Class 1. Pulmonary Hypertension Associated with Liver Disease

Paediatric porto-sinusoidal vascular disease: Two different clinical phenotypes with subtle histological differences

Angelo Di Georgio, Lorenza Matarazzo, Aurelio Sonzogni, Emanuele Nicastro, Andrea Pietrobattista, Mara Cananzi, PAola Gaio, Marco Sciveres, Grazia Di Leo, Raffaele, Iorio, Antonio Marseglia, Greta Carioli, Giuseppe Maggiore, Maria Guido, Lorenzo D’AntigaHospital Papa Giovanni XXIII. IRCCS Bambino Gesù, Pediatric Hospital. University Hospital of Padova.  Istituto Mediterraneo per i Trapianti e Terapie. IRCCS Burlo Garofolo. University

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Abernethy Malformation: Possible Diagnosis for Patients with Congenital Heart Disease and Persistent Cyanosis

Marilia Maroneze Brun, Mariana Rodero Cardoso, Bruna Cury Borim, Carlos Henrique De Marchi, Ulisses Alexandre CrotiHospital da Criança e Maternidade de São José do Rio Preto.Brazil Brazilian Journal of Cardiovascular SurgeryBraz J Cardiovasc Surg 2023; 38: 300-304DOI: 10.21470/1678-9741-2022-0110 AbstractClinical data: Infant, nine months of age, female, diagnosed with congenital heart disease, with signs of heart failure associated

Abernethy Malformation: Possible Diagnosis for Patients with Congenital Heart Disease and Persistent Cyanosis Read More »

Congenital Portosystemic Shunts in Children: Associations, Complications, and Outcomes

Frank DiPaola, Andrew T. Trout, Ashley E. Walther, Anita Gupta, Rachel Sheridan, Kathleen M. Campbell, Greg Tiao, Jorge A. Bezerra, Kevin E. Bove, Manish Patel, Jaimie D. NathanC.S. Mott Children’s Hospital. Cincinnati Children’s Hospital Medical Center. University of Cincinnati Medical Center. Children’s Hospital Los Angeles.United States Digestive Diseases and SciencesDig Dis Sci 2020; 65: 1239-1251DOI: 10.1007/s10620-019-05834-w

Congenital Portosystemic Shunts in Children: Associations, Complications, and Outcomes Read More »

Case Report: A Rare Syncope Case Caused by Abernethy II and a Review of the Literature

Xue-qin Lin, Jing-yi Rao, Yi-fei Xiang, Li-wei Zhang, Xiao-ling Cai, Yan-song Guo, Kai-yang LinShengli Clinical Medical College of Fujian Medical University and Fujian Provincial Hospital. Fujian Clinical Medical Research Center for Cardiovascular Diseases.China Frontiers in Cardiovascular DiseaseFront Cardiovasc Dis 2022; 8: DOI: 10.3389/fcvm.2021.784739 AbstractBackground: Abernethy malformation is an extremely rare anomaly of the splanchnic venous system, and

Case Report: A Rare Syncope Case Caused by Abernethy II and a Review of the Literature Read More »

A new variant of Abernethy malformation treated by transhepatic interventional closure: a case report

Ludger Sieverding, Michael Hofbeck, Jörg Michel, Andreas Hornung, Christian Scheckenbach, Gerd Grözinger, Ekkehard Sturm, Steven W. Warmann, Anja HanserUniversity Children’s Hospital, University Hospital of Tübingen and University of Tübingen. Germany BioMed Central GastroenterologyBMC Gastroenterol 2022; 22: DOI: 10.1186/s12876-022-02123-1 AbstractBackground: Congenital portosystemic shunts (CPSS) are rare vascular malformations and can be classified into extrahepatic and intrahepatic shunts. Extrahepatic

A new variant of Abernethy malformation treated by transhepatic interventional closure: a case report Read More »

Congenital portosystemic shunt with multiple splenic artery aneurysms: Reversing pulmonary hypertension and preventing aneurysm rupture

Anand P. Subramanian, Adaligere Paraswanath Bharath, Ashita Barthur, Mahimarangaiah JayranganathSri Jayadeva Institute of Cardiovascular Sciences and ResearchIndia Annals of Pediatric CardiologyAnn Pediatr Cardiol 2022; 15: 300-303DOI: 10.4103/apc.apc_142_21 AbstractWe report an unusual occurrence of multiple splenic artery aneurysms and splenomegaly in a young woman with severe pulmonary hypertension, secondary to a congenital portosystemic shunt (CPS). The splenic

Congenital portosystemic shunt with multiple splenic artery aneurysms: Reversing pulmonary hypertension and preventing aneurysm rupture Read More »

Transcatheter closure of congenital portosystemic shunts – A multicenter experience

Nageswara Rao Koneti, Shweta Bakhru, Mahimarangaiah Jayranganath, Mahesh Kappanayil, Prashant Bobhate, Lakshmivenkateshiah Srinivas, Snehal Kulkarni, Usha Mandikal Kodandarama Sastry, Raman Krishna KumarRainbow Children’s Heart Institute. Sri Jayadeva Institute of Cardiovascular Sciences and Research. Amrita Institute of Medical Sciences. Kokilaben Ambani Hospital. Jupiter Hospital.India Annals of Pediatric CardiologyAnn Pediatr Cardiol 2022; 15: 114-120DOI: 10.4103/apc.apc_5_22 AbstractBackground: Congenital portosystemic shunts

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Hemodynamic and Clinical Response to Liver Transplantation in Children and Young Adults POPH Patients

Shiro Baba, Eri Ogawa, Kentaro Akagi, Koichi Matsuda, Takuya Hirata, Tatsuya Okamoto, Hideaki Okajima, Junko TakitaKyoto UniversityJapan Pediatric CardiologyPediatr Cardiol 2023; DOI: 10.1007/s00246-023-03121-0 AbstractPortopulmonary hypertension is an intractable form of pulmonary hypertension. Although liver transplantation is recommended for patients who respond poorly to treatments, the mechanisms by which liver transplantation improves pulmonary hypertension remain unclear. The

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