Filed (PHiled). Greater than 1-2 years since publication

Arteriovenous Malformations-Current Understanding of the Pathogenesis with Implications for Treatment

Katharina Schimmel, Khadem Ali, Serena Y. Tan, Joyce Teng, Huy M. Do, Gary K. Steinberg, David A. Stevenson, Edda SpiekerkoetterStanford University. Lucile Packard Children’s Hospital. United States International Journal of Molecular SciencesInt J Mol Sci 2021; 22: DOI: 10.3390/ijms22169037 AbstractArteriovenous malformations are a vascular anomaly typically present at birth, characterized by an abnormal connection between an […]

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Congenital lymphatic dysplasia and severe bone disease in a term neonate with a novel homozygous PIEZO1 variant

Elizabeth H. Ketchum, Charles L. Groomes, Alexis N. Ghersi, Brian B. Graziose, Sharen C. Wilson, Sidney E. Zven, Rebecca L. Hicks, William A. Langley, Michael A. Reott Jr,. John P. Schacht, Elizabeth V. Schulz, Jerri CurtisUniformed Services University. Walter Reed National Military Medical Center. MNG Laboratories.United States Clinical Case ReportsClin Case Rep 2024; 12: DOI: 10.1002/ccr3.9082

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Magnification pulmonary wedge angiography in the evaluation of children with congenital heart disease and pulmonary hypertension

Michael R. Nihill, Dan G. McNamaraBaylor College of Medicine and Texas Children’s Hospital.United States CirculationCirculation 1978; 58: 1094-1106DOI: 10.1161/01.cir.58.6.1094 AbstractIn order to determine the presence and extent of obstructive pulmonary vascular disease in pa-tients with congenital heart disease, magnified cineangiograms were obtained with a catheter in the pulmonary artery wedge position in 155 infants and children

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Bronchial arteries to right pulmonary artery anastomoses in right pulmonary vein atresia

J. Fred Johnson, Andrew L Juris, Edith Valerie BarnesTripler Army Medical Center.United States Cardiovascular and Interventional RadiologyCardiovasc Interv Radiol 1982; 5: 238-240DOI: 10.1007/BF02565403 AbstractAbstract Not Available CategorySegmental Pulmonary Venous Disease. Without a Focus on Pulmonary HypertensionSymptoms and Findings Associated with Pulmonary Vascular DiseaseDiagnostic Testing for Pulmonary Vascular Disease. Invasive Testing Age Focus: Pediatric Pulmonary Vascular Disease

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Congenital atresia of unilateral pulmonary veins associated with a single ventricle: a rare case report and literature review

Hsing-Yuan Lee, Betau Hwang, Pi-Chang Lee, Sheng-Ling Jan, C.C. Laura MengTaoyuan Armed Force General Hospital.Taiwan Circulation JournalCirc J 2008; 72: 1544-1546DOI: 10.1253/circj.cj-07-0516 AbstractCongenital atresia or extreme hypoplasia of individual pulmonary veins is a rare condition that is usually asymptomatic if it only involves 1 or 2 segments of the lungs. It may be fatal if it

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Acquired unilateral pulmonary vein atresia in a 3-year-old boy

Mohammed Firdouse, Arnav Agarwal, Lars Grosse-Wortmann, Tapas K. MondalUniversity of Toronto and Hospital for Sick Children. McMaster University McMaster Children’s Hospital.Canada Journal of UltrasoundJ Ultrasound 2014; 18: 73-78DOI: 10.1007/s40477-014-0135-0 AbstractWhile unilateral pulmonary venous atresia (UPVA) most commonly presents as an extremely rare late embryological defect resulting in complete occlusion or absence of the PV pathway, it

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Unilateral absence of the pulmonary veins: an unusual diagnosis with characteristic imaging findings

Terry L. Levin, Bradford W. Betz, Lisa M. Gennarini, Chana WircbergChildren’s Hospital of Montefiore Medical Center.United States Clinical ImagingClin Imaging 2019; 55:107-111DOI: 10.1016/j.clinimag.2019.01.022 AbstractBackground: Congenital unilateral absence of the pulmonary vein (UCAPV) is a rare entity with characteristic clinical and imaging findings. Despite its congenital nature, the radiographic findings and symptoms of UCAPV may not be recognized

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A 12-Year-Old Girl With Dyspnea and Unilateral Interlobular Septal Thickening

Yong Chen, Yao Xiao, Ying Zhang, Guangfa Zhu, Ruiyu Dou, Hong GuBeijing Anzhen Hospital and Capital Medical University.China ChestChest 2019; 156: e57-e61DOI: 10.1016/j.chest.2019.03.022 AbstractA 12-year-old girl was admitted to the hospital for exercise intolerance and radiographic abnormalities. She presented with a 5-year history of shortness of breath during intense exercise and did not undergo any medical

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Diagnosis and management of congenital right pulmonary venous atresia

I. Ricardo Argueta-morales, Ruchira Garg, William M. DeCampliMiami Children’s Hospital and Arnold Palmer Hospital for Children.United States Cardiology in the YoungCardiol Young 2009; 19: 648-651DOI: 10.1017/S1047951109991867 AbstractCongenital unilateral pulmonary venous atresia is a rare anatomical defect. Patients present with pulmonary symptoms, and diagnosis may be elusive. Pulmonary arterial wedge angiography is the gold standard with which

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Right Pulmonary Venous Atresia: A Rare Cause for Recurrent Unilateral Pneumonia

Prashant P. PatilLotus Children Hospital.India Journal of Clinical and Diagnostic ResearchJ Clin Diag Res 2017; 11:DOI: 10.7860/JCDR/2017/25670.10596 AbstractRecurrent unilateral pneumonia poses a diagnostic dilemma for all paediatricians. Isolated pulmonary venous atresia is an uncommon entity, which presents with recurrent unilateral pulmonary infections, dyspnoea on exertion and haemoptysis. It is associated with significant mortality and morbidity. Owing

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