Class 1. Pulmonary Hypertension Associated with Connective Tissue Disease

The clinical assessment of lung involvement in patients with Still’s disease, results from the multicentre international AIDA Network Still’s Disease Registry

Piero Ruscitti 1, Antonio Vitale 2 3, Ilenia Di Cola 1, Valeria Caggiano 2 3, Pierpaolo Palumbo 4, Ernesto Di Cesare 1, Andrea Hinojosa-Azaola 5, Jiram Torres-Ruiz 5, Guillermo Arturo Guaracha-Basañez 5, Eduardo Martín-Nares 5, Giuseppe Lopalco 6, Maria Morrone 6, Florenzo Iannone 6, Henrique A Mayrink Giardini 7, Rafael Alves Cordeiro 7, Isabele Parente de Brito Antonelli 7, Onorina Berardicurti 8 9, Luca Navarini 8 9, Francesco Ciccia 10, Maria Chiara Visconti 10, Daniela Iacono 10, Haner Direskeneli 11, Sukran Erten 12, Haihong Yao 13, Maissa Thabet 14, Samar Tharwat 15 16, Gaafar Ragab 17 18, Verónica Gómez-Caverzaschi 19, Petros P Sfikakis 20, Lampros Fotis 21, Francesco La Torre 22, Armin Maier 23, Anastasios Karamanakos 24, Ibrahim A Almaghlouth 25 26, Micol Frassi 27, Abdurrahman Tufan 28, Marcello Govoni 29, Jurgen Sota 2 3, Gabriele Simonini 30, Giacomo Emmi 31 32, Francesca Li […]

The clinical assessment of lung involvement in patients with Still’s disease, results from the multicentre international AIDA Network Still’s Disease Registry Read More »

Pulmonary Arterial Hypertension Incidence in Scleroderma Patients Treated with Bosentan for Digital Ulcers: Evidence from the Italian SPRING Registry

Fabio Cacciapaglia, Rossella De Angelis, Clodoveo Ferri, Gianluigi Bajocchi, Silvia Bellando-Randone, Cosimo Bruni, Martina Orlandi, Marco Fornaro, Edoardo Cipolletta, Giovanni Zanframundo, Roberta Foti, Giovanna Cuomo, Alarico Ariani, Edoardo Rosato, Gemma Lepri, Francesco Girelli, Elisabetta Zanatta, Silvia Laura Bosello, Ilaria Cavazzana, Francesca Ingegnoli, Maria De Santis, Giuseppe Murdaca, Giuseppina Abignano, Pettiti Giorgio, Alessandra Della Rossa, Maurizio Caminiti, Annamaria Iuliano, Giovanni Ciano, Lorenzo Beretta, Gianluca Bagnato, Ennio Lubrano, Ilenia De Andres, Alessandro Giollo, Marta Saracco, Cecilia Agnes, Corrado Campochiaro, Federica Lumetti, Amelia Spinella, Luca Magnani, Giacomo De Luca, Veronica Codullo, Elisa Visalli, Carlo Iandoli, Antonietta Gigante, Greta Pellegrino, Franco Cozzi, Maria Grazia Lazzaroni, Elena

Pulmonary Arterial Hypertension Incidence in Scleroderma Patients Treated with Bosentan for Digital Ulcers: Evidence from the Italian SPRING Registry Read More »

Diagnostic enigma of pulmonary hypertension: Tale from a series of three patients

Anil Kumar Singhi, Anup Banerji, Nandini Biswas, Soumen DasMedica Super Specialty Hospital. India Medical Journal Armed Forces IndiaMed J Armed Forces Ind 2024; 80 (Suppl 1): S320-S324DOI: 10.1016/j.mjafi.2023.08.003 AbstractPulmonary hypertension (PH) is a complex condition with multiple etiological factors. The ability to identify a potential underlying cause is crucial for accurate diagnosis, patient management, and prognostication.

Diagnostic enigma of pulmonary hypertension: Tale from a series of three patients Read More »

Pulmonary manifestations of juvenile vs. adult systemic sclerosis: insights into pathophysiological and clinical features

Gabriele Di Pasquale, Nicholas Caione, Alessio Di Berardino, Giulio Di DonatoUniversity of L’Aquila.Italy Pediatric PulmonologyPediatr Pulmonol 2024; DOI: 10.1002/ppul.27347 AbstractJuvenile systemic sclerosis (jSSc), the pediatric counterpart of systemic sclerosis (SSc), is a rare autoimmune disorder characterized by vasculopathy and fibrotic disorders. It ranks among the rheumatologic diseases with the highest rates of morbidity and mortality, predominantly

