Pulmonary vein stenosis: Etiology, diagnosis and management

Pablo Pazos-López, Cristina García-Rodríguez, Alba Guitián-González, Emilio Paredes-Galán, María Ángel De La Guarda Álvarez-Moure, Marta Rodríguez-Álvarez, José Antonio Baz-Alonso, Elvis Teijeira-Fernández, Francisco Eugenio Calvo-Iglesias, Andrés Íñiguez-Romo
Complexo Hospitalario Universitario de Vigo and Hospital Álvaro Cunqueiro.
Spain

World Journal of Cardiology
World J Cardiol 2016; 8: 81-88
DOI: 10.4330/wjc.v8.i1.81

Abstract
Pulmonary vein stenosis (PVS) is rare condition characterized by a challenging diagnosis and unfavorable prognosis at advance stages. At present, injury from radiofrequency ablation for atrial fibrillation has become the main cause of the disease. PVS is characterized by a progressive lumen size reduction of one or more pulmonary veins that, when hemodynamically significant, may raise lobar capillary pressure leading to signs and symptoms such as shortness of breath, cough, and hemoptysis. Image techniques (transesophageal echocardiography, computed tomography, magnetic resonance and perfusion imaging) are essential to reach a final diagnosis and decide an appropriate therapy. In this regard, series from referral centers have shown that surgical and transcatheter interventions may improve prognosis. The purpose of this article is to review the etiology, assessment and management of PVS.

Category
Segmental Pulmonary Venous Disease. Without a Focus on Pulmonary Hypertension
Diagnostic Testing for Pulmonary Vascular Disease. Non-invasive Testing
Surgical and Catheter-mediated Interventions for Pulmonary Vascular Disease
Review Articles Concerning Pulmonary Vascular Disease

Age Focus: Pediatric Pulmonary Vascular Disease or Adult Pulmonary Vascular Disease

Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication

Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: Yes

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