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Factors associated with the response to postnatal dexamethasone use in very low birthweight infants: a nationwide cohort study

Seung Hwan Baek, Jeong Eun Shin, Jungho Han, In Gyu Song, Joonsik Park, Su Min Lee, Sungbo Shim, Ho Seon Eun, Soon Min Lee, Joohee Lim, So Jin Yoon, Wook Chang, Min Soo ParkSeverance Hospital. Gangnam Severance Hospital. Yongin Severance Hospital. Republic of Korea British Medical Journal Paediatrics OpenBMJ Paediatr Open 2023;DOI: 10.1136/bmjpo-2023-002302 AbstractBackground: Dexamethasone is widely

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Cardiovascular complications of sickle cell disease: A primer for the general clinician

Chibuzo Ilonze, Gift C. Echefu, Alexandria L. Broadnax, Adedoyin Johnson, Aniekeme Etuk, Onyedika J. IlonzeUniversity of Alabama at Birmingham. University of Tennessee Health Science Center. Indiana University School of Medicine. Infirmary Health Thomas Hospital.United States Journal of the National Medical AssociationJ Natl Med Assoc 2023;DOI: 10.1016/j.jnma.2023.11.010 AbstractSickle cell disease (SCD) is the most common hereditary hemoglobinopathy

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LRP4 site-specific variants in the third β-propeller domain causes congenital myasthenic syndrome type 17

Tariq Al Jabry, Nadia Al-Hashmi, Basem Abdelhadi, Almundher Al-MaawaliSultan Qaboos University Hospital. Royal Hospital.Oman European Journal of Medical GeneticsEir J Med Genet 2023;DOI: 10.1016/j.ejmg.2023.104903 AbstractLRP4 is expressed in many organs. It mediates SOST-dependent inhibition of bone formation and acts as an inhibitor of WNT signaling. It is also a postsynaptic end plate cell surface receptor at

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Lung transplant is a viable treatment option for patients with congenital and acquired pulmonary vein stenosis

Ankit Bharat, Deidre J. Epstein, Mark Grady, Albert Faro, Peter Michelson, Stuart C. Sweet, Charles B. HuddlestonWashington University.United States Journal of Heart and Lung TransplantationJ Heart Lung Transplant 2013; 32: 621-625DOI: 10.1016/j.healun.2013.03.002 AbstractBackground: Congenital pulmonary vein stenosis (PVS) is associated with high mortality because surgical repair is usually not feasible or is ineffective. In addition, acquired PVS

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Surgery for pulmonary venous obstruction after repair of total anomalous pulmonary venous return

Francois Lacour-GayetDenver Children’s Hospital and University of Colorado.United States Seminars in Thoracic and Cardiovascular Surgery Pediatric Cardiac Surgery AnnualSemin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2006; 9: 45-50DOI: 10.1053/j.pcsu.2006.02.010 AbstractThe major complication and the main cause of reoperation following surgery for total anomalous pulmonary venous return (TAPVR) is the occurrence of pulmonary venous obstruction. Outcomes

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Acute recoil of stents used for the relief of stenotic great vessels in the setting of congenital cardiac disease

Hideshi Tomita, Satoshi Yazaki, Kohji Kimura, Ken Watanabe, Kinya Hatakeyama, Yasuo Ono, Shigeyuki EchigoNational Cardiovascular Center.Japan Cardiology in the YoungCardiol Young 2003; 13: 519-525DOI: Not Available AbstractWe implanted either large or medium Palmaz stents, or a Palmaz Corinthian stent, in various stenotic vessels, such as the pulmonary arteries, pulmonary veins, aorta, or superior caval vein.

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Never Say Never: The Use of Nitric Oxide in Patients With Obstructed Pulmonary Veins: A Case Report

Victoria Sokoliuk, James A. DiNardo, Morgan L. BrownBoston Children’s Hospital.United States A and A PracticeA A Pract 2019; 12: 205-207DOI: 10.1213/XAA.0000000000000885 AbstractPulmonary vein stenosis (PVS) is a progressive disease with pulmonary hypertension (PH) as a major cause of morbidity and mortality. Traditional management of PH with inhaled nitric oxide (iNO) is typically avoided in PVS patients

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The impact of right ventricular pressure and function on survival in patients with pulmonary vein stenosis

Michelle C. Sykes, Christina Ireland, Julia E. McSweeney, Emily Rosenholm, Kristofer G. Andren, Thomas J. KulikBoston Children’s Hospital.United States Pulmonary CirculationPulm Circ 2018;DOI: 10.1177/2045894018776894 AbstractPulmonary vein stenosis (PVS) is associated with pulmonary hypertension (PH), but there is little information regarding the impact of PH on right ventricular (RV) systolic function and survival. We conducted a retrospective

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How is pulmonary arterial blood flow affected by pulmonary venous obstruction in children? A phase-contrast magnetic resonance study

Kevin S. Roman, Christian Kellenberger, Christopher K. Macgowan, John Coles, Andrew N. Reddington, Lee N. Benson, Shi-Joon YooHospital for Sick Children.Canada Pediatric RadiologyPediatr Radiol 2005; 35: 580-586DOI: 10.1007/s00247-004-1399-x AbstractBackground: Hemodynamic changes within a stenosed pulmonary vein might not reflect the severity of the obstruction if redistribution of pulmonary artery flow occurs.Objective: The purpose was to investigate flow changes

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Gadolinium-enhanced three-dimensional magnetic resonance angiography of pulmonary and systemic venous anomalies

Gerald F. Greil, Andrew J. Powell, Hans P. Gildein, Tal GevaChildren’s Hospital, Boston.United States Journal of the American College of CardiologyJ Am Coll Cardiol 2002; 39: 335-341DOI: 10.1016/s0735-1097(01)01730-2 AbstractObjective: The goal of this study was to evaluate the diagnostic value of gadolinium (Gd)-enhanced three-dimensional (3D) magnetic resonance angiography (MRA) in patients with congenital and acquired anomalies of

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