Israel Diamond
Children’s Hospital and University of Louisville School of Medicine
United States
Pediatrics
Pediatrics 1958; 22: 279–288
https://doi.org/10.1542/peds.22.2.279
Abstract
The Hamman-Rich syndrome is described in a 4-year-old Negro male. The clinical picture was that of persistent cough and progressive dyspnea beginning at 4 months of age. Diagnosis was made ante mortem by lung biopsy. The fibrotic process and arteriolosclerosis were more marked in the right lung. The disease may have been initiated by a bout of aspiration. There was accompanying stenosis of the right pulmonary artery and vein and occlusion of the lumen of the right pulmonary vein at its entrance to the left atrium. The hilar vascular findings are believed to be secondary to hilar areolar inflammation.
Category
Segmental Pulmonary Venous Disease. Without a Focus on Pulmonary Hypertension
Segmental Pulmonary Arterial Disease
Environmental Factors Associated with Pulmonary Vascular Disease
Pulmonary Vascular Pathology
Age Focus: Pediatric Pulmonary Vascular Disease
Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication
Article Access
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