Adult Pulmonary Vascular Disease

Dysregulated Tricarboxylic Acid Cycle Metabolism Is Associated With Right Ventricular Maladaptation in Pulmonary Vascular Disease

Darin T. Rosen, Todd M. Kolb, Stephen C. Mathai, Karthik Suresh, Rachel Damico, Steven Hsu, Ryan J. Tedford, Anna R. Hemnes, Jane A. Leopold, Evelyn M. Horn, Erika S. Berman‐Rosenzweig, Franz Rischard, Robert P. Frantz, Serpil C. Erzurum, Gerald J. Beck, Nicholas S. Hill, John Barnard, Samar Farha, Gabriele Grunig, Christine Jellis, Deborah H. Kwon, Reena Mehra, Margaret M. Park, W. H. Wilson Tang, Paul M. Hassoun, Catherine E. Simpson, the PVDOMICS Study GroupJohns Hopkins University. University of Miami, Medical University of South Carolina. Vanderbilt University. Brigham and Women’s Hospital. Cornell University Medical Center. Westchester Medical Center and New […]

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Hemodynamic rounds: Transcatheter creation of ventricular septal defect in pulmonary arterial hypertension with suprasystemic pressures

Kothandam SivakumarMadras Medical Mission.India Annals of Pediatric CardiologyAnn Pediatr Cardiol 2024; 17: 448-454DOI: 10.4103/apc.apc_211_24 AbstractThis hemodynamic round section deals with severe pulmonary arterial hypertension with suprasystemic pulmonary artery pressures in a patient who underwent delayed surgical correction of the double-outlet right ventricle with a large subaortic ventricular septal defect (VSD). Recreation of a moderate-sized VSD by

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Tet Methylcytosine Dioxygenase 2 (TET2) Mutation Drives a Global Hypermethylation Signature in Patients With Pulmonary Arterial Hypertension (PAH): Correlation With Altered Gene Expression Relevant to a Common T Cell Phenotype

Charles C. T. Hindmarch, Francois Potus, Ruaa Al-Qazazi, Benjamin P. Ott, William C. Nichols,Michael J. Rauh, Stephen L. ArcherQueen’s University. Universitaire de Cardiologie et de Pneumologie de Québec. Cincinnati Children’s Hospital Medical Center and University of Cincinnati College of Medicine.Canada and United States Comprehensive PhysiologyCompr Physiol 2025; 15: DOI: 10.1002/cph4.70011 AbstractEpigenetic changes in gene expression due

Tet Methylcytosine Dioxygenase 2 (TET2) Mutation Drives a Global Hypermethylation Signature in Patients With Pulmonary Arterial Hypertension (PAH): Correlation With Altered Gene Expression Relevant to a Common T Cell Phenotype Read More »

Altered maturation and activation state of circulating monocytes is associated with their enhanced recruitment in pulmonary arterial hypertension

Rebecca L. Harper, Xin Zhou, David P. Marciano, Aiqin Cao, Lingli Wang, Guibin Chen, Mir S. Adil, Wenyu Zhou, Peter Maguire, Shanthi Deivanayagam, Quan Yu, Vignesh Viswanathan, Dan Yang, Marcy Martin, Sarasa Isobe, Shoichiro Otsuki, Jordan Burgess, Audrey Inglis, Devon Kelley, Patricia A. del Rosario, Andrew Hsi, Francois Haddad, Roham T. Zamanian, Manfred Boehm, Michael

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Cardiopulmonary Exercise Testing With Forehead and Popliteal Oximetry in Evaluating Efficacy of Reverse Potts Shunt

Keti Mamillo, Robert P. Frantz, Jason H. Anderson, Thomas G. AllisonMayo Clinic.United States Journal of the American College of Cardiology Case ReportsJACC Case Rep 2025; 30: DOI: 10.1016/j.jaccas.2025.103409 AbstractReverse Potts shunt (rPS) is a surgical procedure that creates an anastomosis between the left pulmonary artery and descending aorta to decompress the right ventricle in suprasystemic pulmonary

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Iatrogenic esophageal dysmotility as a barrier to transplantation in pulmonary arterial hypertension

