Meghan M. Cirulis, Lynda O. Jorgensen, Ronald W. Day
University of Utah and Primary Children’s Hospital.
United States
Respiratory Medicine Case Reports
Respir Med Case Rep 2019; 28:
DOI: 10.1016/j.rmcr.2019.100911
Abstract
The pulmonary arterial pressure of a child with severe pulmonary arterial hypertension immediately normalized while breathing nitric oxide during heart catheterization at 8 years of age. Her acute pulmonary vascular response to nitric oxide has persisted throughout her life. Her acute response to other medications has been similar to her long-term response to medications in the same class. Acute vasodilator testing with inhaled nitric oxide and other medications may be an opportunity to refine study design and advance precision care for patients with pulmonary hypertension.
Category
Class I. Pulmonary hypertension Associated with Favorable Response to Nitric Oxide and Calcium Channel Blockers
Diagnostic Testing for Pulmonary Vascular Disease. Invasive Testing
Precision Care for Pulmonary Vascular Disease
Age Focus: Pediatric Pulmonary Vascular Disease or Adult Pulmonary Vascular Disease
Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication
Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: Yes