Filed (PHiled). Greater than 1-2 years since publication

Acid ceramidase gene therapy ameliorates pulmonary arterial hypertension with right heart dysfunction

Michael G. Katz, Yoav Hadas, Adam Vincek, Lina Freage‑Kahn, Nataly Shtraizent, Jeko M. Madjarov, Peter Pastuszko, Efrat Eliyahu Icahn School of Medicine at Mount Sinai. SeneX Therapeutics Inc. Atrium Health Sanger Heart and Vascular Institute. Wake Forest School of Medicine. United States Respiratory ResearchRespir Res 2023; 24DOI: 10.1186/s12931-023-02487-2 AbstractBackground: Up-regulation of ceramides in pulmonary hypertension (PH), contributing to […]

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Identification of ACKR4 as an immune checkpoint in pulmonary arterial hypertension

Chen-Yu Jiang, Li-Wei Wu, Yi-Wei Liu, Bei Feng, Lin-Cai Ye, Xu Huang, Yang-Yang He, Yi Shen, Yi-Fan Zhu, Xing-Liang Zhou, Dai-Ji Jiang, Hai-Kun Qi, Hao Zhang, Yi YanShanghai Children’s Medical Center. Henan University. Shanghaitech University. China Frontiers in ImmunologyFront Immunol 2023; DOI: 10.3389/fimmu.2023.1153573 AbstractObjective: Inflammation is recognized as a contributor in the development of pulmonary arterial hypertension

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Atrial septal defect-associated pulmonary hypertension with decompensated heart failure: outcomes after fenestrated device closure

Ahmad Deniwar, Jason Hernandez, Enrique O. Aregullin, Sana K. Khan, Sihong Huang, Michael T. Finn, Joseph J. VettukattilHelen DeVos Children’s Hospital of Spectrum Health Hospital and Michigan State University College of Human Medicine.United States Cardiology in the YoungCardiol Young 2023; DOI: 10.1017/S104795112300152X AbstractBackground: Up to 90% of adults with untreated atrial septal defect will be symptomatic by

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Practices and Outcomes from a Prospective, Multicenter Registry for Preterm Newborns with Pulmonary Hypertension

Nicolle Fernandez Dyess, Claire Palmer, Roger F. Soll, Reese H. Clark, Steven H. Abman, John P. Kinsella and the Preterm Newborn Pulmonary Hypertension Registry Study Group with Multiple Collaborating InvestigatorsUniversity of Colorado School of Medicine. University of Vermont. Pediatrix Center for Research. Multiple Collaborating Institutions.United States Journal of PediatricsJ Pediatr 2023; DOI: 10.1016/j.jpeds.2023.113614 AbstractObjective: To describe current

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Can Speckle Tracking Of Right Ventricle Add Value For Evaluation Of Asthma Severity In Children?

Ahmed Mohammad Abbas, Hany Hussein Mousa, Reda Biomy Bastawesy, Osama ElagamyKafrelsheikh University.Egypt Journal of the Pakistan Medical AssociationJ Pak Med Assoc 2023; 73(Suppl 4): S156-S160DOI: 10.47391/JPMA.EGY-S4-32 AbstractObjectives: To investigate myocardial deformation by tracking speckles along with evaluation of cardiac function using conventional and tissue Doppler imaging.Method: The case-control study was conducted at Kafrelsheikh University Hospital, Egypt, from September

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Pulmonary Vasodilator Therapy in Pediatric Patients on Ventricular Assist Device Support: A Single-Center Experience and Proposal for Use

Jennifer E. Schramm, John C. Dykes, Rachel K. Hopper, Jeffrey A. Feinstein, David N. Rosenthal, Rebecca J. KamenyJohns Hopkins University School of Medicine. Stanford University School of Medicine.United States American Society for Artificial Internal Organs JournalASAIO J 2023; DOI: 10.1097/MAT.0000000000002023 AbstractPediatric precapillary pulmonary hypertension can develop in response to systemic atrial hypertension. Systemic atrial decompression following

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Human liver single nuclear RNA sequencing implicates BMPR2, GDF15, arginine, and estrogen in portopulmonary hypertension

Arun Jose, Jean M. Elwing, Steven M. Kawut, Michael W. Pauciulo, Kenneth E. Sherman, William C. Nichols, Michael B. Fallon, Francis X. McCormackUniversity of Cincinnati College of Medicine and Cincinnati Children’s Hospital Medical Center. Perelman School at the University of Pennsylvania. University of Arizona. United States Communications BiologyCommun Biol 2023; 6DOI: 10.1038/s42003-023-05193-3 AbstractPortopulmonary hypertension (PoPH) is

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Outcomes of pregnancy in women with different types of pulmonary hypertension

Yang Liu, Haitao Li, Yanna Li, Jun Zhang, Hong Gu, Jiangang Wang, Qiang WangBeijing Anzhen Hospital Affiliated to Capital Medical University. Beijing Anzhen Hospital. China BioMed Central Cardiovascular DisordersBMC Cardiovasc Disord 2023; 23:DOI: 10.1186/s12872-023-03423-4 AbstractBackground: Pulmonary hypertension (PH) is considered to increase maternal and fetal risk, and we attempt to explore pregnancy outcomes in women with different

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Atypical Hemolytic-Uremic Syndrome: Genetic Basis, Clinical Manifestations, and a Multidisciplinary Approach to Management

Keval Yerigeri, Saurav Kadatane, Kai Mongan, Olivia Boyer, Linda LG Burke, Sidharth Kumar Sethi, Christoph Licht, Rupesh RainaCase Western Reserve University and The MetroHealth System. University of Oklahoma Health Sciences Center. Northeast Ohio Medical University. Necker-Enfants Malades Hospital. Kidney and Urology Institute. University of Toronto. Akron Children’s Hospital.United States, France and Canada Journal of Multidisciplinary

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Variants in FGF10 cause early onset of severe childhood interstitial lung disease: A detailed description of four affected children

Katharina Schutz, Axel Schmidt, Nicolaus Schwerk, Diane Miriam Renz, Benedicte Gerard, Elise Schaefer, Maria Cristina Antal, Sophia Peters, Matthias Griese, Christina K. Rapp, Hartmut Engels, Kristen Cremer, Anke Katharina Bergmann, Gunnar Schmidt, Bernd Auber, Jan C. Kamp, Florian Laenger, Sandra von HardenbergHannover Medical School. School of Medicine, University Hospital Bonn and University of Bonn. German

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