Class 4. Pulmonary Hypertension Associated with Thromboembolic Disease

Severe fat embolism syndrome following minor trauma in a child with Duchenne muscular dystrophy: A case report

R. Montero-Yéboles, J. L. López-Prats, A. Barrés-Fernández, B. Guzman-Morais, L. Tarongi-Marco, P. Rosello-MilletHospital Clínico Universitario de Valencia. Universitat de València.Spain Molecular Genetics and Metabolism ReportsMol Genet Metab Rep 2026; 49:DOI: 10.1016/j.ymgmr.2026.101361 AbstractBackground Fat embolism syndrome (FES) is a rare but potentially life-threatening complication classically associated with long-bone fractures and orthopedic procedures. Patients with Duchenne muscular

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Successful Pregnancy in Chronic Obstructive Pulmonary Hypertension Secondary to Pulmonary and Cardiac Hydatid Cysts: A Case Report

Farnaz Ahmadi, Raha Parnia, Bahamin Astani, Mohammad-Sadegh Keshmiri, Shakiba Khodadad, Hakimeh Sheikhzadeh, Zahra Daneshmandi, Faezeh Ansari, Mahsa Riahi, Sima Noorali, Hannaneh Yousefi-Koma, Babak Sharif-Kashani, Shadi ShafaghiShahid Beheshti University of Medical Sciences. Simon Fraser University. Erfan Hospital. Mofid Children’s Hospital. Masih Daneshvari Hospital.Iran, Canada Research in Heart Yield and Translational MedicineRes Heart Yield Transl Med 2026;

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Obese Adolescent with Factor V Leiden-Related Pulmonary Embolism: Case-Based Insight into Paediatric Thrombosis Management

Filip Bossowski, Magdalena Bossowska, Katarzyna Masłowska, Paweł Sliwko, Helena Zórawska, Kornel Semeran, Jacek Robert Janica, Artur BossowskiMedical University of Białystok. Poland DiagnosticsDiagnostics 2026; 16: DOI: 10.3390/diagnostics16172842 AbstractBackground/Objectives: Paediatric pulmonary embolism (PE) is rare but potentially lethal, and its diagnosis is complicated by non-specific presentations and multiple predisposing risk factors. We describe a 15-year-old girl who

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Successful Pulmonary Thromboendarterectomy for Malignancy-Associated Septic Chronic Thromboembolic Disease in Children

Andrés Felipe Rubio-Duarte, Laura Isabel Manosalva-Arciniegas, Diego Márquez-Bohorquez, Carolina Riveros-Bustos, Albert Franz Guerrero-BecerraHospital Internacional de Colombia HIC, Fundacion Cardiovascular de Colombia FCV and Fundacion Universitaria FCV. Columbia Journal of the American College of Cardiology Case ReportsJACC Case Rep 2026; DOI: 10.1016/j.jaccas.2026.109336 AbstractBackground: Chronic thromboembolic pulmonary hypertension is exceptionally rare in children and is typically associated with major

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Pulmonary Endarterectomy in Pediatric Patients: Institutional Experience

Çağatay Çetinkaya, Nezih Onur Ermerak, Ela Erdem, Figen Akalın, Koray Ak, Eylem Tuncer, Altuğ Sağır, Bedrettin Yildizeli BedrettinUskudar University. Marmara University. University of Health Sciences.Turkey Thoracic and Cardiovascular SurgeonThorac Cardiovasc Surg 2026; DOI: 10.1055/a-2875-1852 AbstractBackground: Chronic thromboembolic pulmonary hypertension (CTEPH) is rare in children and published experience with pulmonary endarterectomy (PEA) is limited.Methods: We retrospectively reviewed six patients

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Pediatric Pulmonary Infarction and Infarction-Like Pulmonary Injury: An Etiology-Oriented Narrative Review

Shuxuan Li, Yanran Zhang, Xiangxiang Tian, Wanqing Zhao, Yongsheng XuTianjin Medical University and Tianjin Children’s Hospital (Children’s Hospital of Tianjin University).China Seminars in Thrombosis and HemostasisSemin Thromb Hemost 2026; DOI: 10.1055/a-2889-7005 Abstract Pulmonary infarction (PI) has traditionally been regarded as a complication of pulmonary embolism (PE). However, increasing evidence suggests that pediatric PI represents a heterogeneous

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Animal models of chronic thromboembolic pulmonary hypertension

Yong-Jian Zhu, Lin-Chao Zhou, Xiao-Xue Zhang, Xiao-Yang Ren,Yi Yan, Shao-Fei LiuFirst Affiliated Hospital of Zhengzhou University. Henan Provincial People’s Hospital. Shanghai Children’s Medical Center, National Children’s Medical Center and Shanghai Jiao Tong University School of Medicine. Changhai Hospital and Naval Medical University.China Animal Models and Experimental MedicineAnimal Model Exp Med 2026; DOI: 10.1002/ame2.70167 AbstractChronic thromboembolic pulmonary

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Non-Extremity Thrombosis Sequelae in Children: Screening, Diagnosis, and Management

Riten Kumar, Vilmarie Rodriguez, Clay Cohen, Madhvi Rajpurkar, Ayesha ZiaBoston Children’s Hospital and Harvard Medical School. Nationwide Children’s Hospital and Ohio State University. Texas Children’s Hospital and Baylor College of Medicine. Central Michigan University, Children’s Hospital of Michigan and Wayne State University. University of Texas Southwestern.United States Journal od Thrombosis and HemostasisJ Thronb Hemost 2026;

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[Analysis of follow-up and prognosis in pediatric rheumatic diseases associated with pulmonary embolism]

T. Yue, Y. C. Yan, M. Kang, J. Zhu, Y. J. Xu, D. Zhang, M. Li, M. Wen, F. F. Wu, J. M. LaiCapital Center for Children’s Health and Capital Medical University. China Chinese Journal of PediatricsZhonghua Er Ke Za Zhi 2025; 64: 89-94DOI: 10.3760/cma.j.cn112140-20250714-00613 AbstractObjective: To explore the clinical characteristics, diagnosis and treatment strategies, and prognosis

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Quantitative Evaluation of Lung Perfusion by Dynamic Chest Radiography in Chronic Thromboembolic Pulmonary Hypertension: Comparison With Lung Perfusion Scintigraphy

Megumi Ikeda, Yuzo Yamasaki, Koji Sagiyama, Kazuya Hosokawa, Daisuke Toyomura Tomoyuki Hida, Takuya Hino, Kosuke Tabata, Takuro Isoda, Noritsugu Matsutani, Hidetake Yabuuchi, Kohtaro Abe, Koichi Akashi, Kousei IshigamiKyushu University. Japan Pulmonary CirculationPulm Circ 2025; 15: DOI: 10.1002/pul2.70170 AbstractPulmonary perfusion assessment is essential for the management of chronic thromboembolic pulmonary hypertension (CTEPH). Lung perfusion scintigraphy and contrast-enhanced

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