Ali H. Mashadi, Yasin Essa & Sameh M. Said
Maria Fareri Children’s Hospital and Westchester Medical Center.
United States
Multimedia Manual of Cardio-Thoracic Surgery
Multimed Man Cardiothorac Surg 2025;
DOI: 10.1510/mmcts.2024.117
Abstract
A 3-month-old, 5.2-kg infant with Williams syndrome presented with failure to thrive and a systolic murmur. He was taken to the cardiac catheterization laboratory for a planned pulmonary valvotomy based on findings of severe pulmonary stenosis on the transthoracic echocardiogram. However, he suffered cardiac arrest and had to be resuscitated; the procedure was aborted. Cardiac catheterization revealed suprasystemic right ventricular pressure and severe bilateral branch pulmonary artery stenosis with bilateral branch hypoplasia. The decision was made to proceed with surgical relief of the obstruction.
Category
Segmental Pulmonary Arterial Disease
Genetic Factors Associated with Pulmonary Vascular Disease
Symptoms and Findings Associated with Pulmonary Vascular Disease
Age Focus: Pediatric Pulmonary Vascular Disease
Fresh or Filed Publication: Fresh (PHresh). Less than 1-2 years since publication
Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: Yes