Class 1. Pulmonary Hypertension Associated with Congenital Cardiovascular Disease

Vein of Galen aneurysmal malformation: rationalizing medical management of neonatal heart failure

Melinda Cory, Phillippe Durand, Rafael Sillero, Luc Morin, Rashmin Savani, Lina Chalak, Dimitrios AngelesThe University of Texas Southwestern Medical Center. Paris-Saclay University Hospitals, Bicêtre Medical Centre and Assistance Publique-Hospitaux de Paris.United States and France Pediatric ResearchPediatr Res 2023; 93: 39-48DOI: 10.1038/s41390-022-02064-1 AbstractNeonates who present in high output heart failure secondary to vein of Galen aneurysmal malformation […]

Vein of Galen aneurysmal malformation: rationalizing medical management of neonatal heart failure Read More »

Differential biventricular adaption to pulmonary vascular disease in patients with idiopathic/heritable and congenital heart disease: a prospective cardiac magnetic resonance and invasive study

Zhuoyuan Xu, Ruiyu Dou, Zhen Zhou, Hongsheng Zhang, Chen Zhang, Qiangqiang Li, Lei Xu, Hong GuBeijing Anzhen Hospital and Capital Medical University. China European Heart Journal Cardiovascular ImagingEur Heart J Cardiovasc Imag 2023; DOI: 10.1093/ehjci/jead106 AbstractAims: Despite shared pathophysiological mechanisms, patients with idiopathic/heritable pulmonary arterial hypertension (IPAH/HPAH) have a poorer prognosis than those with PAH after congenital

Differential biventricular adaption to pulmonary vascular disease in patients with idiopathic/heritable and congenital heart disease: a prospective cardiac magnetic resonance and invasive study Read More »

Outcomes in Patients with Pulmonary Arterial Hypertension Underwent Transcatheter Closure of an Atrial Septal Defect

Jae-Hee Seol, Se-Yong Jung, Han-Byul Lee, Ah-Young Kim, Eun-Hwa Kim, In-Kyung Min, Nam-Kyun Kim, Jae-Young ChoiSeverance Cardiovascular Hospital and Yonsei University College of Medicine. Yonsei University Wonju College of Medicine. Soonchunhyang University College of Medicine. Republic of Korea Journal of Clinical MedicineJ Clin Med 2023; 12:DOI: 10.3390/jcm12072540 AbstractPulmonary arterial hypertension (PAH) related to an atrial septal

Outcomes in Patients with Pulmonary Arterial Hypertension Underwent Transcatheter Closure of an Atrial Septal Defect Read More »

Endothelin inhibitors lower pulmonary vascular resistance and improve functional capacity in patients with Fontan circulation

Gabriella Agnoletti, Simona Gala, Francesca Ferroni, Roberto Bordese, Lorenzo Appendini, Carlo Pace Napoleone, Laura BergamascoCitta’ della Salute e della Scienza. Italy Journal of Thoracic and Cardiovascular SurgeryJ Thorac Cardiovasc Surg 2017; 153: 1468-1475DOI: 10.1016/j.jtcvs.2017.01.051 AbstractObjectives: To evaluate the effects of endothelin inhibitors (ERAs) on hemodynamic and functional parameters in patients post-Fontan procedure with high pulmonary vascular resistance

Endothelin inhibitors lower pulmonary vascular resistance and improve functional capacity in patients with Fontan circulation Read More »

Assessment of the effect of two regimens of milrinone infusion in paediatric patients with pulmonary artery hypertension undergoing corrective cardiac procedure: A prospective observational study

Mrugesh Prajapati, Jigar Patel, Hasmukh Patel, Hemang Gandhi, Guriqbal Singh, Pravin PatelU.N. Mehta Institute of Cardiology and Research CenterIndia Annals of Pediatric CardiologyAnn Pediatr Cardiol 2022; 15: 358-363DOI: 10.4103/apc.apc_230_21 AbstractBackground: The aim of the study was to compare the effect of two different regimens of milrinone in pediatric patients with pulmonary artery hypertension (PAH) undergoing corrective procedure.Materials

