All Categories

Systemic sclerosis sine scleroderma in children is more aggressive than in adults

Francesca Tirelli, Elisabetta Zanatta, Beatrice Moccaldi, Marco Binda, Giorgia Martini, Chiara Giraudo, Fabio Vittadello, Alessandra Meneghel, Francesco ZulianUniversity of Padova. Italy RheumatologyRheumatology 2024; DOI: 10.1093/rheumatology/keae304 AbstractObjectives: To compare the clinical and laboratory features of pediatric systemic sclerosis sine scleroderma (ssJSSc) with adult-onset ssSSc.Methods: Demographic, clinical and laboratory data of ssJSSc, retrospectively retrieved from our hospital medical records, case

Systemic sclerosis sine scleroderma in children is more aggressive than in adults Read More »

Right Atrial Strain in Pediatric Pulmonary Hypertension-A Prospective Observational Study

Subhrashis Guha Niyogi, Avneet Singh, Bhupesh Kumar, Anand Kumar Mishra, Goverdhan Dutt PuriAll India Institute of Medical Sciences. Government Medical College and Hospital. Post Graduate Institute of Medical Education and Research. India Pediatric CardiologyPediatr Cardiol 2024; DOI: 10.1007/s00246-024-03523-8 AbstractRight ventricular (RV) afterload due to elevated pulmonary arterial (PA) pressure in pulmonary hypertension (PH) causes long-term right

Right Atrial Strain in Pediatric Pulmonary Hypertension-A Prospective Observational Study Read More »

Expanding the phenotypic spectrum of NOTCH1 variants: clinical manifestations in families with congenital heart disease

Kaitlin J. Stanley, Kelsey J. Kalbfleisch, Olivia M. Moran, Rajiv R. Chaturvedi, Maian Roifman, Xin Chen, Roozbeh Manshaei, Nicole Martin, Simina McDermott, Vanda McNiven, Diane Myles-Reid, Lynne E. Nield, Miriam S. Reuter, Marci L. B. Schwartz, Patrick Shannon, Rachel Silver, Cherith Somerville, Ronni Teitelbaum, Laura Zahavich, Anne S. Bassett, Raymond H. Kim, Seema Mital, David

Expanding the phenotypic spectrum of NOTCH1 variants: clinical manifestations in families with congenital heart disease Read More »

Interstitial macrophage phenotypes in Schistosoma-induced pulmonary hypertension

Rahul Kumar, Sushil Kumar, Claudia Mickael, Dara Fonseca Balladares, Kevin Nolan, Michael H. Lee, Linda Sanders, Julia Nilsson, Ari B. Molofsky, Rubin M. Tuder, Kurt R. Stenmark, Brian B. GrahamUniversity of California, San Francisco and Zuckerberg San Francisco General Hospital. University of Colorado Anschutz Medical Campus. United States Frontiers in ImmunologyFront Immunol 2024; DOI: 10.3389/fimmu.2024.1372957 AbstractBackground: Schistosomiasis

Interstitial macrophage phenotypes in Schistosoma-induced pulmonary hypertension Read More »

Effect of phosphodiesterase type 5 inhibitors on surgical outcome of ventricular septal defect and pulmonary hypertension patients

Khaled Ahmed Shams, Dalia Monir Ellahony, Ahmed Fouad Halima, Rania Salah ElzayatHelwan University. Magdi Yacoub Foundation. Menoufia University.Egypt Egypt Heart JournalEgypt Heart J 2024; 76:DOI: 10.1186/s43044-024-00475-5 AbstractBackground: Children with ventricular septal defect (VSD) and large systemic-to-pulmonary shunts eventually develop pulmonary hypertension (PH). The perioperative management of patients with VSD and PH is quite troublesome and still debatable,

Effect of phosphodiesterase type 5 inhibitors on surgical outcome of ventricular septal defect and pulmonary hypertension patients Read More »

3D Imaging Reveals Complex Microvascular Remodeling in the Right Ventricle in Pulmonary Hypertension

Kenzo Ichimura, Mario Boehm, Adam M. Andruska, Fan Zhang, Katharina Schimmel, Spencer Bonham, Angela Kabiri, Vitaly O. Kheyfets, Shoko Ichimura, Sushma Reddy, Yuqiang Mao, Tianyi Zhang, Gordon Wang, Everton J. Santana, Xuefei Tian, Ilham Essafri, Ryan Vinh, Wen Tian, Mark R. Nicolls, Shin Yajima, Yasuhiro Shudo, John W. McArthur, Y. Joseph Woo, Ross J. Metzger,

3D Imaging Reveals Complex Microvascular Remodeling in the Right Ventricle in Pulmonary Hypertension Read More »

Management of Pulmonary Vascular Disease Associated with Congenital Left to Right Shunts: A Single Center Experience

Hythem Nawaytou, Ramya Lakkaraju, Leah Stevens, Vadiyala Mohan Reddy, Naveen Swami, Roberta L. Keller, David F. Teitel, Jeffrey R. FinemanUniversity of California,San Francisco.United States Journal of Thoracic and Cardiovascular SurgeryJ Thorac Cardiovasc Surg 2024; DOI: 10.1016/j.jtcvs.2024.05.007 AbstractObjective: To describe the course and outcomes of children under 18 with left-to-right (LR) shunts and pulmonary arterial hypertension (PAH) undergoing

Management of Pulmonary Vascular Disease Associated with Congenital Left to Right Shunts: A Single Center Experience Read More »

Case Series of Berry syndrome: A rare constellation of fatal cardiac anomalies

Kevin Moses Hanky Jr Tandayu, Yovi Kurniawati, Indriwanto Sakidjan Atmosudigdo, Oktavia LilyasariNational Cardiovascular Centre Harapan Kita and Universitas Indonesia.Indonesia Annals of Pediatric CardiologyAnn Pediatr Cardiol 2023; 16: 374-377DOI: 10.4103/apc.apc_109_23 AbstractBerry syndrome is an extremely rare constellation of several congenital cardiac anomalies consisting of aortopulmonary window, aortic origin of the right pulmonary artery (AORPA), interrupted aortic arch

Case Series of Berry syndrome: A rare constellation of fatal cardiac anomalies Read More »

Survival and outcomes of isolated neonatal ventricular septal defects: A population-based study from a middle-income country

Mohd Nizam Mat Bah, Mohd Hanafi Sapian, Mohd Hazman Mohd Anuar, Emieliyuza Yusnita AliasHospital Sultanah Aminah.Malaysia Annals of Pediatric CardiologyAnn Pediatr Cardiol 2023; 16: 322-330DOI: 10.4103/apc.apc_130_23 AbstractBackground and aims: Limited data on the survival and outcomes of ventricular septal defect (VSD) in middle-income countries are available. Hence, this study aims to determine the survival and factors associated

Survival and outcomes of isolated neonatal ventricular septal defects: A population-based study from a middle-income country Read More »

The Estimated Fick Method Systematically Over-Estimates Cardiac Index Compared to Thermodilution in Children

Andrew A. Lawson, Paul Tannous, Christina Laternser, Karl MigallyAnn & Robert H. Lurie Children’s Hospital of Chicago and Northwestern University Feinberg School of Medicine. United States Pediatric CardiologyPediatr Cardiol 2024; DOI: 10.1007/s00246-024-03491-z AbstractCardiac index (CI) may be derived from the Fick method, using measured or estimated oxygen consumption (VO2), or from thermodilution. In children, LaFarge VO2 estimates

The Estimated Fick Method Systematically Over-Estimates Cardiac Index Compared to Thermodilution in Children Read More »

Scroll to Top