An Extremely Rare Variant of Pulmonary Venous Atresia

Yuki Nakamura, Kagami Miyaji, Yurie Miyata, Atsushi Kitagawa
Kitasato University Hospital.
Japan

Annals of Thoracic Surgery
AnnThorac Surg 2016; 101: 2382-2384
DOI: 10.1016/j.athoracsur.2015.08.085

Abstract
We describe an unusual case of a newborn with a rare variant of atresia of the common pulmonary vein that was mistaken for total anomalous pulmonary venous connection, cardiac type. The survival of patients with atresia of the common pulmonary vein is dependent on early diagnosis followed by immediate surgical repair, although early accurate diagnosis has been described as difficult in previous reports. Reverse aortic arch flow detected by echocardiography may be an important sign suggesting such a diagnosis.

Category
Segmental Pulmonary Venous Disease. Without a Focus on Pulmonary Hypertension
Symptoms and Findings Associated with Pulmonary Vascular Disease
Diagnostic Testing for Pulmonary Vascular Disease. Non-invasive Testing
Surgical and Catheter-mediated Interventions for Pulmonary Vascular Disease

Age Focus: Pediatric Pulmonary Vascular Disease

Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication

Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: Yes

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