Isolated agenesis of the right pulmonary veins with pulmonary sequestration

Shilpa Patil, Sakshi Sachdeva, Shweta Bakhru, Bharat Dalvi, Nageswara Rao Koneti
Care Hospital. Glenmark Cardiac Center.
India

Annals of Pediatric Cardiology
Ann Pediatr Cardiol 2019; 12: 135-137
DOI: 10.4103/apc.APC_55_18

Abstract
We report two cases of agenesis of the right pulmonary veins (PVs) associated with sequestration of the right lung with systemic to pulmonary collateral. Both the children were referred for evaluation of recurrent lower respiratory tract infections. Transthoracic echocardiographic evaluation showed reversal of flow in the right pulmonary artery (PA) and absent right PVs. Cardiac catheterization confirmed the diagnosis of agenesis of the right PVs. Transcatheter closure of collaterals was performed in view of significant shunt from systemic to PA. Both the patients are asymptomatic on follow-up.

Category
Segmental Pulmonary Venous Disease. Without a Focus on Pulmonary Hypertension
Abnormal Systemic to Pulmonary Arterial Collaterals or Connections
Surgical and Catheter-mediated Interventions for Pulmonary Vascular Disease

Age Focus: Pediatric Pulmonary Vascular Disease

Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication

Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: Yes

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