Isolated pulmonary vein stenosis in complex congenital heart disease, simulating cor triatriatum by cardiac catheterization and transoesophageal echocardiography

A. H. Cromme-Diijkhuis, A. J. Bogers, J. Hess
Sophia Children’s Hospital and University Hospital.
Netherlands

European Heart Journal
Eur Heart J 1995; 16: 287-288
DOI: 10.1093/oxfordjournals.eurheartj.a060900

Abstract
A case of localized stenosis of the lower left pulmonary vein, associated with perimembranous ventricular septal defect (VSD) and secundum atrial defect (ASD), a borderline sized mitral valve apparatus and left ventricle, is described. This final diagnosis was made at surgery, as the localized stenosis of the left pulmonary vein was misinterpreted as partial cor triatriatum by cardiac catheterization, cineangiocardiography and extensive echocardiographic studies. Surgical correction of all the defects was successful, but pulmonary vascular resistance was still increased 2 years after surgery.

Category
Segmental Pulmonary Venous Disease. Without a Focus on Pulmonary Hypertension

Age Focus: Pediatric Pulmonary Vascular Disease

Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication

Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: No

Scroll to Top