I. Artero Muñoz, F. Serrano Puche, M. I. Padín Marín, F. Serrano Ramos
Hospital Regional Universitario Carlos Haya.
Spain
Ragiología
Radiología 2008; 50: 82-85
DOI: 10.1016/s0033-8338(08)71934-9
Abstract
Congenital unilateral pulmonary vein atresia is a very rare anomaly that generally presents during childhood or adolescence as recurrent episodes of pulmonary infections or hemoptysis. Its presentation in adults is highly exceptional. We describe two patients with congenital unilateral pulmonary vein atresia: the first is a 26-year-old woman with recurrent episodes of hemoptysis, and the second is a three-year-old boy with a history of bronchospasm and recurrent pneumonia from the age of three months. Although the diagnosis has classically been reached using cardiac catheterization and pulmonary angiography, we think that the CT and MRI findings can enable the diagnosis of congenital unilateral pulmonary vein atresia in cases with compatible clinical presentation. We emphasize the capacity of MRI for characterizing the vascular anomaly present in these patients.
Category
Segmental Pulmonary Venous Disease. Without a Focus on Pulmonary Hypertension
Symptoms and Findings Associated with Pulmonary Vascular Disease
Diagnostic Testing for Pulmonary Vascular Disease. Non-invasive Testing
Age Focus: Pediatric Pulmonary Vascular Disease or Adult Pulmonary Vascular Disease
Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication
Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: No