Bilateral Pulmonary Arteriovenous Malformations: Challenges in a Rare and Complex Case

Aayushi Joshi, Vasu Saini, Bhumika Bheemavarapu, Anjani Mahesh Kumar Cherukuri, Mohd. Shaban
Shri Guru Ram Rai Institute of Medical and Health Sciences. Jawaharlal Institute of Postgraduate Medical Education and Research. Guntur Medical College.
India

Cureus
Cureus 2024; 16:
DOI: 10.7759/cureus.70231

Abstract
Pulmonary arteriovenous malformations (PAVMs) are abnormal vascular connections between the pulmonary arteries and pulmonary veins. Despite their relatively uncommon incidence, PAVMs should be considered in the differential diagnosis of children presenting with cyanosis due to the life-threatening complications posed by paradoxical emboli. The primary management approach involves eliminating the abnormal connections, either through surgical or endovascular methods. We present a case of a five-year-old boy who was seen in the Outpatient Department with cyanosis of the lips and nail beds persisting for eight months. On examination, grade 3 clubbing was noted. Imaging and subsequent angiography revealed multiple bilateral diffuse AVMs, which were treated using an endovascular approach.

Category
Pulmonary Arteriovenous Malformations
Symptoms and Findings Associated with Pulmonary Vascular Disease
Surgical and Catheter-mediated Interventions for Pulmonary Vascular Disease

Age Focus: Pediatric Pulmonary Vascular Disease

Fresh or Filed Publication: Fresh (PHresh). Less than 1-2 years since publication

Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: Yes

Scroll to Top