Pulmonary manifestations of juvenile vs. adult systemic sclerosis: insights into pathophysiological and clinical features Read More »

The role of immune cells in the pathogenesis of connective tissue diseases-associated pulmonary arterial hypertension

Zhe Li, Juan Ma, Xuejing Wang, Liquan Zhu, Yu Gan, Baoquan DaiWeifang Maternal and Child Health Hospital. Shandong Second Medical University.China Frontiers in ImmunologyFront Immunol 2024; 15: DOI: 10.3389/fimmu.2024.1464762 AbstractConnective tissue diseases-related pulmonary arterial hypertension (CTD-PAH) is a disease characterized by an elevated pulmonary artery pressure that arises as a complication of connective tissue diseases. The

The role of immune cells in the pathogenesis of connective tissue diseases-associated pulmonary arterial hypertension Read More »

Utility of factor D and other alternative complement factors as biomarkers in systemic sclerosis-associated pulmonary arterial hypertension (SSc-PAH)

Eva Petrow, Changyong Feng, Ashley Frazer-Abel, Roberta Goncalves Marangoni, Katie Lutz, William C. Nichols, V. Michael Holers, Christopher Ritchlin, R. James White III, Benjamin D. KormanUniversity of Rochester Medical Center. University of Colorado School of Medicine. Cincinnati Children’s Medical Center and University of Cincinnati College of Medicine. United States Seminars in Arthritis and RheumatismSemin Arthritis

Utility of factor D and other alternative complement factors as biomarkers in systemic sclerosis-associated pulmonary arterial hypertension (SSc-PAH) Read More »

A Single Center Experience of Pulmonary Arterial Hypertension Management in Korea: A 25-Year Comparative Analysis Following the Introduction of Targeted Therapy

Ji Hyun Cha I-Seok Kang, Shin Yi Jang, June Huh Jeong Hoon Yang, Jinyoung Song, Taek Kyu Park, Seung Woo Park, Hojoong Kim, Duk-Kyung Kim Sung-A ChangSamsung Medical Center, Samsung Changwon Hospital and Sungkyunkwan University School of Medicine. Republic of Korea Korean Circulation JournalKorean Circ J 2024; DOI: 10.4070/kcj.2023.0316 AbstractBackground and objectives: The transformation of pulmonary arterial

A Single Center Experience of Pulmonary Arterial Hypertension Management in Korea: A 25-Year Comparative Analysis Following the Introduction of Targeted Therapy Read More »

Neonatal lupus erythematosus with severe persistent pulmonary hypertension

Bin Zhuang, Yulin Chen, Shuping HanWomen’s Hospital of Nanjing Medical University and Nanjing Women and Children’s Healthcare HospitalChina Quarterly Journal of MedicineQJM 2024; DOI: 10.1093/qjmed/hcae134 AbstractAbstract Not Available CategoryClass I. Persistent Pulmonary Hypertension of the NewbornClass I. Pulmonary Hypertension Associated with Connective Tissue Disease Age Focus: Pediatric Pulmonary Vascular Disease Fresh or Filed Publication: Fresh (PHresh).

Neonatal lupus erythematosus with severe persistent pulmonary hypertension Read More »

Resistin predicts disease severity and survival in patients with pulmonary arterial hypertension

Li Gao, John Skinner, Tanmay Nath, Qing Lin, Megan Griffiths, Rachel L. Damico, Michael W. Pauciulo, William Nichols, Paul M. Hassoun, Allen Everett, Roger A. JohnsJohns Hopkins University School of Medicine. University of Texas Southwestern Medical Center. Cincinnati Children’s Hospital Medical Center and University of Cincinnati. United States Respiratory ResearchRespir Res 2024; 25: DOI: 10.1186/s12931-024-02861-8 AbstractBackground: Abnormal

Resistin predicts disease severity and survival in patients with pulmonary arterial hypertension Read More »

Systemic sclerosis sine scleroderma in children is more aggressive than in adults

Francesca Tirelli, Elisabetta Zanatta, Beatrice Moccaldi, Marco Binda, Giorgia Martini, Chiara Giraudo, Fabio Vittadello, Alessandra Meneghel, Francesco ZulianUniversity of Padova. Italy RheumatologyRheumatology 2024; DOI: 10.1093/rheumatology/keae304 AbstractObjectives: To compare the clinical and laboratory features of pediatric systemic sclerosis sine scleroderma (ssJSSc) with adult-onset ssSSc.Methods: Demographic, clinical and laboratory data of ssJSSc, retrospectively retrieved from our hospital medical records, case

Systemic sclerosis sine scleroderma in children is more aggressive than in adults Read More »

Scroll to Top