Pulmonary hypertension secondary to partial pulmonary venous obstruction in a child with Cantu syndrome

Daisuke Kobayashi, Amanda L. Cook, Derek A. Williams
Wake Forest University School of Medicine.
United States

Pediatric Pulmonology
Pediatr Pulmonol 2010; 5: 727-729
DOI: 10.1002/ppul.21215

Abstract
We report on an African-American male with Cantu syndrome who required a pericardial window for a significant pericardial effusion in infancy and was subsequently found to have partial pulmonary venous obstruction (PVO) leading to pulmonary hypertension. Measurement of bilateral pulmonary capillary wedge pressures is important to uncover partial PVO.

Category
Class II. Pulmonary Hypertension Associated with Pulmonary Vein Stenosis
Genetic Factors Associated with Pulmonary Vascular Disease
Diagnostic Testing for Pulmonary Vascular Disease. Invasive Testing

Age Focus: Pediatric Pulmonary Vascular Disease

Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication

Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: No

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