Class 1. Pulmonary Hypertension Associated with Connective Tissue Disease

Resistin predicts disease severity and survival in patients with pulmonary arterial hypertension

Li Gao, John Skinner, Tanmay Nath, Qing Lin, Megan Griffiths, Rachel L. Damico, Michael W. Pauciulo, William Nichols, Paul M. Hassoun, Allen Everett, Roger A. JohnsJohns Hopkins University School of Medicine. University of Texas Southwestern Medical Center. Cincinnati Children’s Hospital Medical Center and University of Cincinnati. United States Respiratory ResearchRespir Res 2024; 25: DOI: 10.1186/s12931-024-02861-8 AbstractBackground: Abnormal […]

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Systemic sclerosis sine scleroderma in children is more aggressive than in adults

Francesca Tirelli, Elisabetta Zanatta, Beatrice Moccaldi, Marco Binda, Giorgia Martini, Chiara Giraudo, Fabio Vittadello, Alessandra Meneghel, Francesco ZulianUniversity of Padova. Italy RheumatologyRheumatology 2024; DOI: 10.1093/rheumatology/keae304 AbstractObjectives: To compare the clinical and laboratory features of pediatric systemic sclerosis sine scleroderma (ssJSSc) with adult-onset ssSSc.Methods: Demographic, clinical and laboratory data of ssJSSc, retrospectively retrieved from our hospital medical records, case

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Fatal pulmonary arterial hypertension (PAH): A rare association of anti-MDA-5 positive juvenile dermatomyositis

R. Shreyas, Anagha Patteri, M. B. Hayagrivas, Tanya Singla, Shivaprasad Pannasamudra Mohankumar, Saurabh Kumar Gupta, Manisha Jana, Narendra Kumar Bagri, A. V. RamananAll India Institute of Medical Sciences. Bristol Royal Hospital for Children.India and United Kingdom International Journal of Rheumatic DiseasesInt J Rheum Dis 2024; 27: DOI: 10.1111/1756-185X.15180 AbstractAbstract Not Available CategoryClass I. Pulmonary Hypertension Associated

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Cardiovascular risk and inflammation in a population with autoimmune diseases: a narrative review

Camilla Bertoni, Alessandra Mazzocchi, Ludovica Leone, Carlo Agostoni, Giovanni FilocamoUniversity of Milan. Fondazione Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) Ca’ Grande Ospedale Maggiore Policlinico. Italy Frontiers in ImmunologyFront Immunol 2024; 15:DOI: 10.3389/fimmu.2024.1380372 AbstractJuvenile Systemic Connective Tissue Diseases (JSCTD) are a heterogeneous group of chronic autoimmune diseases, associated with dyslipidemia and increased cardiovascular risk

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Systemic juvenile idiopathic arthritis-associated lung disease: A retrospective cohort study

Konstantin E. Belozerov, Natalia M. Solomatina, Eugenia A. Isupova, Alla A. Kuznetsiva, Mikhail M. KostikSaint-Petersburg State Pediatric Medical University. Children’s City Polyclinic No. 29 of the Kalininsky District of St. Petersburg. Almazov National Medical Research Centre.Russia World Journal of Clinical PediatricsWorld J Clin Pediar 2024; 13:DOI: 10.5409/wjcp.v13.i1.88912 AbstractBackground: Lung damage in systemic juvenile arthritis (sJIA) is one

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Long-term safety and tolerability of ambrisentan treatment for pediatric patients with pulmonary arterial hypertension: An open-label extension study

Dunbar Ivy, Maurice Beghetti, Ernesto Juaneda‑Simian, Ramiya Ravindranath, Mary Ann Lukas, Sandra Machlitt‑Northen, Nicola Scott, Jun Narita, Rolf M. F. BergerChildren’s Hospital Colorado. University Children’s Hospital HUG and University of Geneva. Hospital de Niños de la Santísma Trinidad. Glaxo-Smith-Kline. Osaka University Graduate School of Medicine. Beatrix Children’s Hospital, University Medical Center Groningen and University of

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Longitudinal follow-up of mixed connective tissue disease and overlapping autoimmune diseases of childhood onset in the Afro-descendant population of the French West Indies

Arthur Felix, Lindsay Osei, Frederique Delion, Benoit Suzon, Aurore Abel, Moustapha Drame, Yves Hatchuel, Christophe Deligny, Fabienne Louis‑SidneyUniversity of the French West Indies and Martinique University Hospital. CHU de la Martinique La Meynard. Andrée Rosemon Hospital. Guadeloupe University Hospital. France Pediatric Rheumatology Online JournalPediatr Rheumatol Online J 2024; 22:DOI: 10.1186/s12969-023-00951-3 AbstractIntroduction: Overlap autoimmune syndromes (OAS) and mixed

Longitudinal follow-up of mixed connective tissue disease and overlapping autoimmune diseases of childhood onset in the Afro-descendant population of the French West Indies Read More »

Systemic lupus erythematosus in pediatric patients: Pulmonary manifestations

Jonathan G. Palafox-Floresa, Omar E. Valencia-Ledezmab, Guillermo Vargas-L´opezc, Lourdes Jamaica-Balderasd, Nydia Acevedo-Silvae, Carlos A. Castro-FuentesHospital Regional de Alta Especialidad de Ixtapaluca. Hospital Infantil de México Federico Gómez. Mexico Respiratory MedicineRespir Med 2023; DOI: 10.1016/j.rmed.2023.107456 AbstractThe pulmonary manifestations of Systemic Lupus Erythematosus (SLE) in pediatric patients are poorly understood and the pulmonary manifestations reported from the adult

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Kynurenine pathway metabolism evolves with development of preclinical and scleroderma-associated pulmonary arterial hypertension

Catherine E. Simpson, Anjira S. Ambade, Robert Harlan, Aurelie Roux, Susan Aja, David Graham, Ami A. Shah, Laura K. Hummers, Anna R. Humnes, Jane A. Leopold, Evelyn M. Horn, Erika S. Berman-Rosenzweig, Gabrielle Grunig, Michaela A. Aldred, John Barnard, Suzy A. A. Comhair, W. H. Wilson Tang, Megan Griffiths, Franz Rischard, Robert P. Frantz, Serpil

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Metabolomic differences in connective tissue disease-associated versus idiopathic pulmonary arterial hypertension in the PVDOMICS cohort

Catherine E. Simpson, Anna R. Hemnes, Megan Griffiths, Gabriele Grunig, W. H. Wison Tang, Joe G. N. Garcia, John Barnard, Suzy A. Comhair, Rachel L. Damico, Stephen C. Mathai, Paul M. Hassoun, the PVDOMICS Study GroupJohns Hopkins University. Vanderbilt University. University of Texas Southwestern Medical Center. New York University Grossman School of Medicine. Cleveland Clinic.

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