Chandler E. Yost, Angelica R. Putnam, Megan K. Dishop, Lynda O. Jorgenson, Paul E. Wirkus, Ronald W. Day
University of Utah, Primary Children’s Hospital, Phoenix Children’s Hospital and Wasatch Pediatrics
United States
Journal of the American College of Cardiology Case Reports
JACC Case Rep 2020; 2: 1492-1495
DOI: 10.1016/j.jaccas.2020.05.055
Abstract
A patient with alveolar capillary dysplasia has survived more than 56 months with medical therapy. Intrauterine exposure to metformin potentially modified the severity of disease. In combination with other agents, endothelin receptor antagonists and amlodipine have been key medications in lowering pulmonary arterial pressure and managing right heart failure.
Category
Class 3. Developmental Diseases of the Lung
Genetic Factors Associated with Pulmonary Vascular Disease.
Age Classification: Pediatric Pulmonary Vascular Disease
Fresh or Filed Publication: Filed (PHiled), Greater than 1-2 years since publication
Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: Yes