Francois Lacour-Gayet, Christian Rey, Claude Planché
Marie-Lannelongue Hospital and Paris-Sud University.
France
Archives des Maladies du Coeur et des Vaisseaux
Arch Mal Couer Vaiss 1996; 89: 633-636
DOI: Not Available
Abstract
Pulmonary vein stenosis is a rare cardiac disease associated with a disastrous prognosis. Nowadays, it is more often a iatrogenic complication, following neonatal surgical repair of total anomalous pulmonary venous drainage (TAPVD). It is as well a native congenital anomaly. The responsible histologic lesion is an intimal hyperplasia that proliferates to involve the extracardiac segment of the pulmonary veins. This lesion tends to be extremely recurrent following surgical or angioplastic attempts. A new sutureless surgical technique, that tunelizes the pulmonary veins to the left atrium through the pericardium, is described. This method was successfully applied in a 2.5 years old child, presenting with bilateral stenosis of pulmonary veins, following neonatal repair of a TAPVD. The result, controlled 6 months later, by catheterization and angiography was judged satisfactory. This new technique, that has to be confirmed by a longer follow up, may provide a therapeutic answer to this challenging disease.
Category
Segmental Pulmonary Venous Disease. Without a Focus on Pulmonary Hypertension
Surgical and Catheter-mediated Interventions for Pulmonary Vascular Disease
Age Focus: Pediatric Pulmonary Vascular Disease
Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication
Article Access
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