Emine Gülsah Torun, Denizhan Bagrul, Ibrahim Ece
Ankara Bilkent City Hospital.
Turkey
Cardiology in the Young
Cardiol Young 2025;
DOI: 10.1017/S1047951125001374
Abstract
Pulmonary arterial hypertension remains a progressive, life-threatening condition despite advances in medical treatments. We report the first case of the interventional creation of a reverse Potts shunt by stenting a closed ductus arteriosus in a four-year-old child with right ventricular failure due to suprasystemic pulmonary arterial hypertension associated with Von Hippel-Lindau disease, unresponsive to triple anti-pulmonary arterial hypertension therapy. Following the procedure, the patient’s clinical status and echocardiographic systolic and diastolic right ventricular function improved.
Category
Surgical and Catheter-mediated Interventions for Pulmonary Vascular Disease
Genetic Factors Associated with Pulmonary Vascular Disease
Age Focus: Pediatric Pulmonary Vascular Disease
Fresh or Filed Publication: Fresh (PHresh). Less than 1-2 years since publication
Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: No