Michael S. Miller, Shelsey W. Johnson, Alexander R. Opotowsky, Michael J. Landzberg, Nirmal S. Sharma, Hilary J. Goldberg, Alexandra K. Wong, Alison S. Witkin, Josanna Rodriguez-Lopez, Ronald H. Goldstein, Bradley A. Maron, Bradley M. WertheimBrigham and Women’s Hospital, Boston Children’s Hospital and Harvard Medical School. Veterans Affairs Boston Healthcare System. University of Cincinnati School of

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Outcomes of the lateral caval flap and conventional techniques for repair of right-sided partial anomalous pulmonary venous connection in adults

William C. Frankel, Bogdan A. Kindzelski, Benjamin Yang, Rashed Mahboubi, Miza Salim Hammoud, Andrew J. Toth, Hani K. Najm, Gösta B. Pettersson, Tara KaramlouCleveland Clinic. Corewell East William Beaumont University Hospital. United States Journal of Thoracic and Cardiovascular Surgery OpenJTCVS Open 2025; 23: 225-234DOI: 10.1016/j.xjon.2024.10.023 AbstractObjective: In an effort to overcome limitations of conventional techniques for surgical

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Temporal changes in prevalence and severity of pulmonary hypertension, and relationship to outcomes in coarctation of aorta

Ahmed Younis, Yogesh N. V. Reddy, William R. Miranda, Ahmed T. Abdelhalim, Barry A. Borlaug, Heidi M. Connolly, Alexander C. EgbeMayo Clinic.United States International Journal of Cardiology Heart and VasculatureInt J Cardiol Heart Vasc 2025; 57: DOI: 10.1016/j.ijcha.2025.101626 AbstractBackground: Pulmonary hypertension (PH) affects 20% of adults with coarctation of aorta (COA). What is not known is whether

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The prediction value of serum anion gap for short-term mortality in pulmonary hypertension patients with sepsis: a retrospective cohort study

Jinhua Zhu, Zeying Zhang, Yefei Lei, Zhenrong Ouyang, Shelby Kutty, Qiming Liu, Yunbin XiaoFirst People’s Hospital of Chenzhou and Hunan Children’s Hospital Affiliated to Jinan University. Xiamen Cardiovascular Hospital of Xiamen University. Johns Hopkins School of Medicine. Second Xiangya Hospital and Affiliated Children’s Hospital of Central South University. China Frontiers in MedicineFront Med 2025; 11: DOI: 10.3389/fmed.2024.1499677 AbstractBackground: The

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Pulmonary Arterial Hypertension Incidence in Scleroderma Patients Treated with Bosentan for Digital Ulcers: Evidence from the Italian SPRING Registry

Fabio Cacciapaglia, Rossella De Angelis, Clodoveo Ferri, Gianluigi Bajocchi, Silvia Bellando-Randone, Cosimo Bruni, Martina Orlandi, Marco Fornaro, Edoardo Cipolletta, Giovanni Zanframundo, Roberta Foti, Giovanna Cuomo, Alarico Ariani, Edoardo Rosato, Gemma Lepri, Francesco Girelli, Elisabetta Zanatta, Silvia Laura Bosello, Ilaria Cavazzana, Francesca Ingegnoli, Maria De Santis, Giuseppe Murdaca, Giuseppina Abignano, Pettiti Giorgio, Alessandra Della Rossa, Maurizio Caminiti, Annamaria Iuliano, Giovanni Ciano, Lorenzo Beretta, Gianluca Bagnato, Ennio Lubrano, Ilenia De Andres, Alessandro Giollo, Marta Saracco, Cecilia Agnes, Corrado Campochiaro, Federica Lumetti, Amelia Spinella, Luca Magnani, Giacomo De Luca, Veronica Codullo, Elisa Visalli, Carlo Iandoli, Antonietta Gigante, Greta Pellegrino, Franco Cozzi, Maria Grazia Lazzaroni, Elena

Pulmonary Arterial Hypertension Incidence in Scleroderma Patients Treated with Bosentan for Digital Ulcers: Evidence from the Italian SPRING Registry Read More »

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