Arkadi M. Rywlin, Rita M. Fojaco
University of Miami.
United States
Pediatrics
Pediatrics 1968; 41: 931–934
https://doi.org/10.1542/peds.41.5.931
Abstract
Three main theories have to be considered in the pathogenesis of congenital pulmonary lymphangectasis: obstruction of major pulmonary lymphatics, obstruction to pulmonary venous flow, and anomalous pulmonary development. The authors report an infant with congenital pulmonary lymphangiectasis associated with a blind common pulmonary vein. Previously reported cases of congenital pulmonary lymphangiectasis associated with cardiac lesions causing obstruction to pulmonary venous flow are reviewed. This association appears too frequently to be merely coincidental. Obstruction to pulmonary venous flow provides a cause for the persistence of prominent fetal lymphatic channels and thus seems of pathogenetic importance in some cases of congenital pulmonary lymphangiectasis.
Category
Segmental Pulmonary Venous Disease. Without a Focus on Pulmonary Hypertension
Pulmonary Lymphatic Disease
Age Focus: Pediatric Pulmonary Vascular Disease
Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication
Article Access
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