Arif Albulushi, Shabib Al-Asmi, Moosa Al-Abri, Hatem Al-Farhan
University of Nebraska Medical Center. Royal Hospital. Heart Hospital, Armed Forces Hospital and Sultan Qaboos University Hospital. Hamad Medical Corporation.
United States, Oman and Qatar
Journal of the American College of Cardiology Case Reports
JACC Case Rep 2024; 29:
DOI: 10.1016/j.jaccas.2024.102323
Abstract
Our case report details the journey of a 16-year-old male patient with Shone complex and advanced heart failure. We highlight the pivotal role of the HeartWare Ventricular Assist Device (Medtronic) implantation in mitigating severe pulmonary hypertension, thereby facilitating his eligibility for a heart transplant. We discuss the subsequent management of post-transplant pulmonary hypertension and right ventricular dysfunction using targeted pulmonary vasodilators and inotropic support, underscoring the intricacies of postoperative care in pediatric heart transplant patients. This case emphasizes our observation of the critical role that left ventricular assist devices play in redefining transplant candidacy and the necessity for complex, ongoing management in pediatric heart transplant scenarios.
Category
Class II. Pulmonary Hypertension Associated with Valvular Disease of the Left Side of the Heart
Surgical and Catheter-mediated Interventions for Pulmonary Vascular Disease
Medical Therapy. Efficacy or Lack of Efficacy
Age Focus: Pediatric Pulmonary Vascular Disease
Fresh or Filed Publication: Fresh (PHresh). Less than 1-2 years since publication
Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: Yes