Anant Khositseth, Suvipaporn Siriporpitak, Preecha Laohakunakorn
Ramathibodi Hospital Mahidol University.
Thailand
Congenital Heart Disease
Congenit Heart Dis 2010; 5: 76-80
DOI: 10.1111/j.1747-0803.2009.00324.x
Abstract
We present a case of a 6-month-old girl diagnosed as unilateral pulmonary vein stenosis (right inferior pulmonary vein) with dextroposition of the heart, hypoplastic right lung, hypoplastic right pulmonary artery, collateral from the descending aorta supplied right lower lung, connection between collateral and right pulmonary artery with retrograde flow from right pulmonary artery into main pulmonary artery, and right superior and middle pulmonary vein agenesis. A combined modality of imaging including chest film, echocardiography, multidetector computerized tomography, and the cardiac catheterization nicely demonstrated all of the unique and rare congenital abnormalities.
Category
Segmental Pulmonary Venous Disease. Without a Focus on Pulmonary Hypertension
Abnormal Systemic to Pulmonary Arterial Collaterals or Connections
Diagnostic Testing for Pulmonary Vascular Disease. Non-invasive Testing
Diagnostic Testing for Pulmonary Vascular Disease. Invasive Testing
Age Focus: Pediatric Pulmonary Vascular Disease
Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication
Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: No