Pulmonary Hypertension in Congenital Heart Disease: A Scientific Statement From the American Heart Association

Pei-Ni Jone, D. Dunbar Ivy, Amanda Hauck, Tara Karamlou, Uyen Truong, Ryan D. Coleman, Juan Pablo Sandoval, María Jesús del Cerro Marín, Pirooz Eghtesady, Kathryn Tillman, Usha S. Krishnan
Lurie Children’s Hospitaland Northwestern University. University of Colorado. Cleveland Clinic Foundation. Children’s National Hospital. Texas Children’s Hospital and Baylor College of Medicine. Ignacio Chavez National Institute of Cardiology. Hospital Universita-rio Ramon y Cajal. Washington University School of Medicine. Medical College of Wisconsin and Children’s Wisconsin. Columbia University Medical Center/New York Presbyterian Hospital.
United States, Mexico and Spain

Circulation Heart Failure
Circ Heart Fail 2023;
DOI: 10.1161/HHF.0000000000000080

Abstract
Patients with pulmonary hypertension associated with congenital heart disease make up an increasing proportion of the total pulmonary hypertension population who bring with them added complexity because of underlying anatomical and hemodynamic abnormalities. Currently, no consensus recommendations are available on how to best manage this group of patients for either the primary cardiologist or pulmonary hypertension subspecialist, including timing of referral. The purposes of this document are (1) to describe the various pulmonary hypertension groups and subgroups associated with congenital heart disease, (2) to describe imaging modalities used in patient evaluation, (3) to elucidate medical and surgical management considerations, (4) to highlight disparities within this population, and (5) to identify gaps and future research needs of patients with pulmonary hypertension associated with congenital heart disease.

Category
Review Articles Concerning Pulmonary Vascular Disease
Class I. Pulmonary Hypertension Associated with Congenital Cardiovascular Disease

Age Focus: Pediatric Pulmonary Vascular Disease

Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication

Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: Yes

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