Class 1. Pulmonary Hypertension Associated with Congenital Cardiovascular Disease

Sotatercept in Patients With Eisenmenger Syndrome

Oktay Tutarel, Oliver Miera, Felix BergerDeutsches Herzzentrum der Charité, Freie Universität Berlin and Humboldt-Universität zu Berlin.Germany Pulmonary CirculationPulm Circ 2026; 16: DOI: 10.1002/pul2.70283 AbstractEisenmenger syndrome represents a complex and severe form of pulmonary arterial hypertension (PAH) associated with congenital heart disease. Sotatercept, a first-in-class activin-signaling inhibitor, offers a novel therapeutic approach in the treatment of PAH, […]

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Reversing the irreversible? A case of successful surgical repair in a late-presenting aortopulmonary window with severe pulmonary hypertension

Rido Mulawarman, Ericko Ongko Joyo, Muhamad Adrin Aefiansyah Putra, Aditya Agita Sembiring, Sisca Natalia Siagian, Oktavia LilyasarUniversitas Indonesia. Indonesia Egyptian Heart JournalEgypt Heart J 2026; 78: DOI: 10.1186/s43044-026-00726-7 AbstractBackground: Aortopulmonary window (APW) is a rare congenital heart defect, accounting for only 0.2-0.6% of all congenital cardiac anomalies, and is usually identified and surgically corrected within the first

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A Combination Of Vein Of Galen Aneurysmal Malformation And Bovine Aortic Arch In Newborn: A Case Report

Krishna Deo Mandal, Kalpana Subedi, Unnati Amatya, Janak PathakParopakar Maternity and Women’s Hospital. Embassy of India.Nepal Journal of the Nepal Medical AssociationJ Nepal Med Assoc 2025; 63: 347-349DOI: 10.31729/jnma.8987 AbstractVein of Galen aneurysmal malformation is a rare intracranial arteriovenous malformation, coexistence with aortic arch anomalies is even more uncommon, carry high risk of morbidity and mortality

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Systematic Review of the Application of Pulmonary Hypertension Treatments in Ventricular Septal Defect, Pulmonary Atresia, and Major Aortopulmonary Collateral Arteries

Keiichi Hirono, Keiko Uchida, Taku Ishii, Hidekazu Ishida, Shinichi Takatsuki, Hiroyuki Fukushima, Kei Inai, Susumu Hosokawa, Reina Ishizaki, Hirofumi Sawada, Naofumi F. Sumitomo, Ayako Chida-Nagai, Yuichi Ishikawa, Hirohiko Motoki, Atsushi Yao, Shigetoyo Kogaki, Hiroyuki Yamagishi, Shozaburo DoiToyama University Hospital. Tokyo Medical University. Institute of Science Tokyo. Osaka University Graduate School of Medicine. Toho University, Omori

Systematic Review of the Application of Pulmonary Hypertension Treatments in Ventricular Septal Defect, Pulmonary Atresia, and Major Aortopulmonary Collateral Arteries Read More »

Association Between Hemodynamic Parameters and Gut Microbiota in Fontan Circulation: A Cross-Sectional Study

Saviga Sethasathien, Chanon Kunasol, Suchaya Silvilairat, Rekwan Sittiwangkul, Pannipa Suwannasom, Nipon Chattipakorn, Krit Leemasawat, Siriporn C. ChattipakornChiang Mai University. Thailand Journal of the American Heart AssociationJ Am Heart Assoc 2026; DOI: 10.1161/JAHA.125.045962 AbstractBackground: The Fontan operation results in chronic hemodynamic alterations, including central venous hypertension, which may contribute to gut dysbiosis. This study aimed to compare gut

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Microbiome-Metabolome Axis in BALF Reveals Novel Diagnostic Biomarkers for Congenital Heart Disease-Associated Pulmonary Arterial Hypertension

Xiaoyu Zhang, Liming Cheng, Yuan Zhou, Jiahui Xie, Wenting Gui, Jiaxiang Chen, Zidan Zhang, Kai Liu, Runwei MaFuwai Yunnan Hospital, Chinese Academy of Medical Sciences, Affiliated Cardiovascular Hospital of Kunming Medical University. Kunming Children’s Hospital.China Journal of Cardiovascular Development and DiseaseJ Cardiovasc Dev Dis 2026; 13: DOI: 10.3390/jcdd13010032 AbstractBackground: Early identification of irreversible pulmonary vascular remodeling in

Microbiome-Metabolome Axis in BALF Reveals Novel Diagnostic Biomarkers for Congenital Heart Disease-Associated Pulmonary Arterial Hypertension Read More »

Infant with Complex Congenital Cardiac Anomalies: A Case Report and Review of Literature

Aliasgar Taha, Abdullah Ahmed Tariq, Yusur Abbas Mahmood, Leah Leslie Dias, Rahul Binu, Subhranshu Sekhar Kar, Alaa Mohamad HussainRas Al Khaimah Medical and Health Sciences University.United Arab Emirits Annals of African MedicineAnn Afr Med 2026; DOI: 10.4103/aam.aam_631_25 AbstractThe coexistence of multiple complex congenital cardiac anomalies in a single infant – particularly unbalanced Atrioventricular Septal Defect; Double

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Outcome in patients with secundum type atrial septal defect – a single centre experience

Johanna Gorenflo, Victoria Ziesenitz, Mina Farag, Tsvetomir Loukanov, Matthias GorenfloUniversity Medical Centre Mannheim. Heidelberg University. Germany The Thoracic and Cardiovascular SurgeonThorac Cardiovasc Surg 2026; DOI: 10.1055/a-2786-1128 AbstractThis single centre retrospective analysis presents data from 611 patients with ASD closure. Included were patients > 2 years of age. Patients presented at a median [range] age of 6,95

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Navigating the Unique Challenge of Pulmonary Hypertension From Left-to-Right PDA Shunts in Two Cases of Congenital Diaphragmatic Hernia

John T. Wren, Jr., Rhucha Joshi, Patrick J. McNamaraUniversity of Iowa Healthcare. Children’s Hospital of Orange County. United States EchocardiographyEchocardiography 2026; 43: DOI: 10.1111/echo.70396 AbstractPulmonary hypertension (PH) in congenital diaphragmatic hernia (CDH) is nearly universal yet incredibly complex. A patent ductus arteriosus (PDA) is increasingly utilized to both monitor echocardiographically and manage CDH-PH. However, as pulmonary

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Pulmonary arterial hypertension after congenital heart defect correction: a call for timely diagnosis and careful risk stratification to improve outcomes

Qiangqiang Li, Yuan He, Andrew Constantine, Konstantinos Dimopoulos, Chen Zhang, Qiang Wang, Hong GuBeijing Anzhen Hospital and Capital Medical University. Queen Elizabeth Hospital Birmingham and University Hospitals Birmingham NHS Foundation Trust. Royal Brompton Hospital and Royal Brompton and Harefield NHS Foundation Trust. Imperial College London.China and United Kingdom European Heart Journal OpenEur Heart J Open

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