Lance V. Fong, Robert H. Anderson, Sang C. Park, James R. Zuberbuhler
Children’s Hospital of Pittsburgh.
United States
American Journal of Cardiology
Am J Cardiol 1988; 62: 1136-1138
DOI: 10.1016/0002-9149(88)90568-1
Abstract
Congenital stenosis of the pulmonary veins is a rare abnormality causing progressive pulmonary hypertension and cardiac failure in childhood.1 Prognosis is generally bleak despite attempts at surgical repair2,3 and, more recently, transvenous balloon dilatation.4,5 Initial relief has usually been followed by recurrence. We reviewed 9 autopsy cases of this condition catalogued in the Cardiopathological Museum of the Children’s Hospital of Pittsburgh. Cases of pulmonary venous obstruction coexisting with totally anomalous pulmonary venous connections were excluded.
Category
Class II. Pulmonary Hypertension Associated with Pulmonary Vein Stenosis
Pulmonary Vascular Pathology
Age Focus: Pediatric Pulmonary Vascular Disease
Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication
Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: No