Assessment of the effect of two regimens of milrinone infusion in paediatric patients with pulmonary artery hypertension undergoing corrective cardiac procedure: A prospective observational study Read More »

Plasma mid-regional proadrenomedullin level in children with pulmonary hypertension associated with CHD

Shimaa A. Elesawy, Hesham A. El-Serogy, Esraa A. Sorour, Amr M. Zoairar Elsalam General Hospital and Ministry of Health. Tanta University. Egypt Cardiology in the YoungCardiol Young 2023; DOI: 10.1017/S1047951123000471 AbstractAdrenomedullin has been shown to inhibit proliferation in pulmonary artery smooth muscle cells and to alleviate pulmonary artery collagen accumulation in pulmonary hypertension. We aimed to

Plasma mid-regional proadrenomedullin level in children with pulmonary hypertension associated with CHD Read More »

Congenital Portosystemic Shunts in Children: Associations, Complications, and Outcomes

Frank DiPaola, Andrew T. Trout, Ashley E. Walther, Anita Gupta, Rachel Sheridan, Kathleen M. Campbell, Greg Tiao, Jorge A. Bezerra, Kevin E. Bove, Manish Patel, Jaimie D. NathanC.S. Mott Children’s Hospital. Cincinnati Children’s Hospital Medical Center. University of Cincinnati Medical Center. Children’s Hospital Los Angeles.United States Digestive Diseases and SciencesDig Dis Sci 2020; 65: 1239-1251DOI: 10.1007/s10620-019-05834-w

Congenital Portosystemic Shunts in Children: Associations, Complications, and Outcomes Read More »

Pulmonary Hypertension in Infants and Children with Vein of Galen Malformation and Association with Clinical Outcomes

Jai Khurana, Darren B. Orbach, Kimberlee Gauvreau, Shane A. Collins, Joseph B. Tella, Pankai B. Agrawal, Helen A. Christou, Mary P. MullenBoston Children’s Hospital, Boston. Harvard Medical School. Brigham & Women’s Hospital.United States Journal of PediatricsJ Pediatr 2023; DOI: 10.1016/j.jpeds.2023.113404 AbstractObjective: To assess the extent and resolution of pulmonary hypertension (PH), cardiovascular factors, and echocardiographic findings associated

Pulmonary Hypertension in Infants and Children with Vein of Galen Malformation and Association with Clinical Outcomes Read More »

Case Report: Selexipag in pediatric pulmonary hypertension: Initiation, transition, and titration

Jenna M. Faircloth, Neelam D. Bhatt, Corey A. Chartan, Ryan D. Coleman, Natalie Villafranco, Fadel E. Ruiz, Raysa Morales-Demori, Elise Whalen, Erin Ely, Rozmeen Fombin, Nidhy P. VargheseTexas Children’s Hospital and Baylor College of Medicine.United States Frontiers in PediatricsFront Pediatr 2023; 11: DOI: 10.3389/fped.2023.1050508 AbstractSelexipag, a selective prostacyclin receptor agonist, is approved for treating pulmonary arterial

Case Report: Selexipag in pediatric pulmonary hypertension: Initiation, transition, and titration Read More »

Maternal Outcomes Among Pregnant Women With Congenital Heart Disease-Associated Pulmonary Hypertension

Qian Zhang, Fang Zhu, Guochen Shi, Chen Hu, Weituo Zhang, Puzhen Huang, Chunfeng Zhu, Hong Gu, Dong Yang, Qiangqiang Li, Yonghua Niu, Hao Chen, Ruixiang Ma, Ziyi Pan, Huixian Miao, Xin Zhang, Genxia Li, Yabing Tang, Guyuan Qiao, Yichen Yan, Zhongqun Zhu, Hao Zhang, Fangzhen Han, Yanna Li. Jianhua Lin, Huiwen ChenMultiple InstitutionsChina CirculationCirculation 2023;

Maternal Outcomes Among Pregnant Women With Congenital Heart Disease-Associated Pulmonary Hypertension Read More »

Scroll to Top