Congenital portosystemic shunt with multiple splenic artery aneurysms: Reversing pulmonary hypertension and preventing aneurysm rupture

Anand P. Subramanian, Adaligere Paraswanath Bharath, Ashita Barthur, Mahimarangaiah Jayranganath
Sri Jayadeva Institute of Cardiovascular Sciences and Research
India

Annals of Pediatric Cardiology
Ann Pediatr Cardiol 2022; 15: 300-303
DOI: 10.4103/apc.apc_142_21

Abstract
We report an unusual occurrence of multiple splenic artery aneurysms and splenomegaly in a young woman with severe pulmonary hypertension, secondary to a congenital portosystemic shunt (CPS). The splenic artery was occluded using an Amplatzer Duct Occluder-II device, and closure of the large intrahepatic CPS was achieved using a muscular ventricular septal defect occluder. There was resolution of splenomegaly with normal pulmonary artery pressures, a few months after the procedure.

Category
Class I. Pulmonary Hypertension Associated with Liver Disease
Class I. Pulmonary Hypertension Associated with Cardiovascular Heart Disease
Surgical and Catheter-mediated Interventions for Pulmonary Vascular Disease

Age Focus: Pediatric Pulmonary Vascular Disease or Adult Pulmonary Vascular Disease

Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication

Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: Yes

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