Pulmonary Arteriovenous Malformations

Pulmonary arteriovenous malformation with unexplained cyanosis as the first presentation of hereditary haemorrhagic telangiectasia, case report, and literature review

Ali Alakhfash, Abdullah Alqwaiee, Abdulrahman Almesned, Zuhair N. Al-HassnanPrince Sultan cardiac Center-Qassim. Sapienza Università di Roma. King Faisal Specialist Hospital & Research Centre. Saudi Arabia and Italy European Heart Journal Case ReportsEur Heart J Case Rep 2021; 22: DOI: 10.1093/ehjcr/ytab261 AbstractBackground: Pulmonary arteriovenous malformations (PAVMs) are rare pulmonary vascular anomalies. They can result in right-to-left shunt and, […]

Pulmonary arteriovenous malformation with unexplained cyanosis as the first presentation of hereditary haemorrhagic telangiectasia, case report, and literature review Read More »

Pulmonary arterial hypertension associated with pulmonary arteriovenous malformations and pulmonary veno-occlusive disease: A devastating combination

Baukje M. Zaaijera, Nienke Duppena, Brigitte W. M. Willemseb, Martijn V. Verhagenc, Marcus T. R. Roofthoofta, WimT imensd, Rolf M. F. Bergera, Johannes M. DouwesUniversity of Groningen, University Medical Center Groningen, Beatrix Children’s Hospital.Netherlands Respiratory Medicine Case ReportsRespir Med Case Rep 2021; 34: DOI: 10.1016/j.rmcr.2021.101564 AbstractWe describe a case of an adolescent male with the rare

Pulmonary arterial hypertension associated with pulmonary arteriovenous malformations and pulmonary veno-occlusive disease: A devastating combination Read More »

Pulmonary Arteriovenous Malformations Incidentalloma in a 10-Years-Old Child

Daoud Ali Mohamed, Amarkak Waiss, Behyamet Onka, Walid Mohamed, Nazik Allali, Latifa Chat, Siham El HaddadUniversity Hospital of Ibn Sina Rabat. Morroco Global Pediatric HealthGlob Pediatr Health 2021; 3: DOI: 10.1177/2333794X211051186 AbstractPulmonary Arteriovenous Malformations (PAVMs) are structurally abnormal vascular communications between pulmonary arteries and pulmonary veins, which bypass the normal capillary bed and cause a low

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Preservation of Antegrade Pulmonary Blood Flow in Kawashima Procedure With Prior Right Ventricular Outflow Tract Stent

Suneet Bhansali, Puneet Bhatla, Michael Argilla, Sunil Saharan, Ralph Mosca, Tk Susheel KumarLangone Medical Center.United States World Journal of Pediatric and Congenital Heart SurgeryWorld J Pediatr Congenit Heart Surg 2022; 13: 521-523DOI: 10.1177/21501351221080171 AbstractSurgical management of single ventricle with interrupted inferior vena cava and azygos continuation typically requires a Kawashima procedure with subsequent completion of Fontan.

Preservation of Antegrade Pulmonary Blood Flow in Kawashima Procedure With Prior Right Ventricular Outflow Tract Stent Read More »

Pearls & Oy-sters: Cerebral Abscess Secondary to Pulmonary Arteriovenous Malformation in Hereditary Hemorrhagic Telangiectasia

Jodie I. Roberts, Kristine Woodward, Adam Kirton, Michael J. EsserUniversity of Calgary; Alberta Children’s Hospital Research Institute.Canada NeurologyNeurology 2022; 98: 292-295DOI: 10.1212/WNL.0000000000013181 AbstractHereditary hemorrhagic telangiectasia (HHT) is an autosomal dominant condition that is linked to a myriad of neurologic complications arising from vascular malformations of the brain, spinal cord, and lungs. Our case describes a previously

Pearls & Oy-sters: Cerebral Abscess Secondary to Pulmonary Arteriovenous Malformation in Hereditary Hemorrhagic Telangiectasia Read More »

Three-dimensional rotational angiography utility in imaging and intervention in a case of pulmonary arteriovenous malformation

Neeraj Awasthy, Amol GuptaMax Hospital.India Annals of Pediatric CardiologyAnn Pediatr Cardiol 2021; 14: 533-535DOI: 10.4103/apc.APC_111_18 AbstractPulmonary arteriovenous malformation (PAVM) is an abnormal communication between the pulmonary artery and the pulmonary vein. PAVMs are usually congenital in origin; however, they may be acquired. Three-dimensional rotational angiography (3DRA) is a technique used increasingly for imaging in congenital heart

Three-dimensional rotational angiography utility in imaging and intervention in a case of pulmonary arteriovenous malformation Read More »

Hepatic factor may not originate from hepatocytes

Monica Merbach, Ramani Ramchandran, Andrew D. SpearmanMedical College of Wisconsin and Children’s Wisconsin.United States Frontiers in Cardiovascular MedicineFront Cardiovasc Med 2022; DOI: 10.3389/fcvm.2022.999315 AbstractPulmonary arteriovenous malformations (PAVMs) develop universally in patients with univentricular congenital heart disease. They are believed to form due to lack of an unidentified factor from hepatocytes that perfuses the lungs to maintain

Hepatic factor may not originate from hepatocytes Read More »

Hypoxia and Polycythemia: A Pediatric Emergency Department Point of Care Ultrasound Diagnosis of Pulmonary Arteriovenous Malformation

Shachar Oren, Shachar, Galit Brenner, Yael Garty, Eric ScheierKaplan Medical Center. Hebrew University of Jerusalem.Israel Pediatric Emergency CarePediatr Emerg Car 2022; 38: 633-635DOI: 10.1097/PEC.0000000000002721 AbstractPoint of care ultrasound (POCUS) can be useful in the differentiation between cardiac and pulmonary etiologies of hypoxia. Here, we present a child with signs of chronic hypoxia, found on POCUS to

Hypoxia and Polycythemia: A Pediatric Emergency Department Point of Care Ultrasound Diagnosis of Pulmonary Arteriovenous Malformation Read More »

Pulmonary arteriovenous malformations: A case of missed diagnosis in a neonate

Zurina Zainudin, Nadiah Azlisham, Ghee Tiong Koh, Yinn Khurn Ooi, Melissa Anne NunisUniversiti Putra Malaysia. Hospital Pakar Sultanah Fatimah. Hospital Serdang.Malaysia Medical Journal of MalaysiaMed J Malaysia 2022; 77: 274-276DOI: Not available AbstractPulmonary arteriovenous malformation (PAVM) is a congenital vascular abnormality that can cause persistent cyanosis in children. PAVMs can go undetected till adulthood; however,

Pulmonary arteriovenous malformations: A case of missed diagnosis in a neonate Read More »

Brain Abscess and Stroke in Children and Adults With Hereditary Hemorrhagic Telangiectasia: Analysis of a Large National Claims Database

Andrew J. White, Itay Marmor, Kate M. Peacock, Katelin B. Nickel, Jessica Zavadil, Margaret A. OlsenSaint Louis University School of Medicine. Washington University School of Medicine.United States NeurologyNeurology 2023; DOI: 10.1212/WNL.0000000000207269 AbstractObjective: Hereditary hemorrhagic telangiectasia (HHT) is an inherited disease associated with pathogenic variants in TGF-β signaling pathway-related genes, resulting in abnormal vascular development in various organs.

Brain Abscess and Stroke in Children and Adults With Hereditary Hemorrhagic Telangiectasia: Analysis of a Large National Claims Database Read More »

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