Class 1. Pulmonary Hypertension Associated with Congenital Cardiovascular Disease

Characteristics of exercise intolerance in different subgroups of pulmonary arterial hypertension associated with congenital heart disease

Hong-Da Zhang, Yi Yan, Yang-Yang He, Qian-Qian Liu, Fu-Hua Peng, Xin-Xin Yan, Zhi-Yan HanFuwai Hospital and Chinese Academy of Medical Sciences & Peking Union Medical College. Shanghai Children’s Medical Center, National Children’s Medical Center and Shanghai Jiaotong University School of Medicine. Henan University. China International Journal of CardiologyInt J Cardiol 2023; 375: 29-35DOI: 10.1016/j.ijcard.2022.12.033 AbstractBackground: Exercise intolerance […]

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Vein of Galen aneurysmal malformation: rationalizing medical management of neonatal heart failure

Melinda Cory, Phillippe Durand, Rafael Sillero, Luc Morin, Rashmin Savani, Lina Chalak, Dimitrios AngelesThe University of Texas Southwestern Medical Center. Paris-Saclay University Hospitals, Bicêtre Medical Centre and Assistance Publique-Hospitaux de Paris.United States and France Pediatric ResearchPediatr Res 2023; 93: 39-48DOI: 10.1038/s41390-022-02064-1 AbstractNeonates who present in high output heart failure secondary to vein of Galen aneurysmal malformation

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Differential biventricular adaption to pulmonary vascular disease in patients with idiopathic/heritable and congenital heart disease: a prospective cardiac magnetic resonance and invasive study

Zhuoyuan Xu, Ruiyu Dou, Zhen Zhou, Hongsheng Zhang, Chen Zhang, Qiangqiang Li, Lei Xu, Hong GuBeijing Anzhen Hospital and Capital Medical University. China European Heart Journal Cardiovascular ImagingEur Heart J Cardiovasc Imag 2023; DOI: 10.1093/ehjci/jead106 AbstractAims: Despite shared pathophysiological mechanisms, patients with idiopathic/heritable pulmonary arterial hypertension (IPAH/HPAH) have a poorer prognosis than those with PAH after congenital

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Outcomes in Patients with Pulmonary Arterial Hypertension Underwent Transcatheter Closure of an Atrial Septal Defect

Jae-Hee Seol, Se-Yong Jung, Han-Byul Lee, Ah-Young Kim, Eun-Hwa Kim, In-Kyung Min, Nam-Kyun Kim, Jae-Young ChoiSeverance Cardiovascular Hospital and Yonsei University College of Medicine. Yonsei University Wonju College of Medicine. Soonchunhyang University College of Medicine. Republic of Korea Journal of Clinical MedicineJ Clin Med 2023; 12:DOI: 10.3390/jcm12072540 AbstractPulmonary arterial hypertension (PAH) related to an atrial septal

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Endothelin inhibitors lower pulmonary vascular resistance and improve functional capacity in patients with Fontan circulation

Gabriella Agnoletti, Simona Gala, Francesca Ferroni, Roberto Bordese, Lorenzo Appendini, Carlo Pace Napoleone, Laura BergamascoCitta’ della Salute e della Scienza. Italy Journal of Thoracic and Cardiovascular SurgeryJ Thorac Cardiovasc Surg 2017; 153: 1468-1475DOI: 10.1016/j.jtcvs.2017.01.051 AbstractObjectives: To evaluate the effects of endothelin inhibitors (ERAs) on hemodynamic and functional parameters in patients post-Fontan procedure with high pulmonary vascular resistance

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Assessment of the effect of two regimens of milrinone infusion in paediatric patients with pulmonary artery hypertension undergoing corrective cardiac procedure: A prospective observational study

Mrugesh Prajapati, Jigar Patel, Hasmukh Patel, Hemang Gandhi, Guriqbal Singh, Pravin PatelU.N. Mehta Institute of Cardiology and Research CenterIndia Annals of Pediatric CardiologyAnn Pediatr Cardiol 2022; 15: 358-363DOI: 10.4103/apc.apc_230_21 AbstractBackground: The aim of the study was to compare the effect of two different regimens of milrinone in pediatric patients with pulmonary artery hypertension (PAH) undergoing corrective procedure.Materials

Assessment of the effect of two regimens of milrinone infusion in paediatric patients with pulmonary artery hypertension undergoing corrective cardiac procedure: A prospective observational study Read More »

Plasma mid-regional proadrenomedullin level in children with pulmonary hypertension associated with CHD

Shimaa A. Elesawy, Hesham A. El-Serogy, Esraa A. Sorour, Amr M. Zoairar Elsalam General Hospital and Ministry of Health. Tanta University. Egypt Cardiology in the YoungCardiol Young 2023; DOI: 10.1017/S1047951123000471 AbstractAdrenomedullin has been shown to inhibit proliferation in pulmonary artery smooth muscle cells and to alleviate pulmonary artery collagen accumulation in pulmonary hypertension. We aimed to

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Congenital Portosystemic Shunts in Children: Associations, Complications, and Outcomes

Frank DiPaola, Andrew T. Trout, Ashley E. Walther, Anita Gupta, Rachel Sheridan, Kathleen M. Campbell, Greg Tiao, Jorge A. Bezerra, Kevin E. Bove, Manish Patel, Jaimie D. NathanC.S. Mott Children’s Hospital. Cincinnati Children’s Hospital Medical Center. University of Cincinnati Medical Center. Children’s Hospital Los Angeles.United States Digestive Diseases and SciencesDig Dis Sci 2020; 65: 1239-1251DOI: 10.1007/s10620-019-05834-w

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Pulmonary Hypertension in Infants and Children with Vein of Galen Malformation and Association with Clinical Outcomes

Jai Khurana, Darren B. Orbach, Kimberlee Gauvreau, Shane A. Collins, Joseph B. Tella, Pankai B. Agrawal, Helen A. Christou, Mary P. MullenBoston Children’s Hospital, Boston. Harvard Medical School. Brigham & Women’s Hospital.United States Journal of PediatricsJ Pediatr 2023; DOI: 10.1016/j.jpeds.2023.113404 AbstractObjective: To assess the extent and resolution of pulmonary hypertension (PH), cardiovascular factors, and echocardiographic findings associated

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Case Report: Selexipag in pediatric pulmonary hypertension: Initiation, transition, and titration

Jenna M. Faircloth, Neelam D. Bhatt, Corey A. Chartan, Ryan D. Coleman, Natalie Villafranco, Fadel E. Ruiz, Raysa Morales-Demori, Elise Whalen, Erin Ely, Rozmeen Fombin, Nidhy P. VargheseTexas Children’s Hospital and Baylor College of Medicine.United States Frontiers in PediatricsFront Pediatr 2023; 11: DOI: 10.3389/fped.2023.1050508 AbstractSelexipag, a selective prostacyclin receptor agonist, is approved for treating pulmonary arterial

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