Sara Medellin, Nelson Burbano-Vera, Andrej Alfirevic
Cleveland Clinic Foundation
United States
Journal of Cardiothoracic and Vascular Anesthesia
J Cardiothorac Vasc Surg 2023;
DOI: 10.1053/j.jvca.2023.11.006
Abstract
Cor triatriatum is a rare congenital heart defect that occurs when a fibromuscular membrane divides the atrium into two chambers, which may impair blood flow to the ventricle. When it does, the symptoms usually manifest during infancy or early childhood. In this E-challenge, though, the case of a 40-year-old man is reviewed whose symptoms of shortness of breath progressed over the years and were attributed to the diminished mitral valve inflow due to the restricted cor triatriatum sinister associated with pulmonary hypertension, tachycardia-bradycardia syndrome, and atrial fibrillation. Despite routine preoperative evaluation, intraoperative transesophageal echocardiography was used to more accurately evaluate cor triatriatum sinister’s morphology, hemodynamic significance, and associated anomalies.
Category
Class II. Pulmonary Hypertension Associated with Pulmonary Vein Stenosis
Age Focus: Adult Pulmonary Vascular Disease
Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication
Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: No