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Characterisation of paediatric pulmonary hypertensive vascular disease from the PPHNet Registry

Steven H. Abman, Mary P. Mullen, Lynn A. Sleeper, Eric D. Austin, Erika B. Rosenzweig, John P. Kinsella, D. Dunbar Ivy, Rachel K. Hopper, J. Usha Raj, Jeffrey Fineman, Roberta L. Keller, Angela Bates, Usha S. Krishnan, Catherine M. Avitabile, Alexander Davidson, Marc D. Natter, Kenneth D. MandlPediatric Pulmonary Hypertension NetworkUnited States and Canada European Respiratory JournalEur Respir J 2021; DOI: 10.1183/13993003.03337-2020 ExtractBackground: There are limited data about the range of diseases, natural history, age-appropriate end-points and optimal care for children with pulmonary hypertension (PH), including the need for developing […]

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Pregnancy outcomes of women with Eisenmenger syndrome: A single-center study

Yang Liu, Hong Gu, Yanna Li, Jun Zhang, Xiangming Fan, Yichen Zhao, Jiangang WangBeijing Anzhen Hospital affiliated to Capital Medical University. Hebei General Hospital. Zhejiang Children’s Hospital. China International Journal of CardiologyInt J Cardiol 2023; 374: 35-41DOI: 10.1016/j.ijcard.2022.12.014 AbstractBackground: To explore the outcomes of mothers with Eisenmenger syndrome (ES) and their offspring.Methods: Pregnant women with ES admitted to

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Novel variants of seryl-tRNA synthetase resulting in HUPRA syndrome featured in pulmonary hypertension

Fan Yang, Dan Wang, Xuehua Zhang, Haoqin Fan, Yu Zheng, Zhenghui Xiao, Zhi Chen, Yunbin Xiao, Qiming LiuSecond Xiangya Hospital and Central South University. Hunan Children’s Hospital. Fujian Children’s Hospital and Fujian Medical University.China Frontiers in Cardiovascular MedicineFront Cardiovasc Med 2023; DOI: 10.3389/fcvm.2022.1058569 AbstractHyperuricemia, pulmonary hypertension, and renal failure in infancy and alkalosis syndrome (HUPRA syndrome)

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Hemodynamic Characterization of Neonates With Congenital Diaphragmatic Hernia-Associated Pulmonary Hypertension by Cardiac Catheterization

Paula Dias Maia, Jason Gien, John P. Kinsella, Jenny Zablah, Gareth Morgan, D. Dunbar Ivy, Steven H. Abman, Benjamin S. FrankUniversity of Colorado School of Medicine.United States Journal of PediatricsJ Pediatr 2022; DOI: 10.1016/j.jpeds.2022.11.028 AbstractWe examined the results of cardiac catheterization in infants with congenital diaphragmatic hernia (CDH) from 2009 to 2020. Catheterization confirmed pulmonary arterial

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The Oxygen Saturation Index as Early Predictor of Outcomes in Congenital Diaphragmatic Hernia

Emily J. J. Horn-Oudshoorn, Marijn J. Vermeulen, Ronny Knol, Arjan B. te Pas, Suzan C. M. Cochius-den Otter, J. Marco Schnater, Irwin K.M. Reiss, Philip L. J. DeKoninckErasmus MC University Medical Center. Leiden University Medical Center. Netherlands NeonatologyNeonatology 2023; 120: 63-70DOI: 10.1159/000527407 AbstractObjective: The aim of the study was to evaluate the oxygen saturation index (OSI) as

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Fetal endoscopic tracheal occlusion for moderate and severe congenital diaphragmatic hernia: a systematic review and meta-analysis of randomized controlled trials

Qiyu Li, Siyuan Liu, Xuemei Ma, Jiaping YuGeneral Hospital of Northern Theater Command. China Pediatric Surgery InternationalPediatr Surg 2022; 38: 1217-1226 DOI: 10.1007/s00383-022-05170-7 AbstractBackground: Fetoscopic endoluminal tracheal occlusion (FETO) is considered to increase survival among fetuses with congenital diaphragmatic hernia (CDH). Data from high-quality trials had been lacking until the largest randomized controlled trials (the TOTAL trials)

Fetal endoscopic tracheal occlusion for moderate and severe congenital diaphragmatic hernia: a systematic review and meta-analysis of randomized controlled trials Read More »

A Measurement-Based Protocol Improves Interrater Agreement and Accuracy of Right Ventricular Systolic Pressure Assessment by Echocardiography in Children: A Call for Quality Improvement

Hythem Nawaytou, Christine Springston, Ann Lazar, Samuel Keller, Whitnee Hogan, Nicole Cresalia, Shabnam Peyvandi, Mark Cocalis, Anita Moon-Grady, Michael BrookUniversity of California, San Francisco.United States Journal of the American Society of EchocardiographyJ Am Soc Echocardiogr 2022; 35: 1091-1100DOI: 10.1016/j.echo.2022.06.014 AbstractBackground: Echocardiographic measurements carry the promise of improving interrater (IR) agreement over subjective assessment. The aim of this

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Worsened short-term clinical outcomes in a cohort of patients with iNO-unresponsive PPHN: a case for improving iNO responsiveness

Julie Dillard, Leeann R. Pavlek, Saichidroopi Korada, Bernadette ChenSt. Louis University. Nationwide Children’s Hospital and Ohio State University.United States Journal of PerinatologyJ Perinatol 2022; 42: 37-44DOI: 10.1038/s41372-021-01228-x AbstractObjectives: To identify distinguishing characteristics of neonates with persistent pulmonary hypertension of the newborn (PPHN) unresponsive to inhaled nitric oxide (iNO) and evaluate the use of milrinone in this cohort.Study

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Association of the dysfunctional placentation endotype of prematurity with bronchopulmonary dysplasia: a systematic review, meta-analysis and meta-regression

Maria Pierro, Eduardo Villamor-Martinez, Elke van Westering- Kroon, Maria Alvarez-Fuente, Steven H Abman, Eduardo VillamorMaastricht University Medical Centre. Maurizio Bufalini Hospital. Hospital Universitario Ramón y Cajal. University of Colorado – Anschutz Medical Campus. Netherlands, Italy, Spain and United States ThoraxThorax 2022; 77: 268-275DOI: 10.1136/thoraxjnl-2020-216485 AbstractBackground: Antenatal pathological conditions are key in the pathogenesis of bronchopulmonary dysplasia (BPD).

Association of the dysfunctional placentation endotype of prematurity with bronchopulmonary dysplasia: a systematic review, meta-analysis and meta-regression Read More »

Adenosine reverses life-threatening persistent pulmonary hypertension of the neonate refractory to triple vasodilator therapy

Lucie Genet, Daniele De Luca“A.Béclère” Medical Center and Paris Saclay University Hospitals.France Cardiology in the YoungCardiol Young 2022; 32: 996-997DOI: 10.1017/S1047951121004157 AbstractPersistent pulmonary hypertension of the neonate can cause acute and life-threatening hypoxia, but preterm neonates are not suitable candidate to extra-corporeal life support. We report the unique case of an extremely preterm neonates with life-threatening

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