Systemic to Pulmonary Arterial Collaterals or Connections Associated with Pulmonary Vascular Disease Archives

Congenital descending aorta to pulmonary vein fistula: an unusual cause of left ventricular dilation in a 21-year-old female

Xiang Pan, Chan Yu, Zhouhui Chen, Bowen ZhaoSir Run Run Shaw Hospital and Zhejiang University College of Medicine.China Journal of Cardiothoracic SurgeryJ Cardiothorac Surg 2025; 20: DOI: 10.1186/s13019-025-03691-5 AbstractBackground: Congenital descending aorta to pulmonary vein fistula (cDAPVF) is a rare congenital vascular malformation diagnosed in infancy and childhood. Adult cDAPVF is often asymptomatic and usually detected incidentally […]

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Protective Effects of Bronchopulmonary Sequestration (BPS) on the Prognosis of Neonates with Congenital Diaphragmatic Hernia (CDH)

Sujin Gang, Yong Jae Kwon, Hyunhee Kwon, Suhyun Ha, Jueun Park, Byong Sop Lee, Euiseok Jung, Jiyoon Jeong, Soo Hyun Kim, Jung-Man NamgoongAsan Medical Center Children’s Hospital, Asan Medical Center and Jeonbuk National University Hospital. University of Ulsan College of Medicine. Gangneung Asan Hospital.Republic of Korea BioMedical Central PediatricsBMC Prediatr 2025; 25: DOI: 10.1186/s12887-025-05755-w AbstractBackground: Congenital diaphragmatic

Protective Effects of Bronchopulmonary Sequestration (BPS) on the Prognosis of Neonates with Congenital Diaphragmatic Hernia (CDH) Read More »

Unilateral Pulmonary Vein Atresia in a Child

Jia-Bei Liu, Peng LiuFirst Affiliated Hospital of Hunan Normal University and Hunan Provincial People’s Hospital.China Pediatric PulmonologyPediatr Pulmonol 2025; 60:DOI: 10.1002/ppul.27378 AbstractWe describe a case of unilateral pulmonary vein atresia in a child who presented with a recurrent cough. Pulmonary artery CT angiography confirmed the diagnosis. In addition, we found anomalous blood-supplying arteries from the abdominal

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Concurrent Bronchopulmonary Sequestration in Congenital Diaphragmatic Hernia: Is Frequency Increasing or Are We Better at Diagnosis?

Michelle J. Yang, Christian C. Yost, Martha Monson, Paula J. Woodward, Anne M. Kennedy, Stephen J. Fenton, Katie W. Russell, Janice L. B. Byrne, Bradley A. YoderPrimary Children’s Hospital and University of Utah School of Medicine.United States Journal of Pediatrics: Clinical PracticeJ Pediatr Clin Pract 2025; DOI: 10.1016/j.jpedcp.2025.200141 AbstractObjective: To assess the incidence and clinical outcomes of

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Esophageal varices in association with unilateral pulmonary vein atresia

J. Kevin Harrison, Steven E. Hearne, William M. Baker, Peter Van Trigt, Gil Leidig, Thomas M. Bashore, Martin P. O’LaughlinDuke University Medical Center.United States Catheterization and Cardiovascular DiagnosesCathet Cardiovasc Diagn 1996; 38: 387-392DOI: 10.1002/(SICI)1097-0304(199608)38:4<387::AID-CCD14>3.0.CO;2-C AbstractA 27-yr-old woman with recurrent episodes of hemoptysis (and hematemesis due to esophageal varices) was found to have unilateral pulmonary vein atresia.

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Cardiac phenotypic spectrum of KCNT1 mutations

Utkarsh Kohli, Chitra Ravishankar, Douglas NordliComer Children’s Hospital and Pritzker School of Medicine of the University of Chicago. he Children’s Hospital of Philadelphia and Perelman School of Medicine at the University of Pennsylvania. United States Cardiology in the YoungCardiol Young 2020; 30: 1935-1939DOI: 10.1017/S1047951120002735 AbstractWe report a 10-month-old girl with KCNT1 (c1420C > T; p. Arg474Cys,

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Isolated agenesis of the right pulmonary veins with pulmonary sequestration

Shilpa Patil, Sakshi Sachdeva, Shweta Bakhru, Bharat Dalvi, Nageswara Rao KonetiCare Hospital. Glenmark Cardiac Center. India Annals of Pediatric CardiologyAnn Pediatr Cardiol 2019; 12: 135-137DOI: 10.4103/apc.APC_55_18 AbstractWe report two cases of agenesis of the right pulmonary veins (PVs) associated with sequestration of the right lung with systemic to pulmonary collateral. Both the children were referred for

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Hypoplastic right lung associated with right pulmonary vein stenosis and systemic collateral

Anant Khositseth, Suvipaporn Siriporpitak, Preecha LaohakunakornRamathibodi Hospital Mahidol University.Thailand Congenital Heart DiseaseCongenit Heart Dis 2010; 5: 76-80DOI: 10.1111/j.1747-0803.2009.00324.x AbstractWe present a case of a 6-month-old girl diagnosed as unilateral pulmonary vein stenosis (right inferior pulmonary vein) with dextroposition of the heart, hypoplastic right lung, hypoplastic right pulmonary artery, collateral from the descending aorta supplied right lower

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Congenital isolated unilateral agenesis of pulmonary arteries in adults: case series and review

Pankaj Jariwala, Venkata Nagarjuna Maturu, Johann Christopher, Kartik Pandurang JadhavYashoda Hospitals. Care Hospitals.India Indian Journal of Thoracic and Cardiovascular SurgeryIndian J Thorac Cardiovasc Surg 2021; 37 (Suppl 1): 144-154DOI: 10.1007/s12055-020-01032-w AbstractCongenital, isolated unilateral agenesis of pulmonary arteries (UAPA) has a bimodal clinical presentation. It is either diagnosed in early infancy or during adulthood. Early diagnosis and

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Systemic artery to pulmonary artery aneurysm malformations associated with variants at MCF2L

S.E. Mitchell, R. P. Martin, P. Terry, S. E. Drant, D. Valle, H. Dietz, N. SobreiraJohns Hopkins University School of Medicine. Children’s Hospital of Philadelphia. United States American Journal of Medical GeneticsAm J Med Genet 2023; 191: 1250-1260DOI: 10.1002/ajmg.a.63141 AbstractArteriovenous malformations (AVM) are characterized by abnormal vessels connecting arteries and veins resulting in a disruption of

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