Class 1. Pulmonary Hypertension Associated with Congenital Cardiovascular Disease

Expanding the phenotypic spectrum of NOTCH1 variants: clinical manifestations in families with congenital heart disease

Kaitlin J. Stanley, Kelsey J. Kalbfleisch, Olivia M. Moran, Rajiv R. Chaturvedi, Maian Roifman, Xin Chen, Roozbeh Manshaei, Nicole Martin, Simina McDermott, Vanda McNiven, Diane Myles-Reid, Lynne E. Nield, Miriam S. Reuter, Marci L. B. Schwartz, Patrick Shannon, Rachel Silver, Cherith Somerville, Ronni Teitelbaum, Laura Zahavich, Anne S. Bassett, Raymond H. Kim, Seema Mital, David […]

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Effect of phosphodiesterase type 5 inhibitors on surgical outcome of ventricular septal defect and pulmonary hypertension patients

Khaled Ahmed Shams, Dalia Monir Ellahony, Ahmed Fouad Halima, Rania Salah ElzayatHelwan University. Magdi Yacoub Foundation. Menoufia University.Egypt Egypt Heart JournalEgypt Heart J 2024; 76:DOI: 10.1186/s43044-024-00475-5 AbstractBackground: Children with ventricular septal defect (VSD) and large systemic-to-pulmonary shunts eventually develop pulmonary hypertension (PH). The perioperative management of patients with VSD and PH is quite troublesome and still debatable,

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Management of Pulmonary Vascular Disease Associated with Congenital Left to Right Shunts: A Single Center Experience

Hythem Nawaytou, Ramya Lakkaraju, Leah Stevens, Vadiyala Mohan Reddy, Naveen Swami, Roberta L. Keller, David F. Teitel, Jeffrey R. FinemanUniversity of California,San Francisco.United States Journal of Thoracic and Cardiovascular SurgeryJ Thorac Cardiovasc Surg 2024; DOI: 10.1016/j.jtcvs.2024.05.007 AbstractObjective: To describe the course and outcomes of children under 18 with left-to-right (LR) shunts and pulmonary arterial hypertension (PAH) undergoing

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Case Series of Berry syndrome: A rare constellation of fatal cardiac anomalies

Kevin Moses Hanky Jr Tandayu, Yovi Kurniawati, Indriwanto Sakidjan Atmosudigdo, Oktavia LilyasariNational Cardiovascular Centre Harapan Kita and Universitas Indonesia.Indonesia Annals of Pediatric CardiologyAnn Pediatr Cardiol 2023; 16: 374-377DOI: 10.4103/apc.apc_109_23 AbstractBerry syndrome is an extremely rare constellation of several congenital cardiac anomalies consisting of aortopulmonary window, aortic origin of the right pulmonary artery (AORPA), interrupted aortic arch

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Survival and outcomes of isolated neonatal ventricular septal defects: A population-based study from a middle-income country

Mohd Nizam Mat Bah, Mohd Hanafi Sapian, Mohd Hazman Mohd Anuar, Emieliyuza Yusnita AliasHospital Sultanah Aminah.Malaysia Annals of Pediatric CardiologyAnn Pediatr Cardiol 2023; 16: 322-330DOI: 10.4103/apc.apc_130_23 AbstractBackground and aims: Limited data on the survival and outcomes of ventricular septal defect (VSD) in middle-income countries are available. Hence, this study aims to determine the survival and factors associated

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Therapeutic effects of treat and repair strategy in pediatric patients with pulmonary arterial hypertension and simple congenital heart defects

Xiaofeng Wang, Shilin Wang, Zhongyuan Lu, Wenlong Wang, Xu WangFuWai Hospital Chinese Academy of Medical Sciences and Peking Union Medical College.China Pulmonary CirculationPulm Circ 2024; 14: DOI: 10.1002/pul2.12387 AbstractSurgical indications for patients with pulmonary arterial hypertension (PAH) and congenital heart defects are controversial. The treat and repair strategy has demonstrated efficacy in adult populations, but there

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Interventional heart catheterization to close atrial septal defect, patent ductus arteriosus, ventricular septal defect in a 3.5-year-old girl; a case report study

Zahra Kamiab, Reza DerakhshanRafsanjan University of Medical Sciences. Kerman University of Medical Sciences.Iran Journal of Surgigal Case ReportsJ Surg Case Rep 2024; DOI: 10.1093/jscr/rjae161 AbstractThe aim of this study was to introduce an interventional heart catheterization to close patent ductus arteriosus (PDA), ventricular septal defect (VSD), atrial septal defect (ASD), and pulmonary hypertension without complications from

Interventional heart catheterization to close atrial septal defect, patent ductus arteriosus, ventricular septal defect in a 3.5-year-old girl; a case report study Read More »

The prognostic value of prognostic nutritional index in postoperative onset of PAH in children with isolated VSD: a prospective cohort study based on propensity score matching analysis

Zeying Zhang, Jing Su, Chenyang Li, Shirui Cao, Chao Sun, Qiuzhen Lin, Haiyan Luo, Zhenghui Xiao, Yunbin Xiao, Qiming LiuSecond Xiangya Hospital of Central South University. Hunan Children’s Hospital. China Frontiers in PediatricsFront Pediatr 2024; 12:DOI: 10.3389/fped.2024.1292786 AbstractBackground: The mechanism of pulmonary arterial hypertension (PAH) after surgery/intervention for isolated venticlular septal defect (VSD) in children is unknown.

The prognostic value of prognostic nutritional index in postoperative onset of PAH in children with isolated VSD: a prospective cohort study based on propensity score matching analysis Read More »

Successful Atrial Septal Defect Closure Subsequent to Medical Pulmonary Preconditioning in an Infant With Severe Pulmonary Hypertension Associated With Bronchopulmonary Dysplasia

Maki Sato, Hirofumi Saiki, Kanchi Saito, Akira Sato, Seiko Kuwata, Satoshi Nakano, Junichi Koizumi, Kotaro Oyama, Manami AkasakaIwate Medical University. Michinoku Medical Center on Disability and Health.Japan CureusCureus 2024; 16: DOI: 10.7759/cureus.57290 AbstractWhile atrial septal defect (ASD) may contribute to right ventricular decompression in patients with severe pulmonary hypertension (PH), the pulmonary vasculature might be compromised

Successful Atrial Septal Defect Closure Subsequent to Medical Pulmonary Preconditioning in an Infant With Severe Pulmonary Hypertension Associated With Bronchopulmonary Dysplasia Read More »

A Bioinformatic Algorithm based on Pulmonary Endoarterial Biopsy for Targeted Pulmonary Arterial Hypertension Therapy

Abraham Rothman, David Mann, Jose A. Nunez, Reinhardt Tarmidi, Humberto Restrepo, Valeri Sarukhanov, Roy Williams, William N. EvansChildren’s Heart Center Nevada. Kirk Kerkorian School of Medicine at UNLV. Vascular Biosciences. University of California, Santa Barbara. University of California, San Diego.United States Open Respiratory Medicine JournalOpen Respir Med J 2023; DOI: 10.2174/18743064-v17-230927-2023-9 AbstractBackground: Optimal pharmacological therapy for pulmonary

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