Class 3. Pulmonary Hypertension Associated with Lung Hypoplasia

Importance of age at diagnosis of pulmonary hypertension in children living at high altitude: Longitudinal follow-up of 86 patients

Gabriel F. Diaz, Carlos E. Diaz‐Castrillon, Alicia Marquez Garcia, Rachel K. Hopper, Vinicio de J. PerezUniversidad Nacional De Colombia. University of Pittsburgh. Centro Policlínico Del Olaya and Clínica De La Mujer. Stanford University School of Medicine. Columbia and United States Pulmonary CirculationPulm Circ 2025; 15: DOI: 10.1002/pul2.70017 AbstractPulmonary hypertension (PH) at high altitudes presents unique characteristics […]

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Respiratory Support Strategies for Surgical Neonates: A Review

Piero Alberti, Niyi Ade-Ajayi, Anne GreenoughKing’s College London.United Kingdom ChildrenChildren 2025; 12: DOI: 10.3390/children12030273 AbstractNeonates with congenital conditions which require surgical management frequently experience respiratory distress. This review discusses the management of pulmonary complications and the respiratory support strategies for four conditions: oesophageal atresia-tracheoesophageal fistula (OA-TOF), congenital diaphragmatic hernia (CDH), congenital lung malformations (CLM), and anterior

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Omphalocele and Associated Anomalies: Exploring Pulmonary Development and Genetic Correlations-A Literature Review

Dina Al Namat, Romulus Adrian Ros, Razan Al Namat, Elena Hanganu, Andrei Ivan, Delia Hînganu, Ancut Lupu, Marius Valeriu HînganuUniversity of Medicine and Pharmacy “Grigore T. Popa”. “Saint Mary” Emergency Children HospitalRomania DiagnosticsDiagnostics 2025; 15: DOI: 10.3390/diagnostics15060675 AbstractOmphalocele is a rare congenital abdominal wall defect, occurring in approximately 3.38 per 10,000 pregnancies. It is characterized by

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Increased circulating Endothelin-1 is a risk factor for ECMO use and mortality in neonates with congenital diaphragmatic hernia: a prospective observational study

Lotte Lemloh, Aster de Vadder, Tamene Melaku, Bartolomeo Bo, Neil Patel, Stefan Holdenrieder, Andreas Mueller, Florian KipfmuellerChildren’s Hospital, University of Bonn. Royal Hospital for Children. Technical University of Munich. University Medical Center Mannheim, University of Heidelberg.Germany and United Kingdom Respiratory ResearchRespir Res 2025; 25: DOI: 10.1186/s12931-025-03188-8 AbstractBackground: Elevated levels of Endothelin-1 (ET-1), a vasoactive peptide, have been

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Hemodynamic precision to guide surgical timing for neonates with congenital diaphragmatic hernia: a narrative review

John T. Wren, Neil Patel, Matthew T. Harting, Patrick J. McNamaraUniversity of Iowa Hospitals and Clinics. Royal Hospital for Children. McGovern Medical School at the University of Texas Health Science Center and Children’s Memorial Hermann Hospital. United States and United Kingdom Journal of PerinatologyJ Perinatol 2025; DOI: 10.1038/s41372-025-02265-6 AbstractDespite a near universal approach focused on physiologic

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Concurrent Bronchopulmonary Sequestration in Congenital Diaphragmatic Hernia: Is Frequency Increasing or Are We Better at Diagnosis?

Michelle J. Yang, Christian C. Yost, Martha Monson, Paula J. Woodward, Anne M. Kennedy, Stephen J. Fenton, Katie W. Russell, Janice L. B. Byrne, Bradley A. YoderPrimary Children’s Hospital and University of Utah School of Medicine.United States Journal of Pediatrics: Clinical PracticeJ Pediatr Clin Pract 2025; DOI: 10.1016/j.jpedcp.2025.200141 AbstractObjective: To assess the incidence and clinical outcomes of

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A machine learning approach to predict mortality and neonatal persistent pulmonary hypertension in newborns with congenital diaphragmatic hernia. A retrospective observational cohort study

Luana Conte, Ilaria Amodeo, Giorgio De Nunzio, Genny Rafaeli, Irene Borzani, Nicola Persico, Alice Griggio, Giuseppe Como, Mariarosa Colnaghi, Monica Fumagalli, Donato Cascio, Giacomo CavallaroUniversità Degli Studi Di Palermo. Fondazione IRCCS Ca’ Granda Ospedale Maggiore Policlinico. Laboratory of Interdisciplinary Research Applied to Medicine (DReAM). “E. De Giorgi”, University of Salento. Università Degli Studi Di Milano.

A machine learning approach to predict mortality and neonatal persistent pulmonary hypertension in newborns with congenital diaphragmatic hernia. A retrospective observational cohort study Read More »

Prevalence and outcomes of air leak syndrome and subtypes in neonates in the United States

Adam Beaton, Prithvi Sendi, Paul A. Martinez, Balagangadhar R. TotapallyCohen Children’s Medical Center. Nicklaus Children’s Hospital. Florida International University. United States Journal of Neonatal-Perinatal MedicineJ Neonatal Perinatal Med 2025; 17: 846-857DOI: 10.1177/19345798241308491 AbstractObjectives: To describe the prevalence, risk factors, and outcomes for neonatal air leak syndrome and its subtypes (pneumothorax, pneumomediastinum, pneumopericardium, pulmonary interstitial emphysema, and pneumoperitoneum), evaluate variables associated with the development

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Fetoscopic Endoluminal Tracheal Occlusion-Synergic Therapies in the Prenatal Treatment of Congenital Diaphragmatic Hernia

Zsolt Bara, Horea Gozar, Nándor Nagy, Simona Gurzu, Zoltán Derzsi, Timea Forró, Evelyn Kovács, Ioan JungGeorge Emil Palade University of Medicine, Pharmacy, Science and Technology of Targu Mures. County Emergency Clinical Hospital. Semmelweis University. Romanian Academy of Medical Sciences.Romania and Hungary International Journal of Molecular SciencesInt J Mol Sci 2025; 26: DOI: 10.3390/ijms26041639 AbstractCongenital diaphragmatic hernia

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Growing Up with Developmental Lung Diseases: A Review for the Adult Pulmonologist

Yadira Rivera-Sanchez, Zachary W. Blair, Tyler J. Wall, Kara N. GossUniversity of Texas Southwestern Medical Center.United States ChestChest 2025; DOI: 10.1016/j.chest.2025.02.014 AbstractTopic importance: Improved childhood management strategies have decreased the early life morbidity and mortality of severe developmental lung disorders, such that an increasing number of individuals ultimately transition care to adult pulmonologists for management. Alternatively, individuals

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