Unilateral absence or extreme hypoplasia of pulmonary veins

H. M. Kingston, R. G. Patel, G. H. Watson
Royal Manchester Children’s Hospital.
United Kingdom

British Heart Journal
Brit Heart J 1983; 49: 148-153
DOI: 10.1136/hrt.49.2.148

Abstract
Three children with recurrent chest symptoms and signs caused by unilateral atresia or absence of the pulmonary veins are described, with a discussion of the seven reported cases of unilateral congenital pulmonary venous obstruction. The condition is rare but should enter into the differential diagnosis of recurrent unilateral pulmonary infection or oedema. Pulmonary arteriography is necessary and pulmonary artery wedge angiography is the most informative diagnostic procedure.

Category
Class II. Pulmonary Hypertension Associated with Pulmonary Vein Stenosis
Symptoms and Findings Associated with Pulmonary Vascular Disease
Diagnostic Testing for Pulmonary Vascular Disease. Invasive Testing
Pulmonary Vascular Pathology

Age Focus: Pediatric Pulmonary Vascular Disease

Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication

Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: Yes

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