. Dual-energy computed

Dual-energy computed tomography to detect early pulmonary vascular changes in children with sickle cell disease: a pilot study Read More »

Pulmonary Hypertension and Left Ventricular Geometric Types in Sickle Cell Anemia

Opeyemi Olalekan Oni, Abiona Oluwadamilola Odeyemi, Tetende Toyin Olasinde, Abimbola Ololade Odayemi, Kehinde Joyce Olufemi-Aworinde, Ademola Toyosi Abolarin, Oluwabukola Ayodele AlaLAUTECH University. Osun State University.  Bowen University. Nigeria American Journal of CardiologyAm J Cardiol 2023; 203: 175-183DOI: 10.1016/j.amjcard.2023.06.100 AbstractPulmonary hypertension (PHT) is multifactorial in origin and a major cause of morbidity and mortality in the sickle

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Rheumatologic manifestations with elevated levels of IL-6, IL-17A, and IL-23 in a patient with scurvy

Masahiro Ueki, Keita Sakamoto, Noriko Nishioka, Hiroki Ohata, Takiko Nobuta, Shunichiro Takezaki, Atsushi Manabe, Masafumi YamadaHokkaido University Hospital. Rakuno Gakuen University. Japan Modern Rheumatology Case ReportsMod Rheumatol Case Rep 2023; 7: 302-306DOI: 10.1093/mrcr/rxac059 AbstractSymptomatic vitamin C deficiency, scurvy, is a relatively rare disease in developed countries, but it has been reported in patients with autism spectrum

Rheumatologic manifestations with elevated levels of IL-6, IL-17A, and IL-23 in a patient with scurvy Read More »

Endothelin-1 gene polymorphism (G8002A) and endothelial monocyte-activating polypeptide II: Role in vascular dysfunction in pediatric patients with β-thalassemia major

Azza Abdel Gawad Tantawy, Mourad Alfy Ramzy Tadros, Amira Abdel Moneam Adly, Eman Abdel Rahman Ismail, Fatma A. Ibrahim, Nanis Mohammed Salah Eldin, Mahitab Morsy Hussein, Mervat Abdalhameed Alfeky, Sarah Mohammed Ibrahim, Marwa Adel Hashem, Fatma Soliman, Elsayed EbeidAin Shams University. Military Medical Services and Military Medical Academy. National Research Center. Egypt CytokineCytokine 2023; DOI: 10.1016/j.cyto.2022.156048

Endothelin-1 gene polymorphism (G8002A) and endothelial monocyte-activating polypeptide II: Role in vascular dysfunction in pediatric patients with β-thalassemia major Read More »

Pulmonary Histopathologic Findings in Pediatric Patients After Hematopoietic Stem Cell Transplantation: An Autopsy Study

Nahir Cortes-Santiago, Kalyani R. Patel, Hao Wu, Sara E. Sartain, Saleh Bhar, Manuel Silva-Carmona, Jennifer PogorilerTexas Children’s Hospital and Baylor College of Medicine. Yale School of Medicine and Yale New Haven Hospital. Children’s Hospital of Philadelphia.United States Pediatric and Developmental PathologyPediatr Dev Pathol 2023; DOI: 10.1177/10935266231170101 AbstractBackground: Pathologic characterization of pulmonary complications following hematopoietic stem cell transplantation

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Sleep disordered breathing and its relation to stroke and pulmonary hypertension in children with sickle cell disease: a single-center cross-sectional study

Azza Tantawy, Nayera El‑Sherif, Sara Makkeyah, Nahed Salah Eldeen, Noura Bahaa El‑Din Farghal, Nanies Soliman, Fatma S. E. EbeidAin Shams University. Egypt Annals of HematologyAnn Hematol 2023; 102: 271-281DOI: 10.1007/s00277-023-05099-4 AbstractSleep disordered breathing (SDB) is a common underdiagnosed sequela of sickle cell disease (SCD) that has been linked to the frequency of vaso-occlusive crises. To determine the frequency of SDB in children with SCD and its association to

Sleep disordered breathing and its relation to stroke and pulmonary hypertension in children with sickle cell disease: a single-center cross-sectional study Read More »

RASA3 is a candidate gene in sickle cell disease-associated pulmonary hypertension and pulmonary arterial hypertension

Clare C. Prohaska, Xu Zhang, Tae‐Hwi L. Schwantes‐An, Robert S. Stearman, Stanley Hooker, Rick A. Kittles, Micheala A. Aldred, Katie A. Lutz, Michael W. Pauciulo, William C. Nichols, Ankit A. Desai, Victor R. Gordeuk, Roberto F. MachadoIndiana University. University of Illinois at Chicago. City of Hope. Morehouse School of Medicine. Cincinnati Children’s Hospital Medical Center

RASA3 is a candidate gene in sickle cell disease-associated pulmonary hypertension and pulmonary arterial hypertension Read More »

Endothelin-1 gene polymorphism (G8002A) and endothelial monocyte-activating polypeptide II: Role in vascular dysfunction in pediatric patients with β-thalassemia major

Azza Abdel Gawad Tantawy, Mourad Alfy Ramzy Tadros, Amira Abdel Moneam Adly, Eman Abdel Rahman Ismail, Fatma A. Ibrahim, Nanis Mohammed Salah Eldin, Mahitab Morsy Hussein, Mervat Abdalhameed Alfeky, Sarah Mohammed Ibrahim, Marwa Adel Hashem, Fatma Soliman Elsayed EbeidAin Shams University. Military Medical Services and Military Medical Academy.Egypt CytokineCytokine 2023; 161: DOI: 10.1016/j.cyto.2022.156048 AbstractBackground: Endothelin-1 (ET-1), a potent endogenous vasoconstrictor, stimulates production of reactive oxygen species. Endothelial monocyte-activating polypeptide-II (EMAP-II) is a multifunctional polypeptide.Aim: To assess ET-1 gene polymorphism

Endothelin-1 gene polymorphism (G8002A) and endothelial monocyte-activating polypeptide II: Role in vascular dysfunction in pediatric patients with β-thalassemia major Read More »

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