Class 1. Idiopathic Pulmonary Hypertension

Safety and Effectiveness of Selexipag in Pediatric Pulmonary Hypertension: A Retrospective Multi-Center Cohort Study

Benjamin S. Frank, Eliza R. Gentzler, Catherine M. Avitabile, Kathleen Miller-Reed, Zhaoxing Pan, Erika B. Rosenzweig, D. Dunbar Ivy, Usha S. KrishnanUniversity of Colorado School of Medicine and Children’s Hospital Colorado. Columbia University Irving Medical Center and Morgan Stanley Childrens Hospital of New York Presbyterian Hospital. University of Pennsylvania School of Medicine and Children’s Hospital […]

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Pediatric Lung Transplantation for Pulmonary Vascular Diseases: Recent Advances and Challenges

Levent Midyat, Eleanor D. Muise, Gary A. VisnerUniversity of Pittsburgh School of Medicine and Children’s Hospital of Pittsburgh. NYU Grossman School of Medicine and Hassenfeld Children’s Hospital. Harvard Medical School and Boston Children’s Hospital.United states Clinics in Chest MedicineClin Chest Med 2024; 45: 761-769DOI: 10.1016/j.ccm.2024.02.023 AbstractPediatric lung transplantation for pulmonary vascular diseases has seen notable advancements

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Biventricular responses to exercise and their relation to cardiorespiratory fitness in pediatric pulmonary hypertension

Guido E. Pieles, Dan-Mihai Dorobantu, Jessica E. Caterini, Barbara Cifra, Janette Reyes, Sara Roldan Ramos, Eilis Hannon, Craig A. Williams, Tilman Humpl, Luc Mertens, Greg D. Wells, Mark K. FriedbergHospital for Sick Children. University of Exeter.Canada and United Kingdom American Joural of Physiology Heart and Circulatory PhysiologyAm J Physiol Heart Circ Physiol 2024; DOI: 10.1152/ajpheart.00096.2024 AbstractDespite

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Resistin predicts disease severity and survival in patients with pulmonary arterial hypertension

Li Gao, John Skinner, Tanmay Nath, Qing Lin, Megan Griffiths, Rachel L. Damico, Michael W. Pauciulo, William Nichols, Paul M. Hassoun, Allen Everett, Roger A. JohnsJohns Hopkins University School of Medicine. University of Texas Southwestern Medical Center. Cincinnati Children’s Hospital Medical Center and University of Cincinnati. United States Respiratory ResearchRespir Res 2024; 25: DOI: 10.1186/s12931-024-02861-8 AbstractBackground: Abnormal

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ECMO Bridge to Lung Transplant in Children with Idiopathic Pulmonary Arterial Hypertension

Hosam F. Ahmed, David L. S. Morales, Don Hayes, JrCincinnati Children’s Hospital Medical Center and University of Cincinnati College of Medicine.United States LungLung 2024; DOI: 10.1007/s00408-024-00703-4 AbstractIdiopathic pulmonary arterial hypertension (IPAH) represents an important clinical indication for lung transplant (LTx) in children. Recent trends show fewer children with IPAH are undergoing LTx nowadays compared to previous

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Digital Spatial Profiling Identifies Distinct Molecular Signatures of Vascular Lesions in Pulmonary Arterial Hypertension

Rubin M. Tuder, Aneta Gandjeva, Sarah Williams, Sushil Kumar, Vitaly O. Kheyfets, Kyle Matthew Hatton-Jones, Jacqueline R. Starr, Jeong Yun, Jason Hong, Nicholas R. West, Kurt R. StenmarkUniversity of Colorado Anschutz Medical Campus School of Medicine. University of Colorado. Griffith University. Brigham and Women’s Hospital and Harvard Medical School. University of California, Los Angeles.United States

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Predicting Peri-Operative Cardiorespiratory Adverse Events in Children with Idiopathic Pulmonary Arterial Hypertension Undergoing Cardiac Catheterization Using Echocardiography: A Cohort Study

Timothy J. W. Dawes, Valentine Woodham, Emma Sharkey, Angus McEwan, Graham Derrick, Vivek Muthurangu, Shahin Moledina, Lucy HepburnGreat Ormond Street Hospital for Children NHS Foundation Trust. University College London. , Evelina London Children’s Hospital, Guy’s and St. Thomas’ NHS Foundation Trust. United Kingdom Pediatric CardiologyPediatr Cardiol 2024; DOI: 10.1007/s00246-024-03447-3 AbstractGeneral anesthesia in children with idiopathic pulmonary

Predicting Peri-Operative Cardiorespiratory Adverse Events in Children with Idiopathic Pulmonary Arterial Hypertension Undergoing Cardiac Catheterization Using Echocardiography: A Cohort Study Read More »

Hemodynamic and Clinical Profiles of Pulmonary Arterial Hypertension Patients with GDF2 and BMPR2 Variants

Mei-Tzu Wang, Ken-Pen Weng, Sheng-Kai Chang, Wei-Chun Huang, Lee-Wei ChenNational Yang Ming Chiao Tung University. Kaohsiung Veterans General Hospital. Excelsior Biopharma Inc. Fooyin University. National Sun Yat-Sen University.Taiwan International Journal of Molecular SciencesInt J Mol Sci 2024; 25:DOI: 10.3390/ijms25052734 AbstractAsians have a higher carrier rate of pulmonary arterial hypertension (PAH)-related genetic variants than Caucasians do. This

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Combination of high-flow nasal oxygen and ketamine/dexmedetomidine sedation for diagnostic catheterization in a child with pulmonary arterial hypertension: a case report

Kaoru Tsuboi, Misuzu Asai, Toshiki Nakamura, Jun Ninagawa, Hiroshi Ono, Shugo KasuyaNational Center for Child Health and Development. Yokohama City University Hospital.Japan Journal of Anesthesia Clinical ReportsJA Clin Rep 2024; 10:DOI: 10.1186/s40981-024-00699-z AbstractPulmonary hypertension is associated with significant risk of perioperative life-threatening events. We present a case of a 12-year-old child with severe pulmonary arterial hypertension

Combination of high-flow nasal oxygen and ketamine/dexmedetomidine sedation for diagnostic catheterization in a child with pulmonary arterial hypertension: a case report Read More »

Long-term safety and tolerability of ambrisentan treatment for pediatric patients with pulmonary arterial hypertension: An open-label extension study

Dunbar Ivy, Maurice Beghetti, Ernesto Juaneda‑Simian, Ramiya Ravindranath, Mary Ann Lukas, Sandra Machlitt‑Northen, Nicola Scott, Jun Narita, Rolf M. F. BergerChildren’s Hospital Colorado. University Children’s Hospital HUG and University of Geneva. Hospital de Niños de la Santísma Trinidad. Glaxo-Smith-Kline. Osaka University Graduate School of Medicine. Beatrix Children’s Hospital, University Medical Center Groningen and University of

Long-term safety and tolerability of ambrisentan treatment for pediatric patients with pulmonary arterial hypertension: An open-label extension study Read More »

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