Pulmonary Arteriovenous Malformations

Dermatologic findings in hereditary hemorrhagic telangiectasia: association with epistaxis, visceral involvement, and genetics

Andrea Michelerio, Giuseppe Spinozzi, Chiara Giorgini, Carla Olivieri, Annalisa de Silvestri, Fabio Pagella, Camilla VassalloUniversity of Pavia. Fondazione IRCCS Policlinico San Matteo. Italy Italian Journal of Dermatology and VenereologyItal J Dermatol Venereol 2025; DOI: 10.23736/S2784-8671.25.08225-8 AbstractBackground: Hereditary hemorrhagic telangiectasia (HHT) is a genetic vascular disorder characterized by epistaxis, mucocutaneous telangiectasias, and visceral arteriovenous malformations (AVMs). Despite the […]

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Pulmonary vascular complications in children who survive long-term after Kasai portoenterostomy for biliary atresia: a narrative review

Jie Zhang, Gong ChenChildren’s Hospital of Fudan University.China World Journal of Pediatric SurgeryWorld J Pediatr Surg 2025; 8: DOI: 10.1136/wjps-2025-001067 AbstractFollowing Kasai portoenterostomy for biliary atresia (BA), long-term survival in children is associated with chronic liver cirrhosis leading to hepatopulmonary syndrome (HPS) and portopulmonary hypertension (PoPH). This further causes a diverse array of respiratory and circulatory

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Vascular and Non-Vascular Intervention in the Pediatric Chest: An Update

Sunit Davda, Ajit Yadav, Manish Patel, Matt HawkinsGreat Ormond Street Hospital. Sir Ganga Ram Hospital. Cincinnati Children’s Hospital Medical Center. Emory University School of Medicine and Children’s Healthcare of Atlanta.United Kingdom, India and United States CardioVascular and Interventional RadiologyCardiovasc Interv Radiol 2025; DOI: 10.1007/s00270-025-04226-0 AbstractIn pediatric patients, thoracic intervention can involve aerodigestive tract, pleura, pulmonary parenchymal,

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Reduced-Dose Chest CTA for the Detection of Pulmonary Arteriovenous Malformations in Pediatric Patients With Hereditary Hemorrhagic Telangiectasia

Zaid Saadeh, Nadir Demirel, Kelly Horst, Vivek Iyer, Chi Wan Koo, Nicholas B. Larson, Cynthia H. McCollough, Daniel Oo, Yasmeen Tandon, Jamison Thorne, Zhongxing Zhou, Lifeng Yu, Nate C. HullMayo ClinicUnited States Journal of Computer Assisted TomographyJ Comput Assist Tomogr 2025; DOI: 10.1097/RCT.0000000000001804 AbstractObjectives: To determine the feasibility of reduced-dose chest computed tomographic angiography (CTA) with convolutional

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Prolidase Deficiency Presenting With Pulmonary Arteriovenous Malformations and Seizures: Report of Two Cases From Iran

Ali Pajouhi, Rouhollah Rohani, Vahid Ziaee, Mohammad Shahrooei, Zeinab Paymani, Bahar Amiri, Mohammadreza ModaresiLorestan University of Medical Sciences. Children’s Medical Center and Tehran University of Medical Sciences. Pediatric Rheumatology Society of Iran. KU Leuven. Dr. Shahrooei Lab.Iran and Belgium Case Reports in PediatricsCase Rep Pediatr 2025; DOI: 10.1155/crpe/9929135 AbstractProlidase deficiency (PD) is a rare autosomal recessive

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Clinical practice variability among paediatric interventional cardiologists assessing pulmonary arteriovenous malformations

Joshua Fields, Jared Boon, Osama Aldoss, Susan R. Foerster, Todd M. Gudausky, Stephen B. Spurgin, Andrew D. SpearmanMedical College of Wisconsin and Children’s Wisconsin. University of Texas Southwestern Medical Center.United States Cardiology in the YoungCardiol Young 2025; DOI: 10.1017/S1047951125110019 AbstractBackground: Single ventricle pulmonary arteriovenous malformations are poorly understood and variably assessed in published literature. To improve our

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Incidence and risk factors for the development of pulmonary arteriovenous malformations after stage 2 palliation

Lea Behrend, Thibault Schaeffer, Muneaki Matsubara, Jonas Palm, Teresa Lemmen, Nicole Piber, Paul Philipp Heinisch, Stanimir Georgiev, Alfred Hager, Peter Ewert, Jürgen Horer, Masamichi OnoUniversity Hospital of Technische Universität München, University Hospital of Munich and Ludwig-Maximilians-Universität.Germany International Journal of Cardiology Congenital Heart DiseaseInt J Cardiol Congenit Heart Dis 2025; DOI: 10.1016/j.ijcchd.2025.100611 AbstractObjective: This study evaluated the current

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Turner syndrome with pulmonary arteriovenous malformation: a case report

Huibin Guo, Hongqiao Chen, Sihao Chen, Shilong TangUniversity-Town Hospital of Chongqing Medical University. Children’s Hospital of Chongqing Medical University.China Frontiers in Cardiovascular MedicineFront Cardiovasc Med 2025; 12: DOI: 10.3389/fcvm.2025.1603250 AbstractTurner syndrome (TS) is the most common sex chromosome abnormality disorder, caused by complete or partial absence of the X chromosome, its clinical manifestations primarily include short

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Successful Treatment of Severe Hepatopulmonary Syndrome as a Rare Complication of Zellweger Spectrum Disorder

Riya Mary Tharakan, Sanjay Rajwal, Bernd C. SchwahnSt Mary’s Hospital Manchester University NHS Foundation Trust. Leeds Children’s Hospital. Medicine and Health University of Manchester. United Kingdom Journal of Inherited Metabolic Disorders ReportsJIMD Rep 2025; DOI: 10.1002/jmd2.70026 AbstractWe report the case of an 11-year-old girl who developed hepatopulmonary syndrome (HPS) as a rare complication of Zellweger spectrum

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Chronic cyanosis since infancy: Unveiling a giant right pulmonary arteriovenous malformation

Dian Komalaa, Harry Galuh Nugrahaa, Firman Ramadhana, Rais Khairuddina, Rahmat Budi Kuswiyantob, Putria Rayani ApandiUniversitas Padjadjaran.Indonesia Radiology Case ReportsRadiol Case Rep 2025; 20: 5353-5356DOI: 10.1016/j.radcr.2025.06.084 AbstractGiant pulmonary arteriovenous malformations (PAVMs) are rare vascular anomalies involving direct connections between pulmonary arteries and veins, leading to right-to-left shunting and systemic hypoxemia. While small PAVMs may be asymptomatic, larger

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