Class 1. Pulmonary Veno-occlusive Disease and Pulmonary Capillary Hemangiomatosis

Pulmonary Veno-Occlusive Disease Presenting as Congenital Heart Disease-Associated Pulmonary Hypertension

Takanori Suzuki, Satoru Kawai, Satona Tanaka, Hidetoshi Uchida, Hiromu Ukai, Yoji Nomura, Hiroyuki Katsuragawa, Junichi Kawada, Shuichiro YoshidaKariya Toyota General Hospital, Aichi Children’s Health and Medical Center and Fujita Health University. Kyoto University Hospital. Japan Journal of the American College of Cardiology Case ReportsJACC Case Rep 2026; DOI: 10.1016/j.jaccas.2026.109910 AbstractBackground: Pulmonary veno-occlusive disease (PVOD) is a rare […]

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Congenital unilateral pulmonary venous atresia with pulmonary veno-occlusive disease in contralateral lung: an unusual association

Savitri Shrivastava, James H . Moller, Jesse E . EdwardsUniversity of Minnesota.United States Pediatric CardiologyPediatr Cardiol 1986; 7: 213-219DOI: 10.1007/BF02093183 AbstractA patient presenting with the rare association of congenital unilateral pulmonary venous atresia in one lung and pulmonary veno-occlusive disease in the other is described. The patient first presented at the age of 3 1/2 years

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Reverse Potts shunt as rescue from venoarterial extracorporeal membrane oxygenation in pulmonary veno-occlusive disease

Emily Davis, Can Yerebakan, John T. BergerUMC Children’s Hospital and University Medical Center of Southern Nevada. Nationwide Children’s Hospital. Children’s National Hospital.United States Cardiology in the YoungCardiol Young 2025; DOI: 10.1017/S1047951125001957 AbstractPulmonary veno-occlusive disease has no definitive cure apart from lung transplant. The reverse Potts shunt can be a palliative bridge to transplant. A post-arrest 14-year-old

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Diagnostic enigma of pulmonary hypertension: Tale from a series of three patients

Anil Kumar Singhi, Anup Banerji, Nandini Biswas, Soumen DasMedica Super Specialty Hospital. India Medical Journal Armed Forces IndiaMed J Armed Forces Ind 2024; 80 (Suppl 1): S320-S324DOI: 10.1016/j.mjafi.2023.08.003 AbstractPulmonary hypertension (PH) is a complex condition with multiple etiological factors. The ability to identify a potential underlying cause is crucial for accurate diagnosis, patient management, and prognostication.

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Synchrotron-Based Phase-Contrast Micro-CT Combined With Histology to Decipher Differences Between Hereditary and Sporadic Pediatric Pulmonary Veno-Occlusive Disease

Ida Jeremiasen, Niccolò Peruzzi, Elna Lampei, Sofie Meyer, Levent M. Akyürek, Erik Gebre‐Medhin, Ceren Mutgan, Peter Dorfmüller, Lavinia Neubert, Danny Jonigk, Csaba Galambos, Karin Tran‐LundmarkDepartment of Experimental Medical Science and Wallenberg Center for Molecular Medicine Lund University. Skåne University Hospital. Sahlgrenska Academy Hospital. Ludwig Boltzmann Institute for Lung Vascular Research. Universities of Giessen and Marburg

Synchrotron-Based Phase-Contrast Micro-CT Combined With Histology to Decipher Differences Between Hereditary and Sporadic Pediatric Pulmonary Veno-Occlusive Disease Read More »

A case of pulmonary veno-occlusive disease and a new bronchoscopic sign

A. W. Matthews, R. BuchananQueen Alexandra Hospital.United Kingdom Respiratory MedicineRespir Med 1990; 84: 503-505DOI: 10.1016/s0954-6111(08)80117-5 AbstractAbstract Not Available CategoryClass I. Pulmonary Veno-occlusive Disease and Pulmonary Capillary HemangiomatosisSymptoms and Findings Associated with Pulmonary Vascular DiseaseDiagnostic Testing for Pulmonary Vascular Disease. Non-invasive TestingDiagnostic Testing for Pulmonary Vascular Disease. Invasive Testing Age Focus: Adult Pulmonary Vascular Disease Fresh or

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Case report: A finding of PVOD and PAH in first degree relatives suggests shared heritable risk and overlapping features of both pulmonary vascular diseases

Roger Winters, Lindsay M. Forbes, Dunbar Ivy, Carlyne Cool, Bryan D. Park, Peter Hountras, David Badesch, Sue Gu, Edda Spiekerkoetter, Roham Zamanian, Stacey Leier Gluck, Todd M. BullUniversity of Colorado and University of Colorado Children’s Hospital. Stanford University.United States Respirology Case ReportsRespirol Case Rep 2024; 12: DOI: 10.1002/rcr2.70064 AbstractPulmonary veno-occlusive disease (PVOD) is a rare form

Case report: A finding of PVOD and PAH in first degree relatives suggests shared heritable risk and overlapping features of both pulmonary vascular diseases Read More »

GCN2 kinase activation mediates pulmonary vascular remodeling and pulmonary arterial hypertension

Maggie M. Zhu, Jingbo Dai, Zhiyu Dai, Yi Peng, You-Yang ZhaoNorthwestern University Feinberg School of Medicine.United States Journal of Clinical Investigation InsightJCI Insight 2024; DOI: 10.1172/jci.insight.177926 AbstractPulmonary arterial hypertension (PAH) is characterized by progressive increase of pulmonary vascular resistance and remodeling that result in right heart failure. Recessive mutations of EIF2AK4 gene (encoding GCN2, General control

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Pediatric Lung Transplantation for Pulmonary Vascular Diseases: Recent Advances and Challenges

Levent Midyat, Eleanor D. Muise, Gary A. VisnerUniversity of Pittsburgh School of Medicine and Children’s Hospital of Pittsburgh. NYU Grossman School of Medicine and Hassenfeld Children’s Hospital. Harvard Medical School and Boston Children’s Hospital.United states Clinics in Chest MedicineClin Chest Med 2024; 45: 761-769DOI: 10.1016/j.ccm.2024.02.023 AbstractPediatric lung transplantation for pulmonary vascular diseases has seen notable advancements

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Primary pulmonary hypertension with obstructive venous lesions

D. B. Brewer, D. R HumphreysUniversity of Birmingham and the General Hospital ,Birmingham.United Kingdom British Heart JournalBrit Heart J 1960; 22: 445-448DOI: 10.1136/hrt.22.3.445 AbstractAbstract Not Available CategoryClass I. Pulmonary Veno-occlusive Disease and Pulmonary Capillary HemangiomatosisPulmonary Vascular Pathology Age Focus: Pediatric Pulmonary Vascular Disease Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication Article

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