Che‑Chih Cheng, Ming‑Tai Lin, Shu‑Chien Huang, Hsao‑Hsun Hsu
Kaohsiung Armed Forces General Hospital. National Taiwan University Hospital and National Taiwan University College of Medicine.
Taiwan
Journal of Cardiothoracic Surgery
J Cardiothorac Surg 2022; 17:
DOI: 10.1186/s13019-022-01792-z
Abstract
Background: Profound pulmonary arterial hypertension with end-stage right heart failure is considered to be the main cause of death in children with un-repaired congenital heart disease, and the traditional surgical treatment is heart-lung transplantation. We performed bilateral lung transplantation (LTx) with concomitant cardiac repair, and the patient has uplifting outcome.
Case presentation: We have reported the case of a patient with congenital hypoplasia of the bilateral pulmonary arteries and patent ductus arteriosus. The patient’s clinical condition was gradually worsening and severely limited his ability to perform the activities of daily life. Bilateral LTx with concomitant patent ductus arteriosus repair was performed at the age of 11 years. The postoperative course was smooth and cardiopulmonary function nearly returned to normal according to radiological and laboratory examinations.
Conclusions: Bilateral LTx with concomitant cardiac repair may be superior to heart-lung transplantation in the case of the specific congenital heart disease.
Category
Segmental Pulmonary Arterial Disease
Lung Transplantation for Pulmonary Vascular Disease
Age Focus: Pediatric Pulmonary Vascular Disease
Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication
Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: Yes