Sarosh P. Batlivala, Amr Matoq, Shabana Shahanavaz
University of Cincinnati College of Medicine and Cincinnati Children’s Hospital Medical Center.
United States
World Journal of Pediatric and Congenital Heart Surgery
World J Pediatr Congenit Heart Surg 2023;
DOI: 10.1177/21501351231162958
Abstract
Microvascular pulmonary arteriovenous malformations (pAVMs) can lead to profound hypoxemia. “Hepatic factor” is postulated to play a role in their development. Certain patients with congenital heart disease are at particular risk to develop pAVMs, including those with heterotaxy syndromes and complex Fontan palliation. Ideally, an underlying cause is identified and corrected, although pAVMs may persist despite those interventions. We report a patient with heterotaxy syndrome s/p Fontan who had pAVMs that persisted despite Fontan revision with equal hepatic flow to both lungs. We employed a novel method to produce a diabolo configuration of a large covered stent to restrict lung flow while maintaining the potential for future dilation.
Category
Pulmonary Arteriovenous Malformations
Surgical and Catheter-mediated Interventions for Pulmonary Vascular Disease
Age Focus: Pediatric Pulmonary Vascular Disease
Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication
Